2021 ICD-10-CM Diagnosis Code A39.1

Waterhouse-Friderichsen syndrome

    2016 2017 2018 2019 2020 2021 Billable/Specific Code
  • A39.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2021 edition of ICD-10-CM A39.1 became effective on October 1, 2020.
  • This is the American ICD-10-CM version of A39.1 - other international versions of ICD-10 A39.1 may differ.
Applicable To
  • Meningococcal hemorrhagic adrenalitis
  • Meningococcic adrenal syndrome
The following code(s) above A39.1 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to A39.1:
  • A00-B99
    2021 ICD-10-CM Range A00-B99

    Certain infectious and parasitic diseases

    Includes
    • diseases generally recognized as communicable or transmissible
    Type 1 Excludes
    • certain localized infections - see body system-related chapters
    Type 2 Excludes
    • carrier or suspected carrier of infectious disease (Z22.-)
    • infectious and parasitic diseases complicating pregnancy, childbirth and the puerperium (O98.-)
    • infectious and parasitic diseases specific to the perinatal period (P35-P39)
    • influenza and other acute respiratory infections (J00-J22)
    Use Additional
    • code to identify resistance to antimicrobial drugs (Z16.-)
    Certain infectious and parasitic diseases
Approximate Synonyms
  • Waterhouse friderichsen syndrome, meningococcal
ICD-10-CM A39.1 is grouped within Diagnostic Related Group(s) (MS-DRG v38.0):
  • 791 Prematurity with major problems
  • 793 Full term neonate with major problems
  • 870 Septicemia or severe sepsis with mv >96 hours
  • 871 Septicemia or severe sepsis without mv >96 hours with mcc
  • 872 Septicemia or severe sepsis without mv >96 hours without mcc

Convert A39.1 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
Code annotations containing back-references to A39.1:
  • Type 1 Excludes: E27.1
    , E27.4
    , E35
    , E35
    ICD-10-CM Diagnosis Code E27.1

    Primary adrenocortical insufficiency

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Addison's disease
    • Autoimmune adrenalitis
    Type 1 Excludes
    • Addison only phenotype adrenoleukodystrophy (E71.528)
    • amyloidosis (E85.-)
    • tuberculous Addison's disease (A18.7)
    • Waterhouse-Friderichsen syndrome (A39.1)
    ICD-10-CM Diagnosis Code E27.4

    Other and unspecified adrenocortical insufficiency

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • adrenoleukodystrophy [Addison-Schilder] (E71.528)
    • Waterhouse-Friderichsen syndrome (A39.1)
    ICD-10-CM Diagnosis Code E35

    Disorders of endocrine glands in diseases classified elsewhere

      2016 2017 2018 2019 2020 2021 Billable/Specific Code Manifestation Code
    Code First
    • underlying disease, such as:
    • late congenital syphilis of thymus gland [Dubois disease] (A50.5)
    Type 1 Excludes
    • Echinococcus granulosus infection of thyroid gland (B67.3)
    • meningococcal hemorrhagic adrenalitis (A39.1)
    • syphilis of endocrine gland (A52.79)
    • tuberculosis of adrenal gland, except calcification (A18.7)
    • tuberculosis of endocrine gland NEC (A18.82)
    • tuberculosis of thyroid gland (A18.81)
    • Waterhouse-Friderichsen syndrome (A39.1)
    Use Additional
    • code, if applicable, to identify:
    • sequelae of tuberculosis of other organs (B90.8)
    ICD-10-CM Diagnosis Code E35

    Disorders of endocrine glands in diseases classified elsewhere

      2016 2017 2018 2019 2020 2021 Billable/Specific Code Manifestation Code
    Code First
    • underlying disease, such as:
    • late congenital syphilis of thymus gland [Dubois disease] (A50.5)
    Type 1 Excludes
    • Echinococcus granulosus infection of thyroid gland (B67.3)
    • meningococcal hemorrhagic adrenalitis (A39.1)
    • syphilis of endocrine gland (A52.79)
    • tuberculosis of adrenal gland, except calcification (A18.7)
    • tuberculosis of endocrine gland NEC (A18.82)
    • tuberculosis of thyroid gland (A18.81)
    • Waterhouse-Friderichsen syndrome (A39.1)
    Use Additional
    • code, if applicable, to identify:
    • sequelae of tuberculosis of other organs (B90.8)

Diagnosis Index entries containing back-references to A39.1:
  • Adrenalitis, adrenitis E27.8
    ICD-10-CM Diagnosis Code E27.8

    Other specified disorders of adrenal gland

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Abnormality of cortisol-binding globulin
    • meningococcal, hemorrhagic A39.1
  • Apoplexia, apoplexy, apoplectic
    • adrenal A39.1
  • Disease, diseased - see also Syndrome
    • Waterhouse-Friderichsen A39.1
  • Friderichsen-Waterhouse syndrome or disease A39.1
  • Infection, infected, infective (opportunistic) B99.9
    ICD-10-CM Diagnosis Code B99.9

    Unspecified infectious disease

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    • meningococcal A39.9
      - see also condition
      ICD-10-CM Diagnosis Code A39.9

      Meningococcal infection, unspecified

        2016 2017 2018 2019 2020 2021 Billable/Specific Code
      Applicable To
      • Meningococcal disease NOS
      • adrenals A39.1
  • Meningococcus, meningococcal A39.9
    - see also condition
    ICD-10-CM Diagnosis Code A39.9

    Meningococcal infection, unspecified

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Meningococcal disease NOS
    • adrenalitis, hemorrhagic A39.1
  • Sepsis (generalized) (unspecified organism) A41.9
    ICD-10-CM Diagnosis Code A41.9

    Sepsis, unspecified organism

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Septicemia NOS
    • adrenal hemorrhage syndrome A39.1 (meningococcal)
  • Syndrome - see also Disease
    • adrenal
      • hemorrhage A39.1 (meningococcal)
      • meningococcic A39.1
    • Friderichsen-Waterhouse A39.1
    • septicemic adrenal hemorrhage A39.1
    • Waterhouse A39.1 (-Friderichsen)
  • Waterhouse A39.1 (-Friderichsen) syndrome or disease (meningococcal)

ICD-10-CM Codes Adjacent To A39.1
A37.9 Whooping cough, unspecified species
A37.90 …… without pneumonia
A37.91 …… with pneumonia
A38 Scarlet fever
A38.0 Scarlet fever with otitis media
A38.1 Scarlet fever with myocarditis
A38.8 Scarlet fever with other complications
A38.9 Scarlet fever, uncomplicated
A39 Meningococcal infection
A39.0 Meningococcal meningitis
A39.1 Waterhouse-Friderichsen syndrome
A39.2 Acute meningococcemia
A39.3 Chronic meningococcemia
A39.4 Meningococcemia, unspecified
A39.5 Meningococcal heart disease
A39.50 Meningococcal carditis, unspecified
A39.51 Meningococcal endocarditis
A39.52 Meningococcal myocarditis
A39.53 Meningococcal pericarditis
A39.8 Other meningococcal infections
A39.81 Meningococcal encephalitis

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.