Malignant neuroendocrine tumors C7A- >

Use Additional
Use Additional Help
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
  • code to identify any associated endocrine syndrome, such as:
  • carcinoid syndrome (
    ICD-10-CM Diagnosis Code E34.0

    Carcinoid syndrome

      2016 2017 2018 Billable/Specific Code
    Note
    • May be used as an additional code to identify functional activity associated with a carcinoid tumor.
    E34.0
    )
Code Also
Code Also Help
A code also note instructs that 2 codes may be required to fully describe a condition but the sequencing of the two codes is discretionary, depending on the severity of the conditions and the reason for the encounter.
  • any associated multiple endocrine neoplasia [MEN] syndromes (
    ICD-10-CM Diagnosis Code E31.2

    Multiple endocrine neoplasia [MEN] syndromes

      2016 2017 2018 Non-Billable/Non-Specific Code
    Applicable To
    • Multiple endocrine adenomatosis
    Code Also
    • any associated malignancies and other conditions associated with the syndromes
    E31.2-
    )
Type 2 Excludes
Type 2 Excludes Help
A type 2 excludes note represents "not included here". A type 2 excludes note indicates that the condition excluded is not part of the condition it is excluded from but a patient may have both conditions at the same time. When a type 2 excludes note appears under a code it is acceptable to use both the code (C7A) and the excluded code together.
  • malignant pancreatic islet cell tumors (
    ICD-10-CM Diagnosis Code C25.4

    Malignant neoplasm of endocrine pancreas

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Malignant neoplasm of islets of Langerhans
    Use Additional
    • code to identify any functional activity.
    C25.4
    )
  • Merkel cell carcinoma (
    ICD-10-CM Diagnosis Code C4A
    • C4A Merkel cell carcinoma
      • C4A.0 Merkel cell carcinoma of lip
      • C4A.1 Merkel cell carcinoma of eyelid, including ca...
        • C4A.10 Merkel cell carcinoma of unspecified eyelid, ...
        • C4A.11 Merkel cell carcinoma of right eyelid, includ...
        • C4A.12 Merkel cell carcinoma of left eyelid, includi...
      • C4A.2 Merkel cell carcinoma of ear and external aur...
        • C4A.20 Merkel cell carcinoma of unspecified ear and ...
        • C4A.21 Merkel cell carcinoma of right ear and extern...
        • C4A.22 Merkel cell carcinoma of left ear and externa...
      • C4A.3 Merkel cell carcinoma of other and unspecifie...
        • C4A.30 Merkel cell carcinoma of unspecified part of ...
        • C4A.31 Merkel cell carcinoma of nose
        • C4A.39 Merkel cell carcinoma of other parts of face
      • C4A.4 Merkel cell carcinoma of scalp and neck
      • C4A.5 Merkel cell carcinoma of trunk
        • C4A.51 Merkel cell carcinoma of anal skin
        • C4A.52 Merkel cell carcinoma of skin of breast
        • C4A.59 Merkel cell carcinoma of other part of trunk
      • C4A.6 Merkel cell carcinoma of upper limb, includin...
        • C4A.60 Merkel cell carcinoma of unspecified upper li...
        • C4A.61 Merkel cell carcinoma of right upper limb, in...
        • C4A.62 Merkel cell carcinoma of left upper limb, inc...
      • C4A.7 Merkel cell carcinoma of lower limb, includin...
        • C4A.70 Merkel cell carcinoma of unspecified lower li...
        • C4A.71 Merkel cell carcinoma of right lower limb, in...
        • C4A.72 Merkel cell carcinoma of left lower limb, inc...
      • C4A.8 Merkel cell carcinoma of overlapping sites
      • C4A.9 Merkel cell carcinoma, unspecified
    C4A.-
    )
Codes