2017/18 ICD-10-CM Diagnosis Code D47.01

Cutaneous mastocytosis

Applicable To
  • Diffuse cutaneous mastocytosis
  • Maculopapular cutaneous mastocytosis
  • Solitary mastocytoma
  • Telangiectasia macularis eruptiva perstans
  • Urticaria pigmentosa
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as D47.01. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • congenital (diffuse) (maculopapular) cutaneous mastocytosis (
    ICD-10-CM Diagnosis Code Q82.2

    Congenital cutaneous mastocytosis

      2016 2017 2018 - Revised Code Billable/Specific Code POA Exempt
    Applicable To
    • Congenital diffuse cutaneous mastocytosis
    • Congenital maculopapular cutaneous mastocytosis
    • Congenital urticaria pigmentosa
    Type 1 Excludes
    • cutaneous mastocytosis NOS (D47.01)
    • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
    • malignant mastocytosis (C96.2-)
    • systemic mastocytosis (D47.02)
    • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
    Q82.2
    )
  • congenital urticaria pigmentosa (
    ICD-10-CM Diagnosis Code Q82.2

    Congenital cutaneous mastocytosis

      2016 2017 2018 - Revised Code Billable/Specific Code POA Exempt
    Applicable To
    • Congenital diffuse cutaneous mastocytosis
    • Congenital maculopapular cutaneous mastocytosis
    • Congenital urticaria pigmentosa
    Type 1 Excludes
    • cutaneous mastocytosis NOS (D47.01)
    • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
    • malignant mastocytosis (C96.2-)
    • systemic mastocytosis (D47.02)
    • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
    Q82.2
    )
  • extracutaneous mastocytoma (
    ICD-10-CM Diagnosis Code D47.09

    Other mast cell neoplasms of uncertain behavior

      2018 - New Code Billable/Specific Code
    Applicable To
    • Extracutaneous mastocytoma
    • Mast cell tumor NOS
    • Mastocytoma NOS
    • Mastocytosis NOS
    D47.09
    )
The following code(s) above D47.01 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to D47.01:
  • C00-D49
    2018 ICD-10-CM Range C00-D49

    Neoplasms

    Note
    • Functional activity
    • All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
    • Morphology [Histology]
    • Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
    • Primary malignant neoplasms overlapping site boundaries
    • A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
    • Malignant neoplasm of ectopic tissue
    • Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).
    Neoplasms
  • D37-D48
    2018 ICD-10-CM Range D37-D48

    Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes

    Note
    • Categories D37-D44, and D48 classify by site neoplasms of uncertain behavior, i.e., histologic confirmation whether the neoplasm is malignant or benign cannot be made.
    Type 1 Excludes
    • neoplasms of unspecified behavior (D49.-)
    Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes
  • D47.0
    ICD-10-CM Diagnosis Code D47.0

    Mast cell neoplasms of uncertain behavior

      2016 2017 2018 - Deleted Code 2018 - New Code Non-Billable/Non-Specific Code
    Type 1 Excludes
    • congenital cutaneous mastocytosis (Q82.2-)
    • histiocytic neoplasms of uncertain behavior (D47.Z9)
    • malignant mast cell neoplasm (C96.2-)
    Mast cell neoplasms of uncertain behavior
ICD-10-CM D47.01 is grouped within Diagnostic Related Group(s) (MS-DRG v35.0):

Convert D47.01 to ICD-9-CM

Code History
Code annotations containing back-references to D47.01:

Diagnosis Index entries containing back-references to D47.01:

ICD-10-CM Codes Adjacent To D47.01
D46.21 Refractory anemia with excess of blasts 1
D46.22 Refractory anemia with excess of blasts 2
D46.A Refractory cytopenia with multilineage dysplasia
D46.B Refractory cytopenia with multilineage dysplasia and ring sideroblasts
D46.C Myelodysplastic syndrome with isolated del(5q) chromosomal abnormality
D46.4 Refractory anemia, unspecified
D46.Z Other myelodysplastic syndromes
D46.9 Myelodysplastic syndrome, unspecified
D47 Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
D47.0 Mast cell neoplasms of uncertain behavior
D47.01 Cutaneous mastocytosis
D47.02 Systemic mastocytosis
D47.09 Other mast cell neoplasms of uncertain behavior
D47.1 Chronic myeloproliferative disease
D47.2 Monoclonal gammopathy
D47.3 Essential (hemorrhagic) thrombocythemia
D47.4 Osteomyelofibrosis
D47.Z Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
D47.Z1 Post-transplant lymphoproliferative disorder (PTLD)
D47.Z2 Castleman disease
D47.Z9 Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.