2017/18 ICD-10-CM Diagnosis Code D69.42

Congenital and hereditary thrombocytopenia purpura

Applicable To
  • Congenital thrombocytopenia
  • Hereditary thrombocytopenia
Code First
Code First Help
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
  • congential or hereditary disorder, such as:
  • thrombocytopenia with absent radius (TAR syndrome) (
    ICD-10-CM Diagnosis Code Q87.2

    Congenital malformation syndromes predominantly involving limbs

      2016 2017 2018 Billable/Specific Code POA Exempt
    Applicable To
    • Holt-Oram syndrome
    • Klippel-Trenaunay-Weber syndrome
    • Nail patella syndrome
    • Rubinstein-Taybi syndrome
    • Sirenomelia syndrome
    • Thrombocytopenia with absent radius [TAR] syndrome
    • VATER syndrome
    Q87.2
    )
The following code(s) above D69.42 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to D69.42:
  • D50-D89
    2018 ICD-10-CM Range D50-D89

    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

    Type 2 Excludes
    • autoimmune disease (systemic) NOS (M35.9)
    • certain conditions originating in the perinatal period (P00-P96)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • human immunodeficiency virus [HIV] disease (B20)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
  • D69
    ICD-10-CM Diagnosis Code D69

    Purpura and other hemorrhagic conditions

      2016 2017 2018 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • benign hypergammaglobulinemic purpura (D89.0)
    • cryoglobulinemic purpura (D89.1)
    • essential (hemorrhagic) thrombocythemia (D47.3)
    • hemorrhagic thrombocythemia (D47.3)
    • purpura fulminans (D65)
    • thrombotic thrombocytopenic purpura (M31.1)
    • Waldenström hypergammaglobulinemic purpura (D89.0)
    Purpura and other hemorrhagic conditions
  • D69.4
    ICD-10-CM Diagnosis Code D69.4

    Other primary thrombocytopenia

      2016 2017 2018 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • transient neonatal thrombocytopenia (P61.0)
    • Wiskott-Aldrich syndrome (D82.0)
    Other primary thrombocytopenia
Approximate Synonyms ICD-10-CM D69.42 is grouped within Diagnostic Related Group(s) (MS-DRG v35.0):

Convert D69.42 to ICD-9-CM

Code History

Diagnosis Index entries containing back-references to D69.42:

ICD-10-CM Codes Adjacent To D69.42
D68.69 Other thrombophilia
D68.8 Other specified coagulation defects
D68.9 Coagulation defect, unspecified
D69 Purpura and other hemorrhagic conditions
D69.0 Allergic purpura
D69.1 Qualitative platelet defects
D69.2 Other nonthrombocytopenic purpura
D69.3 Immune thrombocytopenic purpura
D69.4 Other primary thrombocytopenia
D69.41 Evans syndrome
D69.42 Congenital and hereditary thrombocytopenia purpura
D69.49 Other primary thrombocytopenia
D69.5 Secondary thrombocytopenia
D69.51 Posttransfusion purpura
D69.59 Other secondary thrombocytopenia
D69.6 Thrombocytopenia, unspecified
D69.8 Other specified hemorrhagic conditions
D69.9 Hemorrhagic condition, unspecified
D70 Neutropenia
D70.0 Congenital agranulocytosis
D70.1 Agranulocytosis secondary to cancer chemotherapy

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.