2017/18 ICD-10-CM Diagnosis Code D76.1

Hemophagocytic lymphohistiocytosis

Applicable To
  • Familial hemophagocytic reticulosis
  • Histiocytoses of mononuclear phagocytes
The following code(s) above D76.1 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to D76.1:
  • D50-D89
    2018 ICD-10-CM Range D50-D89

    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

    Type 2 Excludes
    • autoimmune disease (systemic) NOS (M35.9)
    • certain conditions originating in the perinatal period (P00-P96)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • human immunodeficiency virus [HIV] disease (B20)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
  • D76
    ICD-10-CM Diagnosis Code D76

    Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue

      2016 2017 2018 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • (Abt-) Letterer-Siwe disease (C96.0)
    • eosinophilic granuloma (C96.6)
    • Hand-Schüller-Christian disease (C96.5)
    • histiocytic medullary reticulosis (C96.9)
    • histiocytic sarcoma (C96.A)
    • histiocytosis X, multifocal (C96.5)
    • histiocytosis X, unifocal (C96.6)
    • Langerhans-cell histiocytosis, multifocal (C96.5)
    • Langerhans-cell histiocytosis NOS (C96.6)
    • Langerhans-cell histiocytosis, unifocal (C96.6)
    • leukemic reticuloendotheliosis (C91.4-)
    • lipomelanotic reticulosis (I89.8)
    • malignant histiocytosis (C96.A)
    • malignant reticulosis (C86.0)
    • nonlipid reticuloendotheliosis (C96.0)
    Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue
Approximate Synonyms Clinical Information ICD-10-CM D76.1 is grouped within Diagnostic Related Group(s) (MS-DRG v35.0):

Convert D76.1 to ICD-9-CM

Code History

Diagnosis Index entries containing back-references to D76.1:

ICD-10-CM Codes Adjacent To D76.1
D74.9 Methemoglobinemia, unspecified
D75 Other and unspecified diseases of blood and blood-forming organs
D75.0 Familial erythrocytosis
D75.1 Secondary polycythemia
D75.8 Other specified diseases of blood and blood-forming organs
D75.81 Myelofibrosis
D75.82 Heparin induced thrombocytopenia (HIT)
D75.89 Other specified diseases of blood and blood-forming organs
D75.9 Disease of blood and blood-forming organs, unspecified
D76 Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue
D76.1 Hemophagocytic lymphohistiocytosis
D76.2 Hemophagocytic syndrome, infection-associated
D76.3 Other histiocytosis syndromes
D77 Other disorders of blood and blood-forming organs in diseases classified elsewhere
D78 Intraoperative and postprocedural complications of the spleen
D78.0 Intraoperative hemorrhage and hematoma of the spleen complicating a procedure
D78.01 …… on the spleen
D78.02 Intraoperative hemorrhage and hematoma of the spleen complicating other procedure
D78.1 Accidental puncture and laceration of the spleen during a procedure
D78.11 …… on the spleen
D78.12 Accidental puncture and laceration of the spleen during other procedure

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.