Specific code icon 2017 ICD-10-CM Diagnosis Code E71.311

Medium chain acyl CoA dehydrogenase deficiency

    2016 2017 Billable/Specific Code

  • E71.311 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • This is the American ICD-10-CM version of E71.311. Other international versions of ICD-10 E71.311 may differ.
  • Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

Clinical Information
  • A genetic disorder characterized by deficiency of the enzyme medium-chain acyl-coenzyme a dehydrogenase that metabolizes medium-chain fatty acids. Signs and symptoms appear in infancy or childhood and may be triggered during fasting or illness. They include vomiting, hypoglycemia and lethargy.
Applicable To
  • MCAD
Approximate Synonyms
  • Fatty acid oxidation disorder
  • Medium chain acyl-coa dehydrogenase deficiency
  • Medium-chain acyl-coenzyme A dehydrogenase deficiency
ICD-10-CM E71.311 is grouped within Diagnostic Related Group (MS-DRG v34.0):
  • 642 Inborn and other disorders of metabolism

Convert ICD-10-CM E71.311 to ICD-9-CM

The following ICD-10-CM Index entries contain back-references to ICD-10-CM E71.311: