Specific code icon 2014 ICD-10-CM Diagnosis Code E71.311

Medium chain acyl CoA dehydrogenase deficiency

  • E71.311 is a billable ICD-10-CM code that can be used to specify a diagnosis.
  • On October 1, 2015 ICD-10-CM will replace ICD-9-CM in the United States, therefore, E71.311 and all other ICD-10-CM codes should only be used for training or planning purposes until then.
Clinical Information
  • A genetic disorder characterized by deficiency of the enzyme medium-chain acyl-coenzyme a dehydrogenase that metabolizes medium-chain fatty acids. Signs and symptoms appear in infancy or childhood and may be triggered during fasting or illness. They include vomiting, hypoglycemia and lethargy.
Applicable To
  • MCAD
Description Synonyms
  • Fatty acid oxidation disorder
  • Medium chain acyl-coa dehydrogenase deficiency
  • Medium-chain acyl-coenzyme A dehydrogenase deficiency
ICD-10-CM E71.311 is grouped within Diagnostic Related Group (MS-DRG v30.0):
  • 642 Inborn and other disorders of metabolism
Convert ICD-10-CM E71.311 to ICD-9-CM
The following ICD-10-CM Index entries contain back-references to ICD-10-CM E71.311: