Home > 2014 ICD-10-CM Diagnosis Codes > Endocrine, nutritional and metabolic diseases E00-E89 > Metabolic disorders E70-E88 > Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism E71-
2014 ICD-10-CM Diagnosis Code E71.311
Medium chain acyl CoA dehydrogenase deficiency
E71.311 is a billable ICD-10-CM code that can be used to specify a diagnosis.
On October 1, 2014 ICD-10-CM will replace ICD-9-CM in the United States, therefore, E71.311 and all other ICD-10-CM codes should only be used for training or planning purposes until then.
A genetic disorder characterized by deficiency of the enzyme medium-chain acyl-coenzyme a dehydrogenase that metabolizes medium-chain fatty acids. Signs and symptoms appear in infancy or childhood and may be triggered during fasting or illness. They include vomiting, hypoglycemia and lethargy.
Fatty acid oxidation disorder
Medium chain acyl-coa dehydrogenase deficiency
Medium-chain acyl-coenzyme A dehydrogenase deficiency
ICD-10-CM E71.311 is grouped within Diagnostic Related Group (MS-DRG v30.0):