Home > 2016 ICD-10-CM Diagnosis Codes > Endocrine, nutritional and metabolic diseases E00-E89 > Metabolic disorders E70-E88 > Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism E71-
2016 ICD-10-CM Diagnosis Code E71.311
Medium chain acyl CoA dehydrogenase deficiency
E71.311 is a specific ICD-10-CM code that can be used to specify a diagnosis.
Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.
This is the American ICD-10-CM version of E71.311. Other international ICD-10 versions may differ.
A genetic disorder characterized by deficiency of the enzyme medium-chain acyl-coenzyme a dehydrogenase that metabolizes medium-chain fatty acids. Signs and symptoms appear in infancy or childhood and may be triggered during fasting or illness. They include vomiting, hypoglycemia and lethargy.
Fatty acid oxidation disorder
Medium chain acyl-coa dehydrogenase deficiency
Medium-chain acyl-coenzyme A dehydrogenase deficiency
ICD-10-CM E71.311 is grouped within Diagnostic Related Group (MS-DRG v32.0):