Home > 2015 ICD-10-CM Diagnosis Codes > Endocrine, nutritional and metabolic diseases E00-E89 > Metabolic disorders E70-E88 > Disorders of glycosaminoglycan metabolism E76-
2015 ICD-10-CM Diagnosis Code E76.01
E76.01 is a billable ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
On October 1, 2015 ICD-10-CM will replace ICD-9-CM in the United States, therefore, E76.01 - and all other ICD-10-CM codes - should only be used for training or planning purposes until then.
This is the American ICD-10-CM version of E76.01. Other international ICD-10 versions may differ.
An autosomal recessive inherited disorder of mucopolysaccharide metabolism. It is the most severe form of mucopolysaccharidosis type i. It is characterized by deficiency of the enzyme alpha-l-iduronidase resulting in the accumulation of mucopolysaccharides in the tissues.
ICD-10-CM E76.01 is grouped within Diagnostic Related Group (MS-DRG v30.0):