Specific code icon 2017 ICD-10-CM Diagnosis Code E76.01

Hurler's syndrome

    2016 2017 Billable/Specific Code

  • E76.01 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • This is the American ICD-10-CM version of E76.01. Other international versions of ICD-10 E76.01 may differ.
  • Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

Clinical Information
  • An autosomal recessive inherited disorder of mucopolysaccharide metabolism. It is the most severe form of mucopolysaccharidosis type i. It is characterized by deficiency of the enzyme alpha-l-iduronidase resulting in the accumulation of mucopolysaccharides in the tissues.
Approximate Synonyms
  • Mucopolysaccharidosis MPS-I-H
ICD-10-CM E76.01 is grouped within Diagnostic Related Group (MS-DRG v34.0):
  • 642 Inborn and other disorders of metabolism

Convert ICD-10-CM E76.01 to ICD-9-CM

The following ICD-10-CM Index entries contain back-references to ICD-10-CM E76.01: