2017/18 ICD-10-CM Diagnosis Code G11.3

Cerebellar ataxia with defective DNA repair

Applicable To
  • Ataxia telangiectasia [Louis-Bar]
Type 2 Excludes
Type 2 Excludes Help
A type 2 excludes note represents "not included here". A type 2 excludes note indicates that the condition excluded is not part of the condition it is excluded from but a patient may have both conditions at the same time. When a type 2 excludes note appears under a code it is acceptable to use both the code (G11.3) and the excluded code together.
  • Cockayne's syndrome (
    ICD-10-CM Diagnosis Code Q87.1

    Congenital malformation syndromes predominantly associated with short stature

      2016 2017 2018 Billable/Specific Code POA Exempt
    Applicable To
    • Aarskog syndrome
    • Cockayne syndrome
    • De Lange syndrome
    • Dubowitz syndrome
    • Noonan syndrome
    • Prader-Willi syndrome
    • Robinow-Silverman-Smith syndrome
    • Russell-Silver syndrome
    • Seckel syndrome
    Type 1 Excludes
    • Ellis-van Creveld syndrome (Q77.6)
    • Smith-Lemli-Opitz syndrome (E78.72)
    Q87.1
    )
  • other disorders of purine and pyrimidine metabolism (
    ICD-10-CM Diagnosis Code E79
    • E79 Disorders of purine and pyrimidine metabolism...
      • E79.0 Hyperuricemia without signs of inflammatory a...
      • E79.1 Lesch-Nyhan syndrome
      • E79.2 Myoadenylate deaminase deficiency
      • E79.8 Other disorders of purine and pyrimidine meta...
      • E79.9 Disorder of purine and pyrimidine metabolism,...
    E79.-
    )
  • xeroderma pigmentosum (
    ICD-10-CM Diagnosis Code Q82.1

    Xeroderma pigmentosum

      2016 2017 2018 Billable/Specific Code POA Exempt
    Q82.1
    )
The following code(s) above G11.3 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to G11.3:
  • G00-G99
    2018 ICD-10-CM Range G00-G99

    Diseases of the nervous system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the nervous system
  • G11
    ICD-10-CM Diagnosis Code G11

    Hereditary ataxia

      2016 2017 2018 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • cerebral palsy (G80.-)
    • hereditary and idiopathic neuropathy (G60.-)
    • metabolic disorders (E70-E88)
    Hereditary ataxia
Approximate Synonyms ICD-10-CM G11.3 is grouped within Diagnostic Related Group(s) (MS-DRG v35.0):

Convert G11.3 to ICD-9-CM

Code History
Code annotations containing back-references to G11.3:

Diagnosis Index entries containing back-references to G11.3:

ICD-10-CM Codes Adjacent To G11.3
G06.1 Intraspinal abscess and granuloma
G06.2 Extradural and subdural abscess, unspecified
G07 Intracranial and intraspinal abscess and granuloma in diseases classified elsewhere
G08 Intracranial and intraspinal phlebitis and thrombophlebitis
G09 Sequelae of inflammatory diseases of central nervous system
G10 Huntington's disease
G11 Hereditary ataxia
G11.0 Congenital nonprogressive ataxia
G11.1 Early-onset cerebellar ataxia
G11.2 Late-onset cerebellar ataxia
G11.3 Cerebellar ataxia with defective DNA repair
G11.4 Hereditary spastic paraplegia
G11.8 Other hereditary ataxias
G11.9 Hereditary ataxia, unspecified
G12 Spinal muscular atrophy and related syndromes
G12.0 Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]
G12.1 Other inherited spinal muscular atrophy
G12.2 Motor neuron disease
G12.20 …… unspecified
G12.21 Amyotrophic lateral sclerosis
G12.22 Progressive bulbar palsy

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.