Specific code icon 2014 ICD-10-CM Diagnosis Code G60.0

Hereditary motor and sensory neuropathy

  • G60.0 is a billable ICD-10-CM code that can be used to specify a diagnosis.
  • On October 1, 2015 ICD-10-CM will replace ICD-9-CM in the United States, therefore, G60.0 and all other ICD-10-CM codes should only be used for training or planning purposes until then.
Clinical Information
  • A group of slowly progressive inherited disorders affecting motor and sensory peripheral nerves. Subtypes include hmsns i-vii. Hmsn i and ii both refer to charcot-marie-tooth disease. Hmsn iii refers to hypertrophic neuropathy of infancy. Hmsn iv refers to refsum disease. Hmsn v refers to a condition marked by a hereditary motor and sensory neuropathy associated with spastic paraplegia (see spastic paraplegia, hereditary). Hmsn vi refers to hmsn associated with an inherited optic atrophy (optic atrophies, hereditary), and hmsn vii refers to hmsn associated with retinitis pigmentosa. (from Adams et al., Principles of Neurology, 6th ed, p1343)
  • A hereditary motor and sensory neuropathy transmitted most often as an autosomal dominant trait and characterized by progressive distal wasting and loss of reflexes in the muscles of the legs (and occasionally involving the arms). Onset is usually in the second to fourth decade of life. This condition has been divided into two subtypes, hereditary motor and sensory neuropathy (hmsn) types i and ii. Hmsn i is associated with abnormal nerve conduction velocities and nerve hypertrophy, features not seen in hmsn ii. (Adams et al., Principles of Neurology, 6th ed, p1343)
  • A progressive hereditary disorder that causes nerve damage
  • An inherited degenerative disorder involving the peripheral nerves. It is caused by mutations in the genes that are responsible for the production of proteins necessary for the function and structure of the peripheral nerves. It is characterized by muscle atrophy and weakness in the feet, legs, hands, and arms and loss of sensation in the limbs.
  • Charcot-marie-tooth disease (cmt) is a group of genetic nerve disorders. It is named after the three doctors who first identified it. In the United States, cmt affects about 1 in 3,300 people. Cmt affects your peripheral nerves. Peripheral nerves carry movement and sensation signals between the brain and spinal cord and the rest of the body. Symptoms usually start around the teen years. Foot problems such as high arches or hammertoes can be early symptoms. As cmt progresses, your lower legs may weaken. Later, your hands may also become weak. There is no cure. The disease can be so mild you don't realize you have it or severe enough to make you weak. Many people with cmt lead active lives and have a normal life span. Physical therapy, occupational therapy, braces and other devices and sometimes surgery can help you cope. genetics home reference
  • Group of peripheral nervous system hereditary disorders with varying course, symptoms, neuropathology, and genetics, but generally involving gradual loss of nerve conduction, distal wasting, deformity, and disability.
Applicable To
  • Charcot-Marie-Tooth disease
  • Déjérine-Sottas disease
  • Hereditary motor and sensory neuropathy, types I-IV
  • Hypertrophic neuropathy of infancy
  • Peroneal muscular atrophy (axonal type) (hypertrophic type)
  • Roussy-Levy syndrome
Description Synonyms
  • Charcot Marie Tooth disease
  • Charcot Marie Tooth disease type 1
  • Charcot Marie Tooth disease, Type 2
  • Charcot Marie Tooth disease, Type 3
  • Charcot Marie Tooth disease, Type 4
  • Charcot-Marie-Tooth disease type 4
  • Charcot-Marie-Tooth disease, type 3
  • Charcot-Marie-Tooth disease, type I
  • Charcot-Marie-Tooth disease, type II
  • Dejerine Sottas disease
  • Hereditary motor and sensory neuropathy with optic atrophy
  • Hereditary motor and sensory neuropathy, w optic atrophy
  • Neuropathy (nerve damage) hereditary motor and sensory
Mortality Data
  • Between 1999-2007 there were 451 deaths in the United States where ICD-10 G60.0 was indicated as the underlying cause of death [source: cdc.govlink to cdc.gov]
  • ICD-10 G60.0 as underlying cause of death data broken down by: gender, age, race, year
ICD-10-CM G60.0 is grouped within Diagnostic Related Group(s) (MS-DRG v30.0):
  • 073 Cranial & peripheral nerve disorders with mcc
  • 074 Cranial & peripheral nerve disorders without mcc
Convert ICD-10-CM G60.0 to ICD-9-CM
The following ICD-10-CM Index entries contain back-references to ICD-10-CM G60.0:
  • Ataxia, ataxy, ataxic R27.0
  • Roussy-Lévy G60.0
  • Atrophy, atrophic (of)
  • Charcot-Marie-Tooth G60.0
    muscle, muscular (diffuse) (general) (idiopathic) (primary) M62.50
    neuropathic (peroneal) (progressive) G60.0
    peroneal G60.0
  • Charcot-Marie-Tooth disease, paralysis or syndrome G60.0
  • Curvature
  • spine (acquired) (angular) (idiopathic) (incorrect) (postural) - see Dorsopathy, deforming
    due to or associated with
    Charcot-Marie-Tooth disease - see also subcategory M49.8 G60.0
  • Déjérine-Sottas disease or neuropathy (hypertrophic) G60.0
  • Dystrophy, dystrophia
  • muscular G71.0
    progressive (hereditary) G71.0
    Charcot-Marie (-Tooth) G60.0
  • Marie-Charcot-Tooth neuropathic muscular atrophy G60.0
  • Neuritis (rheumatoid) M79.2
  • Déjérine-Sottas G60.0
    interstitial hypertrophic progressive G60.0
    progressive hypertrophic interstitial G60.0
  • Neuropathy, neuropathic G62.9
  • Déjérine-Sottas G60.0
    hypertrophic G60.0
    Charcot-Marie-Tooth G60.0
    Déjérine-Sottas G60.0
    interstitial progressive G60.0
    of infancy G60.0
    hereditary G60.9
    motor and sensory (types I-IV) G60.0
    motor and sensory - see also Polyneuropathy
    hereditary (types I-IV) G60.0
    progressive
    hypertrophic interstitial G60.0
  • Paralysis, paralytic (complete) (incomplete) G83.9
  • Charcot-Marie-Tooth type G60.0
  • Roussy-Lévy syndrome G60.0