Home > 2014 ICD-10-CM Diagnosis Codes > Diseases of the nervous system G00-G99 > Polyneuropathies and other disorders of the peripheral nervous system G60-G65 > Hereditary and idiopathic neuropathy G60-
2014 ICD-10-CM Diagnosis Code G60.0
Hereditary motor and sensory neuropathy
G60.0 is a billable ICD-10-CM code that can be used to specify a diagnosis.
On October 1, 2014 ICD-10-CM will replace ICD-9-CM in the United States, therefore, G60.0 and all other ICD-10-CM codes should only be used for training or planning purposes until then.
A group of slowly progressive inherited disorders affecting motor and sensory peripheral nerves. Subtypes include hmsns i-vii. Hmsn i and ii both refer to charcot-marie-tooth disease. Hmsn iii refers to hypertrophic neuropathy of infancy. Hmsn iv refers to refsum disease. Hmsn v refers to a condition marked by a hereditary motor and sensory neuropathy associated with spastic paraplegia (see spastic paraplegia, hereditary). Hmsn vi refers to hmsn associated with an inherited optic atrophy (optic atrophies, hereditary), and hmsn vii refers to hmsn associated with retinitis pigmentosa. (from Adams et al., Principles of Neurology, 6th ed, p1343)
A hereditary motor and sensory neuropathy transmitted most often as an autosomal dominant trait and characterized by progressive distal wasting and loss of reflexes in the muscles of the legs (and occasionally involving the arms). Onset is usually in the second to fourth decade of life. This condition has been divided into two subtypes, hereditary motor and sensory neuropathy (hmsn) types i and ii. Hmsn i is associated with abnormal nerve conduction velocities and nerve hypertrophy, features not seen in hmsn ii. (Adams et al., Principles of Neurology, 6th ed, p1343)
A progressive hereditary disorder that causes nerve damage
An inherited degenerative disorder involving the peripheral nerves. It is caused by mutations in the genes that are responsible for the production of proteins necessary for the function and structure of the peripheral nerves. It is characterized by muscle atrophy and weakness in the feet, legs, hands, and arms and loss of sensation in the limbs.
Charcot-marie-tooth disease (cmt) is a group of genetic nerve disorders. It is named after the three doctors who first identified it. In the United States, cmt affects about 1 in 3,300 people. Cmt affects your peripheral nerves. Peripheral nerves carry movement and sensation signals between the brain and spinal cord and the rest of the body. Symptoms usually start around the teen years. Foot problems such as high arches or hammertoes can be early symptoms. As cmt progresses, your lower legs may weaken. Later, your hands may also become weak. There is no cure. The disease can be so mild you don't realize you have it or severe enough to make you weak. Many people with cmt lead active lives and have a normal life span. Physical therapy, occupational therapy, braces and other devices and sometimes surgery can help you cope. genetics home reference
Group of peripheral nervous system hereditary disorders with varying course, symptoms, neuropathology, and genetics, but generally involving gradual loss of nerve conduction, distal wasting, deformity, and disability.
Hereditary motor and sensory neuropathy, types I-IV