2017/18 ICD-10-CM Diagnosis Code I27.0

Primary pulmonary hypertension

Applicable To
  • Heritable pulmonary arterial hypertension
  • Idiopathic pulmonary arterial hypertension
  • Primary group 1 pulmonary hypertension
  • Primary pulmonary arterial hypertension
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as I27.0. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • persistent pulmonary hypertension of newborn (
    ICD-10-CM Diagnosis Code P29.30

    Pulmonary hypertension of newborn

      2018 - New Code Billable/Specific Code Code on Newborn Record POA Exempt
    Applicable To
    • Persistent pulmonary hypertension of newborn
    P29.30
    )
  • pulmonary hypertension NOS (
    ICD-10-CM Diagnosis Code I27.20

    Pulmonary hypertension, unspecified

      2018 - New Code Billable/Specific Code
    Applicable To
    • Pulmonary hypertension NOS
    I27.20
    )
  • secondary pulmonary arterial hypertension (
    ICD-10-CM Diagnosis Code I27.21

    Secondary pulmonary arterial hypertension

      2018 - New Code Billable/Specific Code
    Applicable To
    • (Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
    • (Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension
    Code Also
    • associated conditions if applicable, or adverse effects of drugs or toxins, such as:
    • adverse effect of appetite depressants (T50.5X5)
    • congenital heart disease (Q20-Q28)
    • human immunodeficiency virus [HIV] disease (B20)
    • polymyositis (M33.2-)
    • portal hypertension (K76.6)
    • rheumatoid arthritis (M05.-)
    • schistosomiasis (B65.-)
    • Sjögren syndrome (M35.0-)
    • systemic sclerosis (M34.-)
    I27.21
    )
  • secondary pulmonary hypertension (
    ICD-10-CM Diagnosis Code I27.29

    Other secondary pulmonary hypertension

      2018 - New Code Billable/Specific Code
    Applicable To
    • Group 5 pulmonary hypertension
    • Pulmonary hypertension with unclear multifactorial mechanisms
    • Pulmonary hypertension due to hematologic disorders
    • Pulmonary hypertension due to metabolic disorders
    • Pulmonary hypertension due to other systemic disorders
    Code Also
    • other associated disorders, if known, such as:
    • chronic myeloid leukemia (C92.10- C92.22)
    • essential thrombocythemia (D47.3)
    • Gaucher disease (E75.22)
    • hypertensive chronic kidney disease with end stage renal disease (I12.0, I12.11, I13.2)
    • hyperthyroidism (E05.-)
    • hypothyroidism (E00-E03)
    • polycythemia vera (D45)
    • sarcoidosis (D86.-)
    I27.29
    )
The following code(s) above I27.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to I27.0:
  • I00-I99
    2018 ICD-10-CM Range I00-I99

    Diseases of the circulatory system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    • systemic connective tissue disorders (M30-M36)
    • transient cerebral ischemic attacks and related syndromes (G45.-)
    Diseases of the circulatory system
Approximate Synonyms Clinical Information ICD-10-CM I27.0 is grouped within Diagnostic Related Group(s) (MS-DRG v35.0):

Convert I27.0 to ICD-9-CM

Code History
Code annotations containing back-references to I27.0:

Diagnosis Index entries containing back-references to I27.0:

ICD-10-CM Codes Adjacent To I27.0
I26 Pulmonary embolism
I26.0 Pulmonary embolism with acute cor pulmonale
I26.01 Septic pulmonary embolism with acute cor pulmonale
I26.02 Saddle embolus of pulmonary artery with acute cor pulmonale
I26.09 Other pulmonary embolism with acute cor pulmonale
I26.9 Pulmonary embolism without acute cor pulmonale
I26.90 Septic pulmonary embolism without acute cor pulmonale
I26.92 Saddle embolus of pulmonary artery without acute cor pulmonale
I26.99 Other pulmonary embolism without acute cor pulmonale
I27 Other pulmonary heart diseases
I27.0 Primary pulmonary hypertension
I27.1 Kyphoscoliotic heart disease
I27.2 Other secondary pulmonary hypertension
I27.20 Pulmonary hypertension, unspecified
I27.21 Secondary pulmonary arterial hypertension
I27.22 Pulmonary hypertension due to left heart disease
I27.23 Pulmonary hypertension due to lung diseases and hypoxia
I27.24 Chronic thromboembolic pulmonary hypertension
I27.29 Other secondary pulmonary hypertension
I27.8 Other specified pulmonary heart diseases
I27.81 Cor pulmonale (chronic)

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.