Endocarditis and heart valve disorders in diseases classified elsewhere I39- >

Code First
Code First Help
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
  • underlying disease, such as:
  • Q fever (
    ICD-10-CM Diagnosis Code A78

    Q fever

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Infection due to Coxiella burnetii
    • Nine Mile fever
    • Quadrilateral fever
    A78
    )
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as I39. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • endocardial involvement in:
  • candidiasis (
    ICD-10-CM Diagnosis Code B37.6

    Candidal endocarditis

      2016 2017 2018 Billable/Specific Code
    B37.6
    )
  • gonococcal infection (
    ICD-10-CM Diagnosis Code A54.83

    Gonococcal heart infection

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Gonococcal endocarditis
    • Gonococcal myocarditis
    • Gonococcal pericarditis
    A54.83
    )
  • Libman-Sacks disease (
    ICD-10-CM Diagnosis Code M32.11

    Endocarditis in systemic lupus erythematosus

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Libman-Sacks disease
    M32.11
    )
  • listerosis (
    ICD-10-CM Diagnosis Code A32.82

    Listerial endocarditis

      2016 2017 2018 Billable/Specific Code
    A32.82
    )
  • meningococcal infection (
    ICD-10-CM Diagnosis Code A39.51

    Meningococcal endocarditis

      2016 2017 2018 Billable/Specific Code
    A39.51
    )
  • rheumatoid arthritis (
    ICD-10-CM Diagnosis Code M05.31

    Rheumatoid heart disease with rheumatoid arthritis of shoulder

      2016 2017 2018 Non-Billable/Non-Specific Code
    M05.31
    )
  • syphilis (
    ICD-10-CM Diagnosis Code A52.03

    Syphilitic endocarditis

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Syphilitic aortic valve incompetence or stenosis
    • Syphilitic mitral valve stenosis
    • Syphilitic pulmonary valve regurgitation
    A52.03
    )
  • tuberculosis (
    ICD-10-CM Diagnosis Code A18.84

    Tuberculosis of heart

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Tuberculous cardiomyopathy
    • Tuberculous endocarditis
    • Tuberculous myocarditis
    • Tuberculous pericarditis
    A18.84
    )
  • typhoid fever (
    ICD-10-CM Diagnosis Code A01.02

    Typhoid fever with heart involvement

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Typhoid endocarditis
    • Typhoid myocarditis
    A01.02
    )
Codes