Other heart disorders in diseases classified elsewhere I52- >

Code First
Code First Help
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
  • underlying disease, such as:
  • congenital syphilis (
    ICD-10-CM Diagnosis Code A50.5

    Other late congenital syphilis, symptomatic

      2016 2017 2018 Non-Billable/Non-Specific Code
    Applicable To
    • Any congenital syphilitic condition specified as late or manifest two years or more after birth.
    A50.5
    )
  • mucopolysaccharidosis (
    ICD-10-CM Diagnosis Code E76.3

    Mucopolysaccharidosis, unspecified

      2016 2017 2018 Billable/Specific Code
    E76.3
    )
  • schistosomiasis (
    ICD-10-CM Diagnosis Code B65.0

    Schistosomiasis due to Schistosoma haematobium [urinary schistosomiasis]

      2016 2017 2018 Billable/Specific Code
    B65.0-
    ICD-10-CM Diagnosis Code B65.9

    Schistosomiasis, unspecified

      2016 2017 2018 Billable/Specific Code
    B65.9
    )
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as I52. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • heart disease (in):
  • gonococcal infection (
    ICD-10-CM Diagnosis Code A54.83

    Gonococcal heart infection

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Gonococcal endocarditis
    • Gonococcal myocarditis
    • Gonococcal pericarditis
    A54.83
    )
  • meningococcal infection (
    ICD-10-CM Diagnosis Code A39.50

    Meningococcal carditis, unspecified

      2016 2017 2018 Billable/Specific Code
    A39.50
    )
  • rheumatoid arthritis (
    ICD-10-CM Diagnosis Code M05.31

    Rheumatoid heart disease with rheumatoid arthritis of shoulder

      2016 2017 2018 Non-Billable/Non-Specific Code
    M05.31
    )
  • syphilis (
    ICD-10-CM Diagnosis Code A52.06

    Other syphilitic heart involvement

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Syphilitic coronary artery disease
    • Syphilitic myocarditis
    • Syphilitic pericarditis
    A52.06
    )
Codes