Home > 2017 ICD-10-CM Diagnosis Codes > Diseases of the circulatory system I00-I99 > Diseases of arteries, arterioles and capillaries I70-I79 > Diseases of capillaries I78-
2017 ICD-10-CM Diagnosis Code I78.0
Hereditary hemorrhagic telangiectasia
I78.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
This is the American ICD-10-CM version of I78.0. Other international versions of ICD-10 I78.0 may differ.
Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.
An autosomal dominant hereditary disorder caused by mutations in the acvrl1, eng, and smad4 genes. It is characterized by the presence of telangiectasias in the skin, mucous membranes, lungs, brain, liver, and gastrointestinal tract. It results in hemorrhages from the affected areas.
An autosomal dominant vascular anomaly characterized by telangiectases of the skin and mucous membranes and by recurrent gastrointestinal bleeding. This disorder is caused by mutations of a gene (on chromosome 9q3) which encodes endoglin, a membrane glycoprotein that binds transforming growth factor beta.
ICD-10-CM I78.0 is grouped within Diagnostic Related Group(s) (MS-DRG v34.0):