Respiratory disorders in diseases classified elsewhere J99- >

Code First
Code First Help
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
  • underlying disease, such as:
  • amyloidosis (
    ICD-10-CM Diagnosis Code E85
    • E85 Amyloidosis
      • E85.0 Non-neuropathic heredofamilial amyloidosis
      • E85.1 Neuropathic heredofamilial amyloidosis
      • E85.2 Heredofamilial amyloidosis, unspecified
      • E85.3 Secondary systemic amyloidosis
      • E85.4 Organ-limited amyloidosis
      • E85.8 Other amyloidosis
        • E85.81 Light chain (AL) amyloidosis
        • E85.82 Wild-type transthyretin-related (ATTR) amyloi...
        • E85.89 Other amyloidosis
      • E85.9 Amyloidosis, unspecified
    E85.-
    )
  • ankylosing spondylitis (
    ICD-10-CM Diagnosis Code M45

    Ankylosing spondylitis

      2016 2017 2018 Non-Billable/Non-Specific Code
    Applicable To
    • Rheumatoid arthritis of spine
    Type 1 Excludes
    • arthropathy in Reiter's disease (M02.3-)
    • juvenile (ankylosing) spondylitis (M08.1)
    Type 2 Excludes
    • Behçet's disease (M35.2)
    M45
    )
  • congenital syphilis (
    ICD-10-CM Diagnosis Code A50.5

    Other late congenital syphilis, symptomatic

      2016 2017 2018 Non-Billable/Non-Specific Code
    Applicable To
    • Any congenital syphilitic condition specified as late or manifest two years or more after birth.
    A50.5
    )
  • cryoglobulinemia (
    ICD-10-CM Diagnosis Code D89.1

    Cryoglobulinemia

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Cryoglobulinemic purpura
    • Cryoglobulinemic vasculitis
    • Essential cryoglobulinemia
    • Idiopathic cryoglobulinemia
    • Mixed cryoglobulinemia
    • Primary cryoglobulinemia
    • Secondary cryoglobulinemia
    D89.1
    )
  • early congenital syphilis (
    ICD-10-CM Diagnosis Code A50.0

    Early congenital syphilis, symptomatic

      2016 2017 2018 Non-Billable/Non-Specific Code
    Applicable To
    • Any congenital syphilitic condition specified as early or manifest less than two years after birth.
    A50.0
    )
  • schistosomiasis (
    ICD-10-CM Diagnosis Code B65.0

    Schistosomiasis due to Schistosoma haematobium [urinary schistosomiasis]

      2016 2017 2018 Billable/Specific Code
    B65.0-
    ICD-10-CM Diagnosis Code B65.9

    Schistosomiasis, unspecified

      2016 2017 2018 Billable/Specific Code
    B65.9
    )
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as J99. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • respiratory disorders in:
  • amebiasis (
    ICD-10-CM Diagnosis Code A06.5

    Amebic lung abscess

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Amebic abscess of lung (and liver)
    A06.5
    )
  • blastomycosis (
    ICD-10-CM Diagnosis Code B40.0

    Acute pulmonary blastomycosis

      2016 2017 2018 Billable/Specific Code
    B40.0-
    ICD-10-CM Diagnosis Code B40.2

    Pulmonary blastomycosis, unspecified

      2016 2017 2018 Billable/Specific Code
    B40.2
    )
  • candidiasis (
    ICD-10-CM Diagnosis Code B37.1

    Pulmonary candidiasis

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Candidal bronchitis
    • Candidal pneumonia
    B37.1
    )
  • coccidioidomycosis (
    ICD-10-CM Diagnosis Code B38.0

    Acute pulmonary coccidioidomycosis

      2016 2017 2018 Billable/Specific Code
    B38.0-
    ICD-10-CM Diagnosis Code B38.2

    Pulmonary coccidioidomycosis, unspecified

      2016 2017 2018 Billable/Specific Code
    B38.2
    )
  • cystic fibrosis with pulmonary manifestations (
    ICD-10-CM Diagnosis Code E84.0

    Cystic fibrosis with pulmonary manifestations

      2016 2017 2018 Billable/Specific Code
    Use Additional
    • code to identify any infectious organism present, such as:
    • Pseudomonas (B96.5)
    E84.0
    )
  • dermatomyositis (
    ICD-10-CM Diagnosis Code M33.01

    Juvenile dermatomyositis with respiratory involvement

      2016 2017 2018 - Revised Code Billable/Specific Code
    M33.01
    ,
    ICD-10-CM Diagnosis Code M33.11

    Other dermatomyositis with respiratory involvement

      2016 2017 2018 - Revised Code Billable/Specific Code
    M33.11
    )
  • histoplasmosis (
    ICD-10-CM Diagnosis Code B39.0

    Acute pulmonary histoplasmosis capsulati

      2016 2017 2018 Billable/Specific Code
    B39.0-
    ICD-10-CM Diagnosis Code B39.2

    Pulmonary histoplasmosis capsulati, unspecified

      2016 2017 2018 Billable/Specific Code
    B39.2
    )
  • late syphilis (
    ICD-10-CM Diagnosis Code A52.72

    Syphilis of lung and bronchus

      2016 2017 2018 Billable/Specific Code
    A52.72
    ,
    ICD-10-CM Diagnosis Code A52.73

    Symptomatic late syphilis of other respiratory organs

      2016 2017 2018 Billable/Specific Code
    A52.73
    )
  • polymyositis (
    ICD-10-CM Diagnosis Code M33.21

    Polymyositis with respiratory involvement

      2016 2017 2018 Billable/Specific Code
    M33.21
    )
  • sicca syndrome (
    ICD-10-CM Diagnosis Code M35.02

    Sicca syndrome with lung involvement

      2016 2017 2018 Billable/Specific Code
    M35.02
    )
  • systemic lupus erythematosus (
    ICD-10-CM Diagnosis Code M32.13

    Lung involvement in systemic lupus erythematosus

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Pleural effusion due to systemic lupus erythematosus
    M32.13
    )
  • systemic sclerosis (
    ICD-10-CM Diagnosis Code M34.81

    Systemic sclerosis with lung involvement

      2016 2017 2018 Billable/Specific Code
    M34.81
    )
  • Wegener's granulomatosis (
    ICD-10-CM Diagnosis Code M31.30

    Wegener's granulomatosis without renal involvement

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Wegener's granulomatosis NOS
    M31.30-
    ICD-10-CM Diagnosis Code M31.31

    Wegener's granulomatosis with renal involvement

      2016 2017 2018 Billable/Specific Code
    M31.31
    )
Codes