2017/18 ICD-10-CM Diagnosis Code K76.81

Hepatopulmonary syndrome

Code First
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Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
  • underlying liver disease, such as:
  • alcoholic cirrhosis of liver (
    ICD-10-CM Diagnosis Code K70.3

    Alcoholic cirrhosis of liver

      2016 2017 2018 Non-Billable/Non-Specific Code
    Applicable To
    • Alcoholic cirrhosis NOS
    K70.3-
    )
  • cirrhosis of liver without mention of alcohol (
    ICD-10-CM Diagnosis Code K74.6

    Other and unspecified cirrhosis of liver

      2016 2017 2018 Non-Billable/Non-Specific Code
    K74.6-
    )
The following code(s) above K76.81 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to K76.81:
  • K00-K95
    2018 ICD-10-CM Range K00-K95

    Diseases of the digestive system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the digestive system
  • K70-K77
    2018 ICD-10-CM Range K70-K77

    Diseases of liver

    Type 1 Excludes
    • jaundice NOS (R17)
    Type 2 Excludes
    Diseases of liver
  • K76
    ICD-10-CM Diagnosis Code K76

    Other diseases of liver

      2016 2017 2018 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • alcoholic liver disease (K70.-)
    • amyloid degeneration of liver (E85.-)
    • cystic disease of liver (congenital) (Q44.6)
    • hepatic vein thrombosis (I82.0)
    • hepatomegaly NOS (R16.0)
    • pigmentary cirrhosis (of liver) (E83.110)
    • portal vein thrombosis (I81)
    • toxic liver disease (K71.-)
    Other diseases of liver
Clinical Information ICD-10-CM K76.81 is grouped within Diagnostic Related Group(s) (MS-DRG v35.0):

Convert K76.81 to ICD-9-CM

Code History

Diagnosis Index entries containing back-references to K76.81:

ICD-10-CM Codes Adjacent To K76.81
K76 Other diseases of liver
K76.0 Fatty (change of) liver, not elsewhere classified
K76.1 Chronic passive congestion of liver
K76.2 Central hemorrhagic necrosis of liver
K76.3 Infarction of liver
K76.4 Peliosis hepatis
K76.5 Hepatic veno-occlusive disease
K76.6 Portal hypertension
K76.7 Hepatorenal syndrome
K76.8 Other specified diseases of liver
K76.81 Hepatopulmonary syndrome
K76.89 Other specified diseases of liver
K76.9 Liver disease, unspecified
K77 Liver disorders in diseases classified elsewhere
K80 Cholelithiasis
K80.0 Calculus of gallbladder with acute cholecystitis
K80.00 …… without obstruction
K80.01 …… with obstruction
K80.1 Calculus of gallbladder with other cholecystitis
K80.10 Calculus of gallbladder with chronic cholecystitis without obstruction
K80.11 Calculus of gallbladder with chronic cholecystitis with obstruction

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.