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ICD-10-CM Codes
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M00-M99
Diseases of the musculoskeletal system and connective tissue
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M04-M04
Autoinflammatory syndromes
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M04-
Autoinflammatory syndromes
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2021 ICD-10-CM Diagnosis Code M04.2
2021 ICD-10-CM Diagnosis Code M04.2
Cryopyrin-associated periodic syndromes
2017 - New Code 2018 2019 2020 2021 Billable/Specific Code
- M04.2 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
- The 2021 edition of ICD-10-CM M04.2 became effective on October 1, 2020.
- This is the American ICD-10-CM version of M04.2 - other international versions of ICD-10 M04.2 may differ.
Applicable To- Chronic infantile neurological, cutaneous and articular syndrome [CINCA]
- Familial cold autoinflammatory syndrome
- Familial cold urticaria
- Muckle-Wells syndrome
- Neonatal onset multisystemic inflammatory disorder [NOMID]
The following code(s) above
M04.2 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
- Applicable To annotations, or
- Code Also annotations, or
- Code First annotations, or
- Excludes1 annotations, or
- Excludes2 annotations, or
- Includes annotations, or
- Note annotations, or
- Use Additional annotations
that may be applicable to
M04.2:
Approximate Synonyms
- Cryopyrin associated periodic syndrome
ICD-10-CM M04.2 is grouped within Diagnostic Related Group(s) (MS-DRG v38.0):
- 545 Connective tissue disorders with mcc
- 546 Connective tissue disorders with cc
- 547 Connective tissue disorders without cc/mcc
Convert M04.2 to ICD-9-CM
Code History
- 2017 (effective 10/1/2016): New code
- 2018 (effective 10/1/2017): No change
- 2019 (effective 10/1/2018): No change
- 2020 (effective 10/1/2019): No change
- 2021 (effective 10/1/2020): No change
Code annotations containing back-references to M04.2:
- CINCA M04.2 (chronic infantile neurological, cutaneous and articular syndrome)
- Disorder (of) - see also Disease
- neonatal onset multisystemic inflammatory M04.2 (NOMID)
- NOMID M04.2 (neonatal onset multisystemic inflammatory disorder)
- Syndrome - see also Disease
- chronic
- infantile neurological, cutaneous and articular M04.2 (CINCA)
- cryopyrin-associated periodic M04.2
- familial cold autoinflammatory M04.2
- Muckle-Wells M04.2
- Urticaria L50.9
ICD-10-CM Diagnosis Code L50.9
Urticaria, unspecified
2016 2017 2018 2019 2020 2021 Billable/Specific Code
ICD-10-CM Codes Adjacent To M04.2
M02.869 Other reactive arthropathies, unspecified knee
M02.87 Other reactive arthropathies, ankle and foot
M02.871 Other reactive arthropathies, right ankle and foot
M02.872 Other reactive arthropathies, left ankle and foot
M02.879 Other reactive arthropathies, unspecified ankle and foot
M02.9 Reactive arthropathy, unspecified
M04 Autoinflammatory syndromes
M04.1 Periodic fever syndromes
M04.2
Cryopyrin-associated periodic syndromes
M04.8 Other autoinflammatory syndromes
M04.9 Autoinflammatory syndrome, unspecified
M05 Rheumatoid arthritis with rheumatoid factor
M05.01 Felty's syndrome, shoulder
M05.011 Felty's syndrome, right shoulder
M05.012 Felty's syndrome, left shoulder
M05.019 Felty's syndrome, unspecified shoulder
M05.02 Felty's syndrome, elbow
Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.