ICD-10-CM Codes
Q00-Q99 Congenital malformations of the nervous system
Congenital malformations of the nervous system Q00-Q07

Congenital malformations of the nervous system Q00-Q07

Codes

Q00
Anencephaly and similar malformations
Q01
Encephalocele
Q02
Microcephaly
Q03
Congenital hydrocephalus
Q04
Other congenital malformations of brain
Q05
Spina bifida
Q06
Other congenital malformations of spinal cord
Q07
Other congenital malformations of nervous system

ICD-10-CM Diagnosis Codes Q00-*

Q00 Anencephaly and similar malformations
- Q00.0 Anencephaly
- Q00.1 Craniorachischisis
- Q00.2 Iniencephaly

ICD-10-CM Diagnosis Codes Q01-*

Q01 Encephalocele
- Q01.0 Frontal encephalocele
- Q01.1 Nasofrontal encephalocele
- Q01.2 Occipital encephalocele
- Q01.8 Encephalocele of other sites
- Q01.9 Encephalocele, unspecified

ICD-10-CM Diagnosis Codes Q02-*

Q02 Microcephaly

ICD-10-CM Diagnosis Codes Q03-*

Q03 Congenital hydrocephalus
- Q03.0 Malformations of aqueduct of Sylvius
- Q03.1 Atresia of foramina of Magendie and Luschka
- Q03.8 Other congenital hydrocephalus
- Q03.9 Congenital hydrocephalus, unspecified

ICD-10-CM Diagnosis Codes Q04-*

Q04 Other congenital malformations of brain
- Q04.0 Congenital malformations of corpus callosum
- Q04.1 Arhinencephaly
- Q04.2 Holoprosencephaly
- Q04.3 Other reduction deformities of brain
- Q04.4 Septo-optic dysplasia of brain
- Q04.5 Megalencephaly
- Q04.6 Congenital cerebral cysts
- Q04.8 Other specified congenital malformations of b...
- Q04.9 Congenital malformation of brain, unspecified...

ICD-10-CM Diagnosis Codes Q05-*

Q05 Spina bifida
- Q05.0 Cervical spina bifida with hydrocephalus
- Q05.1 Thoracic spina bifida with hydrocephalus
- Q05.2 Lumbar spina bifida with hydrocephalus
- Q05.3 Sacral spina bifida with hydrocephalus
- Q05.4 Unspecified spina bifida with hydrocephalus
- Q05.5 Cervical spina bifida without hydrocephalus
- Q05.6 Thoracic spina bifida without hydrocephalus
- Q05.7 Lumbar spina bifida without hydrocephalus
- Q05.8 Sacral spina bifida without hydrocephalus
- Q05.9 Spina bifida, unspecified

ICD-10-CM Diagnosis Codes Q06-*

Q06 Other congenital malformations of spinal cord...
- Q06.0 Amyelia
- Q06.1 Hypoplasia and dysplasia of spinal cord
- Q06.2 Diastematomyelia
- Q06.3 Other congenital cauda equina malformations
- Q06.4 Hydromyelia
- Q06.8 Other specified congenital malformations of s...
- Q06.9 Congenital malformation of spinal cord, unspe...

ICD-10-CM Diagnosis Codes Q07-*

Q07 Other congenital malformations of nervous sys...
- Q07.0 Arnold-Chiari syndrome
  - Q07.00 Arnold-Chiari syndrome without spina bifida o...
  - Q07.01 …… with spina bifida
  - Q07.02 …… with hydrocephalus
  - Q07.03 Arnold-Chiari syndrome with spina bifida and ...
- Q07.8 Other specified congenital malformations of n...
- Q07.9 Congenital malformation of nervous system, un...

	Q00-Q99 ICD-10-CM Range Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities Q00-Q07 Congenital malformations of the nervous ... Q10-Q18 Congenital malformations of eye, ear, fa... Q20-Q28 Congenital malformations of the circulat... Q30-Q34 Congenital malformations of the respirat... Q35-Q37 Cleft lip and cleft palate Q38-Q45 Other congenital malformations of the di... Q50-Q56 Congenital malformations of genital orga... Q60-Q64 Congenital malformations of the urinary ... Q65-Q79 Congenital malformations and deformation... Q80-Q89 Other congenital malformations Q90-Q99 Chromosomal abnormalities, not elsewhere...
	ICD10Data.com	Q10-Q18 ICD-10-CM Range Q10-Q18 Congenital malformations of eye, ear, face and neck Type 2 Excludes cleft lip and cleft palate (Q35-Q37) congenital malformation of cervical spine (Q05.0, Q05.5, Q67.5, Q76.0-Q76.4) congenital malformation of larynx (Q31.-) congenital malformation of lip NEC (Q38.0) congenital malformation of nose (Q30.-) congenital malformation of parathyroid gland (Q89.2) congenital malformation of thyroid gland (Q89.2) Q10 Congenital malformations of eyelid, lacr... Q11 Anophthalmos, microphthalmos and macroph... Q12 Congenital lens malformations Q13 Congenital malformations of anterior seg... Q14 Congenital malformations of posterior se... Q15 Other congenital malformations of eye Q16 Congenital malformations of ear causing ... Q17 Other congenital malformations of ear Q18 Other congenital malformations of face a...
	R00-R99 ICD-10-CM Range R00-R99 Symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified R00-R09 Symptoms and signs involving the circula... R10-R19 Symptoms and signs involving the digesti... R20-R23 Symptoms and signs involving the skin an... R25-R29 Symptoms and signs involving the nervous... R30-R39 Symptoms and signs involving the genitou... R40-R46 Symptoms and signs involving cognition, ... R47-R49 Symptoms and signs involving speech and ... R50-R69 General symptoms and signs R70-R79 Abnormal findings on examination of bloo... R80-R82 Abnormal findings on examination of urin... R83-R89 Abnormal findings on examination of othe... R90-R94 Abnormal findings on diagnostic imaging ... R97-R97 Abnormal tumor markers R99-R99 Ill-defined and unknown cause of mortali...

Congenital malformations of the nervous system Q00-Q07

Congenital malformations, deformations and chromosomal abnormalities

Congenital malformations of eye, ear, face and neck

Symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified