Specific code icon 2015 ICD-10-CM Diagnosis Code Q00.0

Anencephaly

    2015 Billable Code POA Exempt

  • Q00.0 is a billable ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • On October 1, 2015 ICD-10-CM will replace ICD-9-CM in the United States, therefore, Q00.0 - and all other ICD-10-CM codes - should only be used for training or planning purposes until then.
  • This is the American ICD-10-CM version of Q00.0. Other international ICD-10 versions may differ.

Clinical Information
  • A malformation of the nervous system caused by failure of the anterior neuropore to close. Infants are born with intact spinal cords, cerebellums, and brainstems, but lack formation of neural structures above this level. The skull is only partially formed but the eyes are usually normal. This condition may be associated with folate deficiency. Affected infants are only capable of primitive (brain stem) reflexes and usually do not survive for more than two weeks. (from menkes, textbook of child neurology, 5th ed, p247)
  • A rare neural tube defect during pregnancy, resulting in the absence of a large portion of the brain and skull in the fetus.
  • Congenital absence of the spinal cord and brain
  • Congenital malformation of the nervous system caused by failure of the anterior neuropore to close; infants are born with intact spinal cords, cerebellums, and brainstems, but lack formation of neural structures above this level; the skull is only partially formed but the eyes are usually normal; affected infants are only capable of primitive reflexes and usually do not survive for more than two weeks; complete absence of the brain is rare.
Applicable To
  • Acephaly
  • Acrania
  • Amyelencephaly
  • Hemianencephaly
  • Hemicephaly
Description Synonyms
  • Amyelencephalus
  • Anencephalus
  • Brain aplasia, congenital
  • Congenital brain aplasia
Present On Admission
  • Q00.0 is considered exempt from POA reporting.
ICD-10-CM Q00.0 is grouped within Diagnostic Related Group(s) (MS-DRG v30.0):
  • 091 Other disorders of nervous system with mcc
  • 092 Other disorders of nervous system with cc
  • 093 Other disorders of nervous system without cc/mcc
  • 793 Full term neonate with major problems

Convert ICD-10-CM Q00.0 to ICD-9-CM

The following ICD-10-CM Index entries contain back-references to ICD-10-CM Q00.0: