Specific code icon 2017 ICD-10-CM Diagnosis Code Q43.1

Hirschsprung's disease

    2016 2017 Billable/Specific Code POA Exempt

  • Q43.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • This is the American ICD-10-CM version of Q43.1. Other international versions of ICD-10 Q43.1 may differ.
  • Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

Clinical Information
  • A congenital disorder characterized by the absence of myenteric ganglion cells in the distal colon. It results in a functional stenosis of the distal colon and a massive distention of the proximal colon.
  • Abnormally large or dilated colon due to congenital absence of myenteric ganglion cells in a distal segment of the large bowel; resultant loss of motor function in this segment causes massive hypertrophic dilatation of the normal proximal colon; condition appears soon after birth; called also hirschsprung's disease, aganglionic megacolon and pelvirectal achalasia.
  • Congenital megacolon resulting from the absence of ganglion cells (aganglionosis) in a distal segment of the large intestine. The aganglionic segment is permanently contracted thus causing dilatation proximal to it. In most cases, the aganglionic segment is within the rectum and sigmoid colon.
Applicable To
  • Aganglionosis
  • Congenital (aganglionic) megacolon
Approximate Synonyms
  • Congenital megacolon
  • Hirschsprungs disease
  • Megacolon, congenital
Present On Admission
  • Q43.1 is considered exempt from POA reporting.
ICD-10-CM Q43.1 is grouped within Diagnostic Related Group(s) (MS-DRG v34.0):
  • 393 Other digestive system diagnoses with mcc
  • 394 Other digestive system diagnoses with cc
  • 395 Other digestive system diagnoses without cc/mcc

Convert ICD-10-CM Q43.1 to ICD-9-CM

The following ICD-10-CM Index entries contain back-references to ICD-10-CM Q43.1: