DRG 198

Interstitial lung disease without cc/mcc

ICD-10-CM B44.81

Allergic bronchopulmonary aspergillosis

    2016 2017 2018 Billable/Specific Code
ICD-10-CM B90.9

Sequelae of respiratory and unspecified tuberculosis

    2016 2017 2018 Billable/Specific Code POA Exempt
Applicable To
  • Sequelae of tuberculosis NOS
ICD-10-CM D86.0

Sarcoidosis of lung

    2016 2017 2018 Billable/Specific Code
ICD-10-CM D86.1

Sarcoidosis of lymph nodes

    2016 2017 2018 Billable/Specific Code
ICD-10-CM D86.2

Sarcoidosis of lung with sarcoidosis of lymph nodes

    2016 2017 2018 Billable/Specific Code
ICD-10-CM D86.3

Sarcoidosis of skin

    2016 2017 2018 Billable/Specific Code
ICD-10-CM D86.81

Sarcoid meningitis

    2016 2017 2018 Billable/Specific Code
ICD-10-CM D86.82

Multiple cranial nerve palsies in sarcoidosis

    2016 2017 2018 Billable/Specific Code
ICD-10-CM D86.83

Sarcoid iridocyclitis

    2016 2017 2018 Billable/Specific Code
ICD-10-CM D86.84

Sarcoid pyelonephritis

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Tubulo-interstitial nephropathy in sarcoidosis
ICD-10-CM D86.85

Sarcoid myocarditis

    2016 2017 2018 Billable/Specific Code
ICD-10-CM D86.86

Sarcoid arthropathy

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Polyarthritis in sarcoidosis
ICD-10-CM D86.87

Sarcoid myositis

    2016 2017 2018 Billable/Specific Code
ICD-10-CM D86.89

Sarcoidosis of other sites

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Hepatic granuloma
  • Uveoparotid fever [Heerfordt]
ICD-10-CM D86.9

Sarcoidosis, unspecified

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J60

Coalworker's pneumoconiosis

    2016 2017 2018 Billable/Specific Code Adult Dx (15-124 years)
Applicable To
  • Anthracosilicosis
  • Anthracosis
  • Black lung disease
  • Coalworker's lung
Type 1 Excludes
  • coalworker pneumoconiosis with tuberculosis, any type in A15 (J65)
ICD-10-CM J61

Pneumoconiosis due to asbestos and other mineral fibers

    2016 2017 2018 Billable/Specific Code Adult Dx (15-124 years)
Applicable To
  • Asbestosis
Type 1 Excludes
  • pleural plaque with asbestosis (J92.0)
  • pneumoconiosis with tuberculosis, any type in A15 (J65)
ICD-10-CM J62.0

Pneumoconiosis due to talc dust

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J62.8

Pneumoconiosis due to other dust containing silica

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Silicosis NOS
ICD-10-CM J63.0

Aluminosis (of lung)

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J63.1

Bauxite fibrosis (of lung)

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J63.2

Berylliosis

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J63.3

Graphite fibrosis (of lung)

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J63.4

Siderosis

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J63.5

Stannosis

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J63.6

Pneumoconiosis due to other specified inorganic dusts

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J64

Unspecified pneumoconiosis

    2016 2017 2018 Billable/Specific Code
Type 1 Excludes
  • pneumonoconiosis with tuberculosis, any type in A15 (J65)
ICD-10-CM J65

Pneumoconiosis associated with tuberculosis

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Any condition in J60-J64 with tuberculosis, any type in A15
  • Silicotuberculosis
ICD-10-CM J66.0

Byssinosis

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Airway disease due to cotton dust
ICD-10-CM J66.1

Flax-dressers' disease

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J66.2

Cannabinosis

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J66.8

Airway disease due to other specific organic dusts

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J67.0

Farmer's lung

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Harvester's lung
  • Haymaker's lung
  • Moldy hay disease
ICD-10-CM J67.1

Bagassosis

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Bagasse disease
  • Bagasse pneumonitis
ICD-10-CM J67.2

Bird fancier's lung

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Budgerigar fancier's disease or lung
  • Pigeon fancier's disease or lung
ICD-10-CM J67.3

Suberosis

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Corkhandler's disease or lung
  • Corkworker's disease or lung
ICD-10-CM J67.4

Maltworker's lung

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Alveolitis due to Aspergillus clavatus
ICD-10-CM J67.5

Mushroom-worker's lung

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J67.6

Maple-bark-stripper's lung

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Alveolitis due to Cryptostroma corticale
  • Cryptostromosis
ICD-10-CM J67.7

Air conditioner and humidifier lung

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Allergic alveolitis due to fungal, thermophilic actinomycetes and other organisms growing in ventilation [air conditioning] systems
ICD-10-CM J67.8

Hypersensitivity pneumonitis due to other organic dusts

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Cheese-washer's lung
  • Coffee-worker's lung
  • Fish-meal worker's lung
  • Furrier's lung
  • Sequoiosis
ICD-10-CM J67.9

Hypersensitivity pneumonitis due to unspecified organic dust

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Allergic alveolitis (extrinsic) NOS
  • Hypersensitivity pneumonitis NOS
ICD-10-CM J70.1

Chronic and other pulmonary manifestations due to radiation

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Fibrosis of lung following radiation
Use Additional
ICD-10-CM J82

Pulmonary eosinophilia, not elsewhere classified

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Allergic pneumonia
  • Eosinophilic asthma
  • Eosinophilic pneumonia
  • Löffler's pneumonia
  • Tropical (pulmonary) eosinophilia NOS
Type 1 Excludes
  • pulmonary eosinophilia due to aspergillosis (B44.-)
  • pulmonary eosinophilia due to drugs (J70.2-J70.4)
  • pulmonary eosinophilia due to specified parasitic infection (B50-B83)
  • pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)
  • pulmonary infiltrate NOS (R91.8)
ICD-10-CM J84.01

Alveolar proteinosis

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J84.02

Pulmonary alveolar microlithiasis

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J84.03

Idiopathic pulmonary hemosiderosis

    2016 2017 2018 Billable/Specific Code Manifestation Code
Applicable To
  • Essential brown induration of lung
Code First
  • underlying disease, such as:
  • disorders of iron metabolism (E83.1-)
Type 1 Excludes
  • acute idiopathic pulmonary hemorrhage in infants [AIPHI] (R04.81)
ICD-10-CM J84.09

Other alveolar and parieto-alveolar conditions

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J84.10

Pulmonary fibrosis, unspecified

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Capillary fibrosis of lung
  • Cirrhosis of lung (chronic) NOS
  • Fibrosis of lung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial) NOS
  • Induration of lung (chronic) NOS
  • Postinflammatory pulmonary fibrosis
ICD-10-CM J84.111

Idiopathic interstitial pneumonia, not otherwise specified

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J84.112

Idiopathic pulmonary fibrosis

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Cryptogenic fibrosing alveolitis
  • Idiopathic fibrosing alveolitis
ICD-10-CM J84.113

Idiopathic non-specific interstitial pneumonitis

    2016 2017 2018 Billable/Specific Code
Type 1 Excludes
  • non-specific interstitial pneumonia NOS, or due to known underlying cause (J84.89)
ICD-10-CM J84.114

Acute interstitial pneumonitis

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Hamman-Rich syndrome
Type 1 Excludes
  • pneumocystis pneumonia (B59)
ICD-10-CM J84.115

Respiratory bronchiolitis interstitial lung disease

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J84.116

Cryptogenic organizing pneumonia

    2016 2017 2018 Billable/Specific Code
Type 1 Excludes
  • organizing pneumonia NOS, or due to known underlying cause (J84.89)
ICD-10-CM J84.117

Desquamative interstitial pneumonia

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J84.17

Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere

    2016 2017 2018 Billable/Specific Code Manifestation Code
Applicable To
  • Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease
  • Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere
  • Organizing pneumonia due to collagen vascular disease
  • Organizing pneumonia in diseases classified elsewhere
Code First
  • underlying disease, such as:
  • progressive systemic sclerosis (M34.0)
  • rheumatoid arthritis (M05.00-M06.9)
  • systemic lupus erythematosis (M32.0-M32.9)
ICD-10-CM J84.2

Lymphoid interstitial pneumonia

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Lymphoid interstitial pneumonitis
ICD-10-CM J84.81

Lymphangioleiomyomatosis

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Lymphangiomyomatosis
ICD-10-CM J84.82

Adult pulmonary Langerhans cell histiocytosis

    2016 2017 2018 Billable/Specific Code Adult Dx (15-124 years)
Applicable To
  • Adult PLCH
ICD-10-CM J84.83

Surfactant mutations of the lung

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J84.841

Neuroendocrine cell hyperplasia of infancy

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J84.842

Pulmonary interstitial glycogenosis

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J84.843

Alveolar capillary dysplasia with vein misalignment

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J84.848

Other interstitial lung diseases of childhood

    2016 2017 2018 Billable/Specific Code
ICD-10-CM J84.89

Other specified interstitial pulmonary diseases

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Endogenous lipoid pneumonia
  • Interstitial pneumonitis
  • Non-specific interstitial pneumonitis NOS
  • Organizing pneumonia NOS
Code First
  • , if applicable:
  • poisoning due to drug or toxin (T51-T65 with fifth or sixth character to indicate intent), for toxic pneumonopathy
  • underlying cause of pneumonopathy, if known
Type 1 Excludes
  • cryptogenic organizing pneumonia (J84.116)
  • idiopathic non-specific interstitial pneumonitis (J84.113)
  • lipoid pneumonia, exogenous or unspecified (J69.1)
  • lymphoid interstitial pneumonia (J84.2)
Use Additional
  • code, for adverse effect, to identify drug (T36-T50 with fifth or sixth character 5), if drug-induced
ICD-10-CM J84.9

Interstitial pulmonary disease, unspecified

    2016 2017 2018 Billable/Specific Code
Applicable To
  • Interstitial pneumonia NOS
ICD-10-CM J99

Respiratory disorders in diseases classified elsewhere

    2016 2017 2018 Billable/Specific Code Manifestation Code
Code First
  • underlying disease, such as:
  • amyloidosis (E85.-)
  • ankylosing spondylitis (M45)
  • congenital syphilis (A50.5)
  • cryoglobulinemia (D89.1)
  • early congenital syphilis (A50.0)
  • schistosomiasis (B65.0-B65.9)
Type 1 Excludes
ICD-10-CM M05.10

Rheumatoid lung disease with rheumatoid arthritis of unspecified site

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.111

Rheumatoid lung disease with rheumatoid arthritis of right shoulder

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.112

Rheumatoid lung disease with rheumatoid arthritis of left shoulder

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.119

Rheumatoid lung disease with rheumatoid arthritis of unspecified shoulder

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.121

Rheumatoid lung disease with rheumatoid arthritis of right elbow

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.122

Rheumatoid lung disease with rheumatoid arthritis of left elbow

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.129

Rheumatoid lung disease with rheumatoid arthritis of unspecified elbow

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.131

Rheumatoid lung disease with rheumatoid arthritis of right wrist

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.132

Rheumatoid lung disease with rheumatoid arthritis of left wrist

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.139

Rheumatoid lung disease with rheumatoid arthritis of unspecified wrist

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.141

Rheumatoid lung disease with rheumatoid arthritis of right hand

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.142

Rheumatoid lung disease with rheumatoid arthritis of left hand

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.149

Rheumatoid lung disease with rheumatoid arthritis of unspecified hand

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.151

Rheumatoid lung disease with rheumatoid arthritis of right hip

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.152

Rheumatoid lung disease with rheumatoid arthritis of left hip

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.159

Rheumatoid lung disease with rheumatoid arthritis of unspecified hip

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.161

Rheumatoid lung disease with rheumatoid arthritis of right knee

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.162

Rheumatoid lung disease with rheumatoid arthritis of left knee

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.169

Rheumatoid lung disease with rheumatoid arthritis of unspecified knee

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.171

Rheumatoid lung disease with rheumatoid arthritis of right ankle and foot

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.172

Rheumatoid lung disease with rheumatoid arthritis of left ankle and foot

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.179

Rheumatoid lung disease with rheumatoid arthritis of unspecified ankle and foot

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M05.19

Rheumatoid lung disease with rheumatoid arthritis of multiple sites

    2016 2017 2018 Billable/Specific Code
ICD-10-CM M34.81

Systemic sclerosis with lung involvement

    2016 2017 2018 Billable/Specific Code
ICD-10-CM P27.0

Wilson-Mikity syndrome

    2016 2017 2018 Billable/Specific Code Code on Newborn Record
Applicable To
  • Pulmonary dysmaturity
ICD-10-CM P27.1

Bronchopulmonary dysplasia originating in the perinatal period

    2016 2017 2018 Billable/Specific Code Code on Newborn Record
ICD-10-CM P27.8

Other chronic respiratory diseases originating in the perinatal period

    2016 2017 2018 Billable/Specific Code Code on Newborn Record
Applicable To
  • Congenital pulmonary fibrosis
  • Ventilator lung in newborn
ICD-10-CM P27.9

Unspecified chronic respiratory disease originating in the perinatal period

    2016 2017 2018 Billable/Specific Code Code on Newborn Record