ICD10Data
Analytics
Code Also Crosswalk

Code Also Crosswalk

The following 213 ICD-10-CM codes contain 'Code Also' annotation references within one-to-many other ICD-10-CM codes.

Displaying codes 1-100 of 213:

A15: D61.82

2023 ICD-10-CM Diagnosis Code D61.82
Myelophthisis
Applicable To
- Leukoerythroblastic anemia
- Myelophthisic anemia
- Panmyelophthisis
Code Also
- the underlying disorder, such as:
- malignant neoplasm of breast (C50.-)
- tuberculosis (A15.-)
Type 1 Excludes
- idiopathic myelofibrosis (D47.1)
- myelofibrosis NOS (D75.81)
- myelofibrosis with myeloid metaplasia (D47.4)
- primary myelofibrosis (D47.1)
- secondary myelofibrosis (D75.81)
B00: D81.82

2023 ICD-10-CM Diagnosis Code D81.82
Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
Applicable To
- p110d-activating mutation causing senescent T cells, lymphadenopathy, and immunodeficiency [PASLI] disease
Code Also
- , if applicable, any associated manifestations, such as:
- bronchiectasis (J47.-)
- herpes virus infections (B00.-)
- other acute respiratory tract infections (J00-J06; J20-J22)
- other infections (A00-B99)
- pneumonia (J12-J18)
B10.89: D47.Z2

2023 ICD-10-CM Diagnosis Code D47.Z2
Castleman disease
Code Also
- , if applicable, human herpesvirus 8 infection (B10.89)
Type 2 Excludes
- Kaposi's sarcoma (C46.-)
B15.9: K76.82

2023 ICD-10-CM Diagnosis Code K76.82
Hepatic encephalopathy
Applicable To
- Hepatic encephalopathy, NOS
- Hepatic encephalopathy without coma
- Hepatocerebral intoxication
- Portal-systemic encephalopathy
Code Also
- underlying liver disease, such as:
- acute and subacute hepatic failure without coma (K72.00)
- alcoholic hepatic failure without coma (K70.40)
- chronic hepatic failure without coma (K72.10)
- hepatic failure with toxic liver disease without coma (K71.10)
- hepatic failure without coma (K72.90)
- icterus of newborn (P55-P59)
- postprocedural hepatic failure (K91.82)
- viral hepatitis without hepatic coma (B15.9, B16.1, B16.9, B17.10, B19.10, B19.20, B19.9)
Type 1 Excludes
- acute and subacute hepatic failure with coma (K72.01)
- alcoholic hepatic failure with coma (K70.41)
- chronic hepatic failure with coma (K72.11)
- hepatic failure with coma (K72.91)
B16.1: K76.82

2023 ICD-10-CM Diagnosis Code K76.82
Hepatic encephalopathy
Applicable To
- Hepatic encephalopathy, NOS
- Hepatic encephalopathy without coma
- Hepatocerebral intoxication
- Portal-systemic encephalopathy
Code Also
- underlying liver disease, such as:
- acute and subacute hepatic failure without coma (K72.00)
- alcoholic hepatic failure without coma (K70.40)
- chronic hepatic failure without coma (K72.10)
- hepatic failure with toxic liver disease without coma (K71.10)
- hepatic failure without coma (K72.90)
- icterus of newborn (P55-P59)
- postprocedural hepatic failure (K91.82)
- viral hepatitis without hepatic coma (B15.9, B16.1, B16.9, B17.10, B19.10, B19.20, B19.9)
Type 1 Excludes
- acute and subacute hepatic failure with coma (K72.01)
- alcoholic hepatic failure with coma (K70.41)
- chronic hepatic failure with coma (K72.11)
- hepatic failure with coma (K72.91)
B16.9: K76.82

2023 ICD-10-CM Diagnosis Code K76.82
Hepatic encephalopathy
Applicable To
- Hepatic encephalopathy, NOS
- Hepatic encephalopathy without coma
- Hepatocerebral intoxication
- Portal-systemic encephalopathy
Code Also
- underlying liver disease, such as:
- acute and subacute hepatic failure without coma (K72.00)
- alcoholic hepatic failure without coma (K70.40)
- chronic hepatic failure without coma (K72.10)
- hepatic failure with toxic liver disease without coma (K71.10)
- hepatic failure without coma (K72.90)
- icterus of newborn (P55-P59)
- postprocedural hepatic failure (K91.82)
- viral hepatitis without hepatic coma (B15.9, B16.1, B16.9, B17.10, B19.10, B19.20, B19.9)
Type 1 Excludes
- acute and subacute hepatic failure with coma (K72.01)
- alcoholic hepatic failure with coma (K70.41)
- chronic hepatic failure with coma (K72.11)
- hepatic failure with coma (K72.91)
B17.10: K76.82

2023 ICD-10-CM Diagnosis Code K76.82
Hepatic encephalopathy
Applicable To
- Hepatic encephalopathy, NOS
- Hepatic encephalopathy without coma
- Hepatocerebral intoxication
- Portal-systemic encephalopathy
Code Also
- underlying liver disease, such as:
- acute and subacute hepatic failure without coma (K72.00)
- alcoholic hepatic failure without coma (K70.40)
- chronic hepatic failure without coma (K72.10)
- hepatic failure with toxic liver disease without coma (K71.10)
- hepatic failure without coma (K72.90)
- icterus of newborn (P55-P59)
- postprocedural hepatic failure (K91.82)
- viral hepatitis without hepatic coma (B15.9, B16.1, B16.9, B17.10, B19.10, B19.20, B19.9)
Type 1 Excludes
- acute and subacute hepatic failure with coma (K72.01)
- alcoholic hepatic failure with coma (K70.41)
- chronic hepatic failure with coma (K72.11)
- hepatic failure with coma (K72.91)
B19.10: K76.82

2023 ICD-10-CM Diagnosis Code K76.82
Hepatic encephalopathy
Applicable To
- Hepatic encephalopathy, NOS
- Hepatic encephalopathy without coma
- Hepatocerebral intoxication
- Portal-systemic encephalopathy
Code Also
- underlying liver disease, such as:
- acute and subacute hepatic failure without coma (K72.00)
- alcoholic hepatic failure without coma (K70.40)
- chronic hepatic failure without coma (K72.10)
- hepatic failure with toxic liver disease without coma (K71.10)
- hepatic failure without coma (K72.90)
- icterus of newborn (P55-P59)
- postprocedural hepatic failure (K91.82)
- viral hepatitis without hepatic coma (B15.9, B16.1, B16.9, B17.10, B19.10, B19.20, B19.9)
Type 1 Excludes
- acute and subacute hepatic failure with coma (K72.01)
- alcoholic hepatic failure with coma (K70.41)
- chronic hepatic failure with coma (K72.11)
- hepatic failure with coma (K72.91)
B19.20: K76.82

2023 ICD-10-CM Diagnosis Code K76.82
Hepatic encephalopathy
Applicable To
- Hepatic encephalopathy, NOS
- Hepatic encephalopathy without coma
- Hepatocerebral intoxication
- Portal-systemic encephalopathy
Code Also
- underlying liver disease, such as:
- acute and subacute hepatic failure without coma (K72.00)
- alcoholic hepatic failure without coma (K70.40)
- chronic hepatic failure without coma (K72.10)
- hepatic failure with toxic liver disease without coma (K71.10)
- hepatic failure without coma (K72.90)
- icterus of newborn (P55-P59)
- postprocedural hepatic failure (K91.82)
- viral hepatitis without hepatic coma (B15.9, B16.1, B16.9, B17.10, B19.10, B19.20, B19.9)
Type 1 Excludes
- acute and subacute hepatic failure with coma (K72.01)
- alcoholic hepatic failure with coma (K70.41)
- chronic hepatic failure with coma (K72.11)
- hepatic failure with coma (K72.91)
B19.9: K76.82

2023 ICD-10-CM Diagnosis Code K76.82
Hepatic encephalopathy
Applicable To
- Hepatic encephalopathy, NOS
- Hepatic encephalopathy without coma
- Hepatocerebral intoxication
- Portal-systemic encephalopathy
Code Also
- underlying liver disease, such as:
- acute and subacute hepatic failure without coma (K72.00)
- alcoholic hepatic failure without coma (K70.40)
- chronic hepatic failure without coma (K72.10)
- hepatic failure with toxic liver disease without coma (K71.10)
- hepatic failure without coma (K72.90)
- icterus of newborn (P55-P59)
- postprocedural hepatic failure (K91.82)
- viral hepatitis without hepatic coma (B15.9, B16.1, B16.9, B17.10, B19.10, B19.20, B19.9)
Type 1 Excludes
- acute and subacute hepatic failure with coma (K72.01)
- alcoholic hepatic failure with coma (K70.41)
- chronic hepatic failure with coma (K72.11)
- hepatic failure with coma (K72.91)
B20: I27.21

2023 ICD-10-CM Diagnosis Code I27.21
Secondary pulmonary arterial hypertension
Applicable To
- (Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
- (Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension
Code Also
- associated conditions if applicable, or adverse effects of drugs or toxins, such as:
- adverse effect of appetite depressants (T50.5X5)
- congenital heart disease (Q20-Q28)
- human immunodeficiency virus [HIV] disease (B20)
- polymyositis (M33.2-)
- portal hypertension (K76.6)
- rheumatoid arthritis (M05.-)
- schistosomiasis (B65.-)
- Sjögren syndrome (M35.0-)
- systemic sclerosis (M34.-)
B33.23: M35.81

2023 ICD-10-CM Diagnosis Code M35.81
Multisystem inflammatory syndrome
Applicable To
- MIS-A
- MIS-C
- Multisystem inflammatory syndrome in adults
- Multisystem inflammatory syndrome in children
- Pediatric inflammatory multisystem syndrome
- PIMS
Code First
- , if applicable, COVID-19 (U07.1)
Code Also
- any associated complications such as:
- acute hepatic failure (K72.0-)
- acute kidney failure (N17.-)
- acute myocarditis (I40.-)
- acute respiratory distress syndrome (J80)
- cardiac arrhythmia (I47-I49.-)
- pneumonia due to COVID-19 (J12.82)
- severe sepsis (R65.2-)
- viral cardiomyopathy (B33.24)
- viral pericarditis (B33.23)
Use Additional
- code, if applicable, for:
- exposure to COVID-19 or SARS-CoV-2 infection (Z20.822)
- personal history of COVID-19 (Z86.16)
- post COVID-19 condition (U09.9)
B33.24: M35.81

2023 ICD-10-CM Diagnosis Code M35.81
Multisystem inflammatory syndrome
Applicable To
- MIS-A
- MIS-C
- Multisystem inflammatory syndrome in adults
- Multisystem inflammatory syndrome in children
- Pediatric inflammatory multisystem syndrome
- PIMS
Code First
- , if applicable, COVID-19 (U07.1)
Code Also
- any associated complications such as:
- acute hepatic failure (K72.0-)
- acute kidney failure (N17.-)
- acute myocarditis (I40.-)
- acute respiratory distress syndrome (J80)
- cardiac arrhythmia (I47-I49.-)
- pneumonia due to COVID-19 (J12.82)
- severe sepsis (R65.2-)
- viral cardiomyopathy (B33.24)
- viral pericarditis (B33.23)
Use Additional
- code, if applicable, for:
- exposure to COVID-19 or SARS-CoV-2 infection (Z20.822)
- personal history of COVID-19 (Z86.16)
- post COVID-19 condition (U09.9)
B65: I27.21

2023 ICD-10-CM Diagnosis Code I27.21
Secondary pulmonary arterial hypertension
Applicable To
- (Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
- (Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension
Code Also
- associated conditions if applicable, or adverse effects of drugs or toxins, such as:
- adverse effect of appetite depressants (T50.5X5)
- congenital heart disease (Q20-Q28)
- human immunodeficiency virus [HIV] disease (B20)
- polymyositis (M33.2-)
- portal hypertension (K76.6)
- rheumatoid arthritis (M05.-)
- schistosomiasis (B65.-)
- Sjögren syndrome (M35.0-)
- systemic sclerosis (M34.-)
C50: D61.82

2023 ICD-10-CM Diagnosis Code D61.82
Myelophthisis
Applicable To
- Leukoerythroblastic anemia
- Myelophthisic anemia
- Panmyelophthisis
Code Also
- the underlying disorder, such as:
- malignant neoplasm of breast (C50.-)
- tuberculosis (A15.-)
Type 1 Excludes
- idiopathic myelofibrosis (D47.1)
- myelofibrosis NOS (D75.81)
- myelofibrosis with myeloid metaplasia (D47.4)
- primary myelofibrosis (D47.1)
- secondary myelofibrosis (D75.81)
C90.0: D47.02

2023 ICD-10-CM Diagnosis Code D47.02
Systemic mastocytosis
Applicable To
- Indolent systemic mastocytosis
- Isolated bone marrow mastocytosis
- Smoldering systemic mastocytosis
- Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
- , if applicable, any associated hematological non-mast cell lineage disease, such as:
- acute myeloid leukemia (C92.6-, C92.A-)
- chronic myelomonocytic leukemia (C93.1-)
- essential thrombocytosis (D47.3)
- hypereosinophilic syndrome (D72.1)
- myelodysplastic syndrome (D46.9)
- myeloproliferative syndrome (D47.1)
- non-Hodgkin lymphoma (C82-C85)
- plasma cell myeloma (C90.0-)
- polycythemia vera (D45)
Type 1 Excludes
- aggressive systemic mastocytosis (C96.21)
- mast cell leukemia (C94.3-)
C92.10: I27.29

2023 ICD-10-CM Diagnosis Code I27.29
Other secondary pulmonary hypertension
Applicable To
- Group 5 pulmonary hypertension
- Pulmonary hypertension with unclear multifactorial mechanisms
- Pulmonary hypertension due to hematologic disorders
- Pulmonary hypertension due to metabolic disorders
- Pulmonary hypertension due to other systemic disorders
Code Also
- other associated disorders, if known, such as:
- chronic myeloid leukemia (C92.10-C92.22)
- essential thrombocythemia (D47.3)
- Gaucher disease (E75.22)
- hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
- hyperthyroidism (E05.-)
- hypothyroidism (E00-E03)
- polycythemia vera (D45)
- sarcoidosis (D86.-)
C92.22: I27.29

2023 ICD-10-CM Diagnosis Code I27.29
Other secondary pulmonary hypertension
Applicable To
- Group 5 pulmonary hypertension
- Pulmonary hypertension with unclear multifactorial mechanisms
- Pulmonary hypertension due to hematologic disorders
- Pulmonary hypertension due to metabolic disorders
- Pulmonary hypertension due to other systemic disorders
Code Also
- other associated disorders, if known, such as:
- chronic myeloid leukemia (C92.10-C92.22)
- essential thrombocythemia (D47.3)
- Gaucher disease (E75.22)
- hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
- hyperthyroidism (E05.-)
- hypothyroidism (E00-E03)
- polycythemia vera (D45)
- sarcoidosis (D86.-)
C92.6: D47.02

2023 ICD-10-CM Diagnosis Code D47.02
Systemic mastocytosis
Applicable To
- Indolent systemic mastocytosis
- Isolated bone marrow mastocytosis
- Smoldering systemic mastocytosis
- Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
- , if applicable, any associated hematological non-mast cell lineage disease, such as:
- acute myeloid leukemia (C92.6-, C92.A-)
- chronic myelomonocytic leukemia (C93.1-)
- essential thrombocytosis (D47.3)
- hypereosinophilic syndrome (D72.1)
- myelodysplastic syndrome (D46.9)
- myeloproliferative syndrome (D47.1)
- non-Hodgkin lymphoma (C82-C85)
- plasma cell myeloma (C90.0-)
- polycythemia vera (D45)
Type 1 Excludes
- aggressive systemic mastocytosis (C96.21)
- mast cell leukemia (C94.3-)
C92.A: D47.02

2023 ICD-10-CM Diagnosis Code D47.02
Systemic mastocytosis
Applicable To
- Indolent systemic mastocytosis
- Isolated bone marrow mastocytosis
- Smoldering systemic mastocytosis
- Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
- , if applicable, any associated hematological non-mast cell lineage disease, such as:
- acute myeloid leukemia (C92.6-, C92.A-)
- chronic myelomonocytic leukemia (C93.1-)
- essential thrombocytosis (D47.3)
- hypereosinophilic syndrome (D72.1)
- myelodysplastic syndrome (D46.9)
- myeloproliferative syndrome (D47.1)
- non-Hodgkin lymphoma (C82-C85)
- plasma cell myeloma (C90.0-)
- polycythemia vera (D45)
Type 1 Excludes
- aggressive systemic mastocytosis (C96.21)
- mast cell leukemia (C94.3-)
C93.1: D47.02

2023 ICD-10-CM Diagnosis Code D47.02
Systemic mastocytosis
Applicable To
- Indolent systemic mastocytosis
- Isolated bone marrow mastocytosis
- Smoldering systemic mastocytosis
- Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
- , if applicable, any associated hematological non-mast cell lineage disease, such as:
- acute myeloid leukemia (C92.6-, C92.A-)
- chronic myelomonocytic leukemia (C93.1-)
- essential thrombocytosis (D47.3)
- hypereosinophilic syndrome (D72.1)
- myelodysplastic syndrome (D46.9)
- myeloproliferative syndrome (D47.1)
- non-Hodgkin lymphoma (C82-C85)
- plasma cell myeloma (C90.0-)
- polycythemia vera (D45)
Type 1 Excludes
- aggressive systemic mastocytosis (C96.21)
- mast cell leukemia (C94.3-)
D35.0: E26.01

2023 ICD-10-CM Diagnosis Code E26.01
Conn's syndrome
Code Also
- adrenal adenoma (D35.0-)
D45: D47.02
, I27.29

2023 ICD-10-CM Diagnosis Code D47.02
Systemic mastocytosis
Applicable To
- Indolent systemic mastocytosis
- Isolated bone marrow mastocytosis
- Smoldering systemic mastocytosis
- Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
- , if applicable, any associated hematological non-mast cell lineage disease, such as:
- acute myeloid leukemia (C92.6-, C92.A-)
- chronic myelomonocytic leukemia (C93.1-)
- essential thrombocytosis (D47.3)
- hypereosinophilic syndrome (D72.1)
- myelodysplastic syndrome (D46.9)
- myeloproliferative syndrome (D47.1)
- non-Hodgkin lymphoma (C82-C85)
- plasma cell myeloma (C90.0-)
- polycythemia vera (D45)
Type 1 Excludes
- aggressive systemic mastocytosis (C96.21)
- mast cell leukemia (C94.3-)
2023 ICD-10-CM Diagnosis Code I27.29
Other secondary pulmonary hypertension
Applicable To
- Group 5 pulmonary hypertension
- Pulmonary hypertension with unclear multifactorial mechanisms
- Pulmonary hypertension due to hematologic disorders
- Pulmonary hypertension due to metabolic disorders
- Pulmonary hypertension due to other systemic disorders
Code Also
- other associated disorders, if known, such as:
- chronic myeloid leukemia (C92.10-C92.22)
- essential thrombocythemia (D47.3)
- Gaucher disease (E75.22)
- hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
- hyperthyroidism (E05.-)
- hypothyroidism (E00-E03)
- polycythemia vera (D45)
- sarcoidosis (D86.-)
D46.9: D47.02

2023 ICD-10-CM Diagnosis Code D47.02
Systemic mastocytosis
Applicable To
- Indolent systemic mastocytosis
- Isolated bone marrow mastocytosis
- Smoldering systemic mastocytosis
- Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
- , if applicable, any associated hematological non-mast cell lineage disease, such as:
- acute myeloid leukemia (C92.6-, C92.A-)
- chronic myelomonocytic leukemia (C93.1-)
- essential thrombocytosis (D47.3)
- hypereosinophilic syndrome (D72.1)
- myelodysplastic syndrome (D46.9)
- myeloproliferative syndrome (D47.1)
- non-Hodgkin lymphoma (C82-C85)
- plasma cell myeloma (C90.0-)
- polycythemia vera (D45)
Type 1 Excludes
- aggressive systemic mastocytosis (C96.21)
- mast cell leukemia (C94.3-)
D47.1: D47.02

2023 ICD-10-CM Diagnosis Code D47.02
Systemic mastocytosis
Applicable To
- Indolent systemic mastocytosis
- Isolated bone marrow mastocytosis
- Smoldering systemic mastocytosis
- Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
- , if applicable, any associated hematological non-mast cell lineage disease, such as:
- acute myeloid leukemia (C92.6-, C92.A-)
- chronic myelomonocytic leukemia (C93.1-)
- essential thrombocytosis (D47.3)
- hypereosinophilic syndrome (D72.1)
- myelodysplastic syndrome (D46.9)
- myeloproliferative syndrome (D47.1)
- non-Hodgkin lymphoma (C82-C85)
- plasma cell myeloma (C90.0-)
- polycythemia vera (D45)
Type 1 Excludes
- aggressive systemic mastocytosis (C96.21)
- mast cell leukemia (C94.3-)
D47.3: D47.02
, I27.29

2023 ICD-10-CM Diagnosis Code D47.02
Systemic mastocytosis
Applicable To
- Indolent systemic mastocytosis
- Isolated bone marrow mastocytosis
- Smoldering systemic mastocytosis
- Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
- , if applicable, any associated hematological non-mast cell lineage disease, such as:
- acute myeloid leukemia (C92.6-, C92.A-)
- chronic myelomonocytic leukemia (C93.1-)
- essential thrombocytosis (D47.3)
- hypereosinophilic syndrome (D72.1)
- myelodysplastic syndrome (D46.9)
- myeloproliferative syndrome (D47.1)
- non-Hodgkin lymphoma (C82-C85)
- plasma cell myeloma (C90.0-)
- polycythemia vera (D45)
Type 1 Excludes
- aggressive systemic mastocytosis (C96.21)
- mast cell leukemia (C94.3-)
2023 ICD-10-CM Diagnosis Code I27.29
Other secondary pulmonary hypertension
Applicable To
- Group 5 pulmonary hypertension
- Pulmonary hypertension with unclear multifactorial mechanisms
- Pulmonary hypertension due to hematologic disorders
- Pulmonary hypertension due to metabolic disorders
- Pulmonary hypertension due to other systemic disorders
Code Also
- other associated disorders, if known, such as:
- chronic myeloid leukemia (C92.10-C92.22)
- essential thrombocythemia (D47.3)
- Gaucher disease (E75.22)
- hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
- hyperthyroidism (E05.-)
- hypothyroidism (E00-E03)
- polycythemia vera (D45)
- sarcoidosis (D86.-)
D57: Z71.87

2023 ICD-10-CM Diagnosis Code Z71.87
Encounter for pediatric-to-adult transition counseling
Code Also
- chronic condition, if applicable, such as:
- autism spectrum disorder (F84.0)
- congenital malformations of the circulatory system (Q20-Q28)
- cystic fibrosis (E84-)
- sickle-cell disorder (D57-)
D69.1: D68.09

2023 ICD-10-CM Diagnosis Code D68.09
Other von Willebrand disease
Applicable To
- Platelet-type von Willebrand disease
- Pseudo-von Willebrand disease
Code Also
- , if applicable, qualitative platelet defects (D69.1)
D72.1: D47.02

2023 ICD-10-CM Diagnosis Code D47.02
Systemic mastocytosis
Applicable To
- Indolent systemic mastocytosis
- Isolated bone marrow mastocytosis
- Smoldering systemic mastocytosis
- Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
- , if applicable, any associated hematological non-mast cell lineage disease, such as:
- acute myeloid leukemia (C92.6-, C92.A-)
- chronic myelomonocytic leukemia (C93.1-)
- essential thrombocytosis (D47.3)
- hypereosinophilic syndrome (D72.1)
- myelodysplastic syndrome (D46.9)
- myeloproliferative syndrome (D47.1)
- non-Hodgkin lymphoma (C82-C85)
- plasma cell myeloma (C90.0-)
- polycythemia vera (D45)
Type 1 Excludes
- aggressive systemic mastocytosis (C96.21)
- mast cell leukemia (C94.3-)
D72.18: C93.1

2023 ICD-10-CM Diagnosis Code C93.1
Chronic myelomonocytic leukemia
Applicable To
- Chronic monocytic leukemia
- CMML-1
- CMML-2
- CMML with eosinophilia
Code Also
- , if applicable, eosinophilia (D72.18)
D84.1: D59.32

2023 ICD-10-CM Diagnosis Code D59.32
Hereditary hemolytic-uremic syndrome
Applicable To
- Atypical hemolytic uremic syndrome with an identified genetic cause
Code Also
- , if applicable:
- defects in the complement system (D84.1)
- methylmalonic acidemia (E71.120)
D86: I27.29

2023 ICD-10-CM Diagnosis Code I27.29
Other secondary pulmonary hypertension
Applicable To
- Group 5 pulmonary hypertension
- Pulmonary hypertension with unclear multifactorial mechanisms
- Pulmonary hypertension due to hematologic disorders
- Pulmonary hypertension due to metabolic disorders
- Pulmonary hypertension due to other systemic disorders
Code Also
- other associated disorders, if known, such as:
- chronic myeloid leukemia (C92.10-C92.22)
- essential thrombocythemia (D47.3)
- Gaucher disease (E75.22)
- hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
- hyperthyroidism (E05.-)
- hypothyroidism (E00-E03)
- polycythemia vera (D45)
- sarcoidosis (D86.-)
E05: I27.29

2023 ICD-10-CM Diagnosis Code I27.29
Other secondary pulmonary hypertension
Applicable To
- Group 5 pulmonary hypertension
- Pulmonary hypertension with unclear multifactorial mechanisms
- Pulmonary hypertension due to hematologic disorders
- Pulmonary hypertension due to metabolic disorders
- Pulmonary hypertension due to other systemic disorders
Code Also
- other associated disorders, if known, such as:
- chronic myeloid leukemia (C92.10-C92.22)
- essential thrombocythemia (D47.3)
- Gaucher disease (E75.22)
- hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
- hyperthyroidism (E05.-)
- hypothyroidism (E00-E03)
- polycythemia vera (D45)
- sarcoidosis (D86.-)
E31.2: C7A
, D3A

2023 ICD-10-CM Diagnosis Code D3A
Benign neuroendocrine tumors
Code Also
- any associated multiple endocrine neoplasia [MEN] syndromes (E31.2-)
Type 2 Excludes
- benign pancreatic islet cell tumors (D13.7)
Use Additional
- code to identify any associated endocrine syndrome, such as:
- carcinoid syndrome (E34.0)
2023 ICD-10-CM Diagnosis Code C7A
Malignant neuroendocrine tumors
Code Also
- any associated multiple endocrine neoplasia [MEN] syndromes (E31.2-)
Type 2 Excludes
- malignant pancreatic islet cell tumors (C25.4)
- Merkel cell carcinoma (C4A.-)
Use Additional
- code to identify any associated endocrine syndrome, such as:
- carcinoid syndrome (E34.0)
E71.120: D59.32

2023 ICD-10-CM Diagnosis Code D59.32
Hereditary hemolytic-uremic syndrome
Applicable To
- Atypical hemolytic uremic syndrome with an identified genetic cause
Code Also
- , if applicable:
- defects in the complement system (D84.1)
- methylmalonic acidemia (E71.120)
E75.22: I27.29

2023 ICD-10-CM Diagnosis Code I27.29
Other secondary pulmonary hypertension
Applicable To
- Group 5 pulmonary hypertension
- Pulmonary hypertension with unclear multifactorial mechanisms
- Pulmonary hypertension due to hematologic disorders
- Pulmonary hypertension due to metabolic disorders
- Pulmonary hypertension due to other systemic disorders
Code Also
- other associated disorders, if known, such as:
- chronic myeloid leukemia (C92.10-C92.22)
- essential thrombocythemia (D47.3)
- Gaucher disease (E75.22)
- hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
- hyperthyroidism (E05.-)
- hypothyroidism (E00-E03)
- polycythemia vera (D45)
- sarcoidosis (D86.-)
E83.01: H18.04

2023 ICD-10-CM Diagnosis Code H18.04
Kayser-Fleischer ring
Code Also
- associated Wilson's disease (E83.01)
E84: Z71.87

2023 ICD-10-CM Diagnosis Code Z71.87
Encounter for pediatric-to-adult transition counseling
Code Also
- chronic condition, if applicable, such as:
- autism spectrum disorder (F84.0)
- congenital malformations of the circulatory system (Q20-Q28)
- cystic fibrosis (E84-)
- sickle-cell disorder (D57-)
E84.0: I27.23

2023 ICD-10-CM Diagnosis Code I27.23
Pulmonary hypertension due to lung diseases and hypoxia
Applicable To
- Group 3 pulmonary hypertension
Code Also
- associated lung disease, if known, such as:
- bronchiectasis (J47.-)
- cystic fibrosis with pulmonary manifestations (E84.0)
- interstitial lung disease (J84.-)
- pleural effusion (J90)
- sleep apnea (G47.3-)
E88.02: H10.51

2023 ICD-10-CM Diagnosis Code H10.51
Ligneous conjunctivitis
Code Also
- underlying condition if known, such as:
- plasminogen deficiency (E88.02)
E88.42: G40.3

2023 ICD-10-CM Diagnosis Code G40.3
Generalized idiopathic epilepsy and epileptic syndromes
Code Also
- MERRF syndrome, if applicable (E88.42)
F01: I67.850

2023 ICD-10-CM Diagnosis Code I67.850
Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy
Applicable To
- CADASIL
Code Also
- any associated diagnoses, such as:
- epilepsy (G40.-)
- stroke (I63.-)
- vascular dementia (F01.-)
F10: G31.2
, I42.6

2023 ICD-10-CM Diagnosis Code I42.6
Alcoholic cardiomyopathy
Code Also
- presence of alcoholism (F10.-)
2023 ICD-10-CM Diagnosis Code G31.2
Degeneration of nervous system due to alcohol
Applicable To
- Alcoholic cerebellar ataxia
- Alcoholic cerebellar degeneration
- Alcoholic cerebral degeneration
- Alcoholic encephalopathy
- Dysfunction of the autonomic nervous system due to alcohol
Code Also
- associated alcoholism (F10.-)
F45.42: G89

2023 ICD-10-CM Diagnosis Code G89
Pain, not elsewhere classified
Code Also
- related psychological factors associated with pain (F45.42)
Type 1 Excludes
- generalized pain NOS (R52)
- pain disorders exclusively related to psychological factors (F45.41)
- pain NOS (R52)
Type 2 Excludes
- atypical face pain (G50.1)
- headache syndromes (G44.-)
- localized pain, unspecified type - code to pain by site, such as:
- abdomen pain (R10.-)
- back pain (M54.9)
- breast pain (N64.4)
- chest pain (R07.1-R07.9)
- ear pain (H92.0-)
- eye pain (H57.1)
- headache (R51.9)
- joint pain (M25.5-)
- limb pain (M79.6-)
- lumbar region pain (M54.5-)
- painful urination (R30.9)
- pelvic and perineal pain (R10.2)
- shoulder pain (M25.51-)
- spine pain (M54.-)
- throat pain (R07.0)
- tongue pain (K14.6)
- tooth pain (K08.8)
- renal colic (N23)
- migraines (G43.-)
- myalgia (M79.1-)
- pain from prosthetic devices, implants, and grafts (T82.84, T83.84, T84.84, T85.84-)
- phantom limb syndrome with pain (G54.6)
- vulvar vestibulitis (N94.810)
- vulvodynia (N94.81-)
F84.0: F78.A1
, F78.A1
, Z71.87

2023 ICD-10-CM Diagnosis Code Z71.87
Encounter for pediatric-to-adult transition counseling
Code Also
- chronic condition, if applicable, such as:
- autism spectrum disorder (F84.0)
- congenital malformations of the circulatory system (Q20-Q28)
- cystic fibrosis (E84-)
- sickle-cell disorder (D57-)
2023 ICD-10-CM Diagnosis Code F78.A1
SYNGAP1-related intellectual disability
Code Also
- , if applicable, any associated:
- autism spectrum disorder (F84.0)
- autistic disorder (F84.0)
- encephalopathy (G93.4-)
- epilepsy and recurrent seizures (G40.-)
- other pervasive developmental disorders (F84.8)
- pervasive developmental disorder, NOS (F84.9)
2023 ICD-10-CM Diagnosis Code F78.A1
SYNGAP1-related intellectual disability
Code Also
- , if applicable, any associated:
- autism spectrum disorder (F84.0)
- autistic disorder (F84.0)
- encephalopathy (G93.4-)
- epilepsy and recurrent seizures (G40.-)
- other pervasive developmental disorders (F84.8)
- pervasive developmental disorder, NOS (F84.9)
F84.8: F78.A1

2023 ICD-10-CM Diagnosis Code F78.A1
SYNGAP1-related intellectual disability
Code Also
- , if applicable, any associated:
- autism spectrum disorder (F84.0)
- autistic disorder (F84.0)
- encephalopathy (G93.4-)
- epilepsy and recurrent seizures (G40.-)
- other pervasive developmental disorders (F84.8)
- pervasive developmental disorder, NOS (F84.9)
F84.9: F78.A1

2023 ICD-10-CM Diagnosis Code F78.A1
SYNGAP1-related intellectual disability
Code Also
- , if applicable, any associated:
- autism spectrum disorder (F84.0)
- autistic disorder (F84.0)
- encephalopathy (G93.4-)
- epilepsy and recurrent seizures (G40.-)
- other pervasive developmental disorders (F84.8)
- pervasive developmental disorder, NOS (F84.9)
G21.8: G96.81

2023 ICD-10-CM Diagnosis Code G96.81
Intracranial hypotension
Code Also
- any associated diagnoses, such as:
- Brachial amyotrophy (G54.5)
- Cerebrospinal fluid leak from spine (G96.02)
- Cranial nerve disorders in diseases classified elsewhere (G53)
- Nerve root and compressions in diseases classified elsewhere (G55)
- Nonpyogenic thrombosis of intracranial venous system (I67.6)
- Nontraumatic intracerebral hemorrhage (I61.-)
- Nontraumatic subdural hemorrhage (I62.0-)
- Other and unspecified cord compression (G95.2-)
- Other secondary parkinsonism (G21.8)
- Reversible cerebrovascular vasoconstriction syndrome (I67.841)
- Spinal cord herniation (G95.89)
- Stroke (I63.-)
- Syringomyelia (G95.0)
G40: F78.A1
, G04.8
, G40.5
, G43.1
, I67.850

2023 ICD-10-CM Diagnosis Code F78.A1
SYNGAP1-related intellectual disability
Code Also
- , if applicable, any associated:
- autism spectrum disorder (F84.0)
- autistic disorder (F84.0)
- encephalopathy (G93.4-)
- epilepsy and recurrent seizures (G40.-)
- other pervasive developmental disorders (F84.8)
- pervasive developmental disorder, NOS (F84.9)
2023 ICD-10-CM Diagnosis Code I67.850
Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy
Applicable To
- CADASIL
Code Also
- any associated diagnoses, such as:
- epilepsy (G40.-)
- stroke (I63.-)
- vascular dementia (F01.-)
2023 ICD-10-CM Diagnosis Code G04.8
Other encephalitis, myelitis and encephalomyelitis
Code Also
- any associated seizure (G40.-, R56.9)
2023 ICD-10-CM Diagnosis Code G40.5
Epileptic seizures related to external causes
Applicable To
- Epileptic seizures related to alcohol
- Epileptic seizures related to drugs
- Epileptic seizures related to hormonal changes
- Epileptic seizures related to sleep deprivation
- Epileptic seizures related to stress
Code Also
- , if applicable, associated epilepsy and recurrent seizures (G40.-)
Use Additional
- code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
2023 ICD-10-CM Diagnosis Code G43.1
Migraine with aura
Applicable To
- Basilar migraine
- Classical migraine
- Migraine equivalents
- Migraine preceded or accompanied by transient focal neurological phenomena
- Migraine triggered seizures
- Migraine with acute-onset aura
- Migraine with aura without headache (migraine equivalents)
- Migraine with prolonged aura
- Migraine with typical aura
- Retinal migraine
Code Also
- any associated seizure (G40.-, R56.9)
Type 1 Excludes
- persistent migraine aura (G43.5-, G43.6-)
G40.3: E88.42

2023 ICD-10-CM Diagnosis Code E88.42
MERRF syndrome
Applicable To
- Myoclonic epilepsy associated with ragged-red fibers
Code Also
- progressive myoclonic epilepsy (G40.3-)
G43.82: N94.3

2023 ICD-10-CM Diagnosis Code N94.3
Premenstrual tension syndrome
Code Also
- associated menstrual migraine (G43.82-, G43.83-)
Type 1 Excludes
- Premenstrual dysphoric disorder (F32.81)
G43.83: N94.3

2023 ICD-10-CM Diagnosis Code N94.3
Premenstrual tension syndrome
Code Also
- associated menstrual migraine (G43.82-, G43.83-)
Type 1 Excludes
- Premenstrual dysphoric disorder (F32.81)
G47.3: I27.23

2023 ICD-10-CM Diagnosis Code I27.23
Pulmonary hypertension due to lung diseases and hypoxia
Applicable To
- Group 3 pulmonary hypertension
Code Also
- associated lung disease, if known, such as:
- bronchiectasis (J47.-)
- cystic fibrosis with pulmonary manifestations (E84.0)
- interstitial lung disease (J84.-)
- pleural effusion (J90)
- sleep apnea (G47.3-)
G53: G96.81

2023 ICD-10-CM Diagnosis Code G96.81
Intracranial hypotension
Code Also
- any associated diagnoses, such as:
- Brachial amyotrophy (G54.5)
- Cerebrospinal fluid leak from spine (G96.02)
- Cranial nerve disorders in diseases classified elsewhere (G53)
- Nerve root and compressions in diseases classified elsewhere (G55)
- Nonpyogenic thrombosis of intracranial venous system (I67.6)
- Nontraumatic intracerebral hemorrhage (I61.-)
- Nontraumatic subdural hemorrhage (I62.0-)
- Other and unspecified cord compression (G95.2-)
- Other secondary parkinsonism (G21.8)
- Reversible cerebrovascular vasoconstriction syndrome (I67.841)
- Spinal cord herniation (G95.89)
- Stroke (I63.-)
- Syringomyelia (G95.0)
G54.5: G96.81

2023 ICD-10-CM Diagnosis Code G96.81
Intracranial hypotension
Code Also
- any associated diagnoses, such as:
- Brachial amyotrophy (G54.5)
- Cerebrospinal fluid leak from spine (G96.02)
- Cranial nerve disorders in diseases classified elsewhere (G53)
- Nerve root and compressions in diseases classified elsewhere (G55)
- Nonpyogenic thrombosis of intracranial venous system (I67.6)
- Nontraumatic intracerebral hemorrhage (I61.-)
- Nontraumatic subdural hemorrhage (I62.0-)
- Other and unspecified cord compression (G95.2-)
- Other secondary parkinsonism (G21.8)
- Reversible cerebrovascular vasoconstriction syndrome (I67.841)
- Spinal cord herniation (G95.89)
- Stroke (I63.-)
- Syringomyelia (G95.0)
G55: G96.81

2023 ICD-10-CM Diagnosis Code G96.81
Intracranial hypotension
Code Also
- any associated diagnoses, such as:
- Brachial amyotrophy (G54.5)
- Cerebrospinal fluid leak from spine (G96.02)
- Cranial nerve disorders in diseases classified elsewhere (G53)
- Nerve root and compressions in diseases classified elsewhere (G55)
- Nonpyogenic thrombosis of intracranial venous system (I67.6)
- Nontraumatic intracerebral hemorrhage (I61.-)
- Nontraumatic subdural hemorrhage (I62.0-)
- Other and unspecified cord compression (G95.2-)
- Other secondary parkinsonism (G21.8)
- Reversible cerebrovascular vasoconstriction syndrome (I67.841)
- Spinal cord herniation (G95.89)
- Stroke (I63.-)
- Syringomyelia (G95.0)
G89: F45.42

2023 ICD-10-CM Diagnosis Code F45.42
Pain disorder with related psychological factors
Code Also
- associated acute or chronic pain (G89.-)
G93.4: F78.A1

2023 ICD-10-CM Diagnosis Code F78.A1
SYNGAP1-related intellectual disability
Code Also
- , if applicable, any associated:
- autism spectrum disorder (F84.0)
- autistic disorder (F84.0)
- encephalopathy (G93.4-)
- epilepsy and recurrent seizures (G40.-)
- other pervasive developmental disorders (F84.8)
- pervasive developmental disorder, NOS (F84.9)
G95.0: G96.81

2023 ICD-10-CM Diagnosis Code G96.81
Intracranial hypotension
Code Also
- any associated diagnoses, such as:
- Brachial amyotrophy (G54.5)
- Cerebrospinal fluid leak from spine (G96.02)
- Cranial nerve disorders in diseases classified elsewhere (G53)
- Nerve root and compressions in diseases classified elsewhere (G55)
- Nonpyogenic thrombosis of intracranial venous system (I67.6)
- Nontraumatic intracerebral hemorrhage (I61.-)
- Nontraumatic subdural hemorrhage (I62.0-)
- Other and unspecified cord compression (G95.2-)
- Other secondary parkinsonism (G21.8)
- Reversible cerebrovascular vasoconstriction syndrome (I67.841)
- Spinal cord herniation (G95.89)
- Stroke (I63.-)
- Syringomyelia (G95.0)
G95.2: G96.81

2023 ICD-10-CM Diagnosis Code G96.81
Intracranial hypotension
Code Also
- any associated diagnoses, such as:
- Brachial amyotrophy (G54.5)
- Cerebrospinal fluid leak from spine (G96.02)
- Cranial nerve disorders in diseases classified elsewhere (G53)
- Nerve root and compressions in diseases classified elsewhere (G55)
- Nonpyogenic thrombosis of intracranial venous system (I67.6)
- Nontraumatic intracerebral hemorrhage (I61.-)
- Nontraumatic subdural hemorrhage (I62.0-)
- Other and unspecified cord compression (G95.2-)
- Other secondary parkinsonism (G21.8)
- Reversible cerebrovascular vasoconstriction syndrome (I67.841)
- Spinal cord herniation (G95.89)
- Stroke (I63.-)
- Syringomyelia (G95.0)
G95.89: G96.81

2023 ICD-10-CM Diagnosis Code G96.81
Intracranial hypotension
Code Also
- any associated diagnoses, such as:
- Brachial amyotrophy (G54.5)
- Cerebrospinal fluid leak from spine (G96.02)
- Cranial nerve disorders in diseases classified elsewhere (G53)
- Nerve root and compressions in diseases classified elsewhere (G55)
- Nonpyogenic thrombosis of intracranial venous system (I67.6)
- Nontraumatic intracerebral hemorrhage (I61.-)
- Nontraumatic subdural hemorrhage (I62.0-)
- Other and unspecified cord compression (G95.2-)
- Other secondary parkinsonism (G21.8)
- Reversible cerebrovascular vasoconstriction syndrome (I67.841)
- Spinal cord herniation (G95.89)
- Stroke (I63.-)
- Syringomyelia (G95.0)
G96.02: G96.81

2023 ICD-10-CM Diagnosis Code G96.81
Intracranial hypotension
Code Also
- any associated diagnoses, such as:
- Brachial amyotrophy (G54.5)
- Cerebrospinal fluid leak from spine (G96.02)
- Cranial nerve disorders in diseases classified elsewhere (G53)
- Nerve root and compressions in diseases classified elsewhere (G55)
- Nonpyogenic thrombosis of intracranial venous system (I67.6)
- Nontraumatic intracerebral hemorrhage (I61.-)
- Nontraumatic subdural hemorrhage (I62.0-)
- Other and unspecified cord compression (G95.2-)
- Other secondary parkinsonism (G21.8)
- Reversible cerebrovascular vasoconstriction syndrome (I67.841)
- Spinal cord herniation (G95.89)
- Stroke (I63.-)
- Syringomyelia (G95.0)
G96.81: G96.0
, G96.11

2023 ICD-10-CM Diagnosis Code G96.0
Cerebrospinal fluid leak
Code Also
- if applicable:
- intracranial hypotension (G96.81-)
Type 1 Excludes
- cerebrospinal fluid leak from spinal puncture (G97.0)
2023 ICD-10-CM Diagnosis Code G96.11
Dural tear
Code Also
- intracranial hypotension, if applicable (G96.81-)
Type 1 Excludes
- accidental puncture or laceration of dura during a procedure (G97.41)
G97.0: G97.84

2023 ICD-10-CM Diagnosis Code G97.84
Intracranial hypotension following other procedure
Code Also
- , if applicable:
- accidental puncture or laceration of dura during a procedure (G97.41)
- cerebrospinal fluid leak from spinal puncture (G97.0)
G97.41: G97.84

2023 ICD-10-CM Diagnosis Code G97.84
Intracranial hypotension following other procedure
Code Also
- , if applicable:
- accidental puncture or laceration of dura during a procedure (G97.41)
- cerebrospinal fluid leak from spinal puncture (G97.0)
G97.83: G97.0

2023 ICD-10-CM Diagnosis Code G97.0
Cerebrospinal fluid leak from spinal puncture
Code Also
- any associated diagnoses or complications, such as:
- intracranial hypotension following a procedure (G97.83-G97.84)
G97.84: G97.0

2023 ICD-10-CM Diagnosis Code G97.0
Cerebrospinal fluid leak from spinal puncture
Code Also
- any associated diagnoses or complications, such as:
- intracranial hypotension following a procedure (G97.83-G97.84)
H10.51: E88.02

2023 ICD-10-CM Diagnosis Code E88.02
Plasminogen deficiency
Applicable To
- Dysplasminogenemia
- Hypoplasminogenemia
- Type 1 plasminogen deficiency
- Type 2 plasminogen deficiency
Code Also
- , if applicable, ligneous conjunctivitis (H10.51)
Use Additional
- code for associated findings, such as:
- hydrocephalus (G91.4)
- otitis media (H67.-)
- respiratory disorder related to plasminogen deficiency (J99)
H18.04: E83.01

2023 ICD-10-CM Diagnosis Code E83.01
Wilson's disease
Code Also
- associated Kayser Fleischer ring (H18.04-)
H20.1: H26.21

2023 ICD-10-CM Diagnosis Code H26.21
Cataract with neovascularization
Code Also
- associated condition, such as:
- chronic iridocyclitis (H20.1-)
H90: F80.4

2023 ICD-10-CM Diagnosis Code F80.4
Speech and language development delay due to hearing loss
Code Also
- type of hearing loss (H90.-, H91.-)
H91: F80.4

2023 ICD-10-CM Diagnosis Code F80.4
Speech and language development delay due to hearing loss
Code Also
- type of hearing loss (H90.-, H91.-)
I05: I27.22

2023 ICD-10-CM Diagnosis Code I27.22
Pulmonary hypertension due to left heart disease
Applicable To
- Group 2 pulmonary hypertension
Code Also
- associated left heart disease, if known, such as:
- multiple valve disease (I08.-)
- rheumatic mitral valve diseases (I05.-)
- rheumatic aortic valve diseases (I06.-)
I06: I27.22

2023 ICD-10-CM Diagnosis Code I27.22
Pulmonary hypertension due to left heart disease
Applicable To
- Group 2 pulmonary hypertension
Code Also
- associated left heart disease, if known, such as:
- multiple valve disease (I08.-)
- rheumatic mitral valve diseases (I05.-)
- rheumatic aortic valve diseases (I06.-)
I08: I27.22

2023 ICD-10-CM Diagnosis Code I27.22
Pulmonary hypertension due to left heart disease
Applicable To
- Group 2 pulmonary hypertension
Code Also
- associated left heart disease, if known, such as:
- multiple valve disease (I08.-)
- rheumatic mitral valve diseases (I05.-)
- rheumatic aortic valve diseases (I06.-)
I10: H35.0

2023 ICD-10-CM Diagnosis Code H35.0
Background retinopathy and retinal vascular changes
Code Also
- any associated hypertension (I10)
I12.0: I27.29

2023 ICD-10-CM Diagnosis Code I27.29
Other secondary pulmonary hypertension
Applicable To
- Group 5 pulmonary hypertension
- Pulmonary hypertension with unclear multifactorial mechanisms
- Pulmonary hypertension due to hematologic disorders
- Pulmonary hypertension due to metabolic disorders
- Pulmonary hypertension due to other systemic disorders
Code Also
- other associated disorders, if known, such as:
- chronic myeloid leukemia (C92.10-C92.22)
- essential thrombocythemia (D47.3)
- Gaucher disease (E75.22)
- hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
- hyperthyroidism (E05.-)
- hypothyroidism (E00-E03)
- polycythemia vera (D45)
- sarcoidosis (D86.-)
I13.11: I27.29

2023 ICD-10-CM Diagnosis Code I27.29
Other secondary pulmonary hypertension
Applicable To
- Group 5 pulmonary hypertension
- Pulmonary hypertension with unclear multifactorial mechanisms
- Pulmonary hypertension due to hematologic disorders
- Pulmonary hypertension due to metabolic disorders
- Pulmonary hypertension due to other systemic disorders
Code Also
- other associated disorders, if known, such as:
- chronic myeloid leukemia (C92.10-C92.22)
- essential thrombocythemia (D47.3)
- Gaucher disease (E75.22)
- hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
- hyperthyroidism (E05.-)
- hypothyroidism (E00-E03)
- polycythemia vera (D45)
- sarcoidosis (D86.-)
I13.2: I27.29

2023 ICD-10-CM Diagnosis Code I27.29
Other secondary pulmonary hypertension
Applicable To
- Group 5 pulmonary hypertension
- Pulmonary hypertension with unclear multifactorial mechanisms
- Pulmonary hypertension due to hematologic disorders
- Pulmonary hypertension due to metabolic disorders
- Pulmonary hypertension due to other systemic disorders
Code Also
- other associated disorders, if known, such as:
- chronic myeloid leukemia (C92.10-C92.22)
- essential thrombocythemia (D47.3)
- Gaucher disease (E75.22)
- hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
- hyperthyroidism (E05.-)
- hypothyroidism (E00-E03)
- polycythemia vera (D45)
- sarcoidosis (D86.-)
I16.1: D59.39

2023 ICD-10-CM Diagnosis Code D59.39
Other hemolytic-uremic syndrome
Applicable To
- Atypical (nongenetic) hemolytic uremic syndrome
- Secondary hemolytic-uremic syndrome
Code First
- , if applicable, any associated:
- COVID-19 (U07.1)
- complications of kidney transplant (T86.1-)
- complications of heart transplant (T86.2-)
- complications of liver transplant (T86.4-)
Code Also
- , if applicable, any associated condition, such as:
- hypertensive emergency (I16.1)
- malignant neoplasm (C00-C96)
- systemic lupus erythematosus (M32.-)
Use Additional
- code, if applicable, for adverse effect to identify drug (T36-T50 with fifth or sixth character 5)
I26: I27.24

2023 ICD-10-CM Diagnosis Code I27.24
Chronic thromboembolic pulmonary hypertension
Applicable To
- Group 4 pulmonary hypertension
Code Also
- associated pulmonary embolism, if applicable (I26.-, I27.82)
I27.21: M34.81

2023 ICD-10-CM Diagnosis Code M34.81
Systemic sclerosis with lung involvement
Code Also
- if applicable:
- other interstitial pulmonary diseases (J84.89)
- secondary pulmonary arterial hypertension (I27.21)
I27.82: I27.24

2023 ICD-10-CM Diagnosis Code I27.24
Chronic thromboembolic pulmonary hypertension
Applicable To
- Group 4 pulmonary hypertension
Code Also
- associated pulmonary embolism, if applicable (I26.-, I27.82)
I27.83: Q21.8
, Q21.8

2023 ICD-10-CM Diagnosis Code Q21.8
Other congenital malformations of cardiac septa
Applicable To
- Eisenmenger's defect
- Pentalogy of Fallot
Code Also
- , if applicable:
- Eisenmenger's complex (I27.83)
- Eisenmenger's syndrome (I27.83)
2023 ICD-10-CM Diagnosis Code Q21.8
Other congenital malformations of cardiac septa
Applicable To
- Eisenmenger's defect
- Pentalogy of Fallot
Code Also
- , if applicable:
- Eisenmenger's complex (I27.83)
- Eisenmenger's syndrome (I27.83)
I34.0: I34.81

2023 ICD-10-CM Diagnosis Code I34.81
Nonrheumatic mitral (valve) annulus calcification
Applicable To
- Nonrheumatic mitral (valve) annular calcification
- Mitral (valve) annulus calcification NOS
Code Also
- , if applicable:
- nonrheumatic mitral (valve) insufficiency (I34.0)
- nonrheumatic mitral (valve) stenosis (I34.2)
I34.2: I34.81

2023 ICD-10-CM Diagnosis Code I34.81
Nonrheumatic mitral (valve) annulus calcification
Applicable To
- Nonrheumatic mitral (valve) annular calcification
- Mitral (valve) annulus calcification NOS
Code Also
- , if applicable:
- nonrheumatic mitral (valve) insufficiency (I34.0)
- nonrheumatic mitral (valve) stenosis (I34.2)
I34.81: I34.0
, I34.2

2023 ICD-10-CM Diagnosis Code I34.2
Nonrheumatic mitral (valve) stenosis
Code Also
- , if applicable:
- nonrheumatic mitral (valve) annulus calcification (I34.81)
2023 ICD-10-CM Diagnosis Code I34.0
Nonrheumatic mitral (valve) insufficiency
Applicable To
- Nonrheumatic mitral (valve) incompetence NOS
- Nonrheumatic mitral (valve) regurgitation NOS
Code Also
- , if applicable:
- nonrheumatic mitral (valve) annulus calcification (I34.81)

Code Also Crosswalk

Myelophthisis

Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]

Castleman disease

Hepatic encephalopathy

Hepatic encephalopathy

Hepatic encephalopathy

Hepatic encephalopathy

Hepatic encephalopathy

Hepatic encephalopathy

Hepatic encephalopathy

Secondary pulmonary arterial hypertension

Multisystem inflammatory syndrome

Multisystem inflammatory syndrome

Secondary pulmonary arterial hypertension

Myelophthisis

Systemic mastocytosis

Other secondary pulmonary hypertension

Other secondary pulmonary hypertension

Systemic mastocytosis

Systemic mastocytosis

Systemic mastocytosis

Conn's syndrome

Systemic mastocytosis

Other secondary pulmonary hypertension

Systemic mastocytosis

Systemic mastocytosis

Systemic mastocytosis

Other secondary pulmonary hypertension

Encounter for pediatric-to-adult transition counseling

Other von Willebrand disease

Systemic mastocytosis

Chronic myelomonocytic leukemia

Hereditary hemolytic-uremic syndrome

Other secondary pulmonary hypertension

Other secondary pulmonary hypertension

Benign neuroendocrine tumors

Malignant neuroendocrine tumors

Hereditary hemolytic-uremic syndrome

Other secondary pulmonary hypertension

Kayser-Fleischer ring

Encounter for pediatric-to-adult transition counseling

Pulmonary hypertension due to lung diseases and hypoxia

Ligneous conjunctivitis

Generalized idiopathic epilepsy and epileptic syndromes

Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy

Alcoholic cardiomyopathy

Degeneration of nervous system due to alcohol

Pain, not elsewhere classified

Encounter for pediatric-to-adult transition counseling

SYNGAP1-related intellectual disability

SYNGAP1-related intellectual disability

SYNGAP1-related intellectual disability

SYNGAP1-related intellectual disability

Intracranial hypotension

SYNGAP1-related intellectual disability

Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy

Other encephalitis, myelitis and encephalomyelitis

Epileptic seizures related to external causes

Migraine with aura

MERRF syndrome

Premenstrual tension syndrome

Premenstrual tension syndrome

Pulmonary hypertension due to lung diseases and hypoxia

Intracranial hypotension

Intracranial hypotension

Intracranial hypotension

Pain disorder with related psychological factors

SYNGAP1-related intellectual disability

Intracranial hypotension

Intracranial hypotension

Intracranial hypotension

Intracranial hypotension

Cerebrospinal fluid leak

Dural tear

Intracranial hypotension following other procedure

Intracranial hypotension following other procedure

Cerebrospinal fluid leak from spinal puncture

Cerebrospinal fluid leak from spinal puncture

Plasminogen deficiency