ICD-10-CM Codes
A00-B99 Certain infectious and parasitic diseases
A50-A64 Infections with a predominantly sexual mode of transmission
A50- Congenital syphilis

2018/2019 ICD-10-CM Diagnosis Code A50.5

Other late congenital syphilis, symptomatic

2016

2017

2018

2019

Non-Billable/Non-Specific Code

A50.5 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
The 2018/2019 edition of ICD-10-CM A50.5 became effective on October 1, 2018.
This is the American ICD-10-CM version of A50.5 - other international versions of ICD-10 A50.5 may differ.

Applicable To

Any congenital syphilitic condition specified as late or manifest two years or more after birth.

The following code(s) above A50.5 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to A50.5:

A00-B99
2019 ICD-10-CM Range A00-B99
Certain infectious and parasitic diseases
Includes
- diseases generally recognized as communicable or transmissible
Type 1 Excludes
- certain localized infections - see body system-related chapters
Type 2 Excludes
- carrier or suspected carrier of infectious disease (Z22.-)
- infectious and parasitic diseases complicating pregnancy, childbirth and the puerperium (O98.-)
- infectious and parasitic diseases specific to the perinatal period (P35-P39)
- influenza and other acute respiratory infections (J00-J22)
Use Additional
- code to identify resistance to antimicrobial drugs (Z16.-)
Certain infectious and parasitic diseases
A50-A64
2019 ICD-10-CM Range A50-A64
Infections with a predominantly sexual mode of transmission
Type 1 Excludes
- human immunodeficiency virus [HIV] disease (B20)
- nonspecific and nongonococcal urethritis (N34.1)
- Reiter's disease (M02.3-)
Infections with a predominantly sexual mode of transmission

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change

Code annotations containing back-references to A50.5:

Code First: N08
, J99
, K23
, K77
, E35
, M02
, I52

ICD-10-CM Diagnosis Code N08
Glomerular disorders in diseases classified elsewhere
Applicable To
- Glomerulonephritis
- Nephritis
- Nephropathy
Code First
- underlying disease, such as:
- amyloidosis (E85.-)
- congenital syphilis (A50.5)
- cryoglobulinemia (D89.1)
- disseminated intravascular coagulation (D65)
- gout (M1A.-, M10.-)
- microscopic polyangiitis (M31.7)
- multiple myeloma (C90.0-)
- sepsis (A40.0-A41.9)
- sickle-cell disease (D57.0-D57.8)
Type 1 Excludes
- glomerulonephritis, nephritis and nephropathy (in):
- antiglomerular basement membrane disease (M31.0)
- diabetes (E08-E13 with .21)
- gonococcal (A54.21)
- Goodpasture's syndrome (M31.0)
- hemolytic-uremic syndrome (D59.3)
- lupus (M32.14)
- mumps (B26.83)
- syphilis (A52.75)
- systemic lupus erythematosus (M32.14)
- Wegener's granulomatosis (M31.31)
- pyelonephritis in diseases classified elsewhere (N16)
- renal tubulo-interstitial disorders classified elsewhere (N16)
ICD-10-CM Diagnosis Code J99
Respiratory disorders in diseases classified elsewhere
Code First
- underlying disease, such as:
- amyloidosis (E85.-)
- ankylosing spondylitis (M45)
- congenital syphilis (A50.5)
- cryoglobulinemia (D89.1)
- early congenital syphilis (A50.0)
- plasminogen deficiency (E88.02)
- schistosomiasis (B65.0-B65.9)
Type 1 Excludes
- respiratory disorders in:
- amebiasis (A06.5)
- blastomycosis (B40.0-B40.2)
- candidiasis (B37.1)
- coccidioidomycosis (B38.0-B38.2)
- cystic fibrosis with pulmonary manifestations (E84.0)
- dermatomyositis (M33.01, M33.11)
- histoplasmosis (B39.0-B39.2)
- late syphilis (A52.72, A52.73)
- polymyositis (M33.21)
- sicca syndrome (M35.02)
- systemic lupus erythematosus (M32.13)
- systemic sclerosis (M34.81)
- Wegener's granulomatosis (M31.30-M31.31)
ICD-10-CM Diagnosis Code K23
Disorders of esophagus in diseases classified elsewhere
Code First
- underlying disease, such as:
- congenital syphilis (A50.5)
Type 1 Excludes
- late syphilis (A52.79)
- megaesophagus due to Chagas' disease (B57.31)
- tuberculosis (A18.83)
ICD-10-CM Diagnosis Code K77
Liver disorders in diseases classified elsewhere
Code First
- underlying disease, such as:
- amyloidosis (E85.-)
- congenital syphilis (A50.0, A50.5)
- congenital toxoplasmosis (P37.1)
- schistosomiasis (B65.0-B65.9)
Type 1 Excludes
- alcoholic hepatitis (K70.1-)
- alcoholic liver disease (K70.-)
- cytomegaloviral hepatitis (B25.1)
- herpesviral [herpes simplex] hepatitis (B00.81)
- infectious mononucleosis with liver disease (B27.0-B27.9 with .9)
- mumps hepatitis (B26.81)
- sarcoidosis with liver disease (D86.89)
- secondary syphilis with liver disease (A51.45)
- syphilis (late) with liver disease (A52.74)
- toxoplasmosis (acquired) hepatitis (B58.1)
- tuberculosis with liver disease (A18.83)
ICD-10-CM Diagnosis Code E35
Disorders of endocrine glands in diseases classified elsewhere
Code First
- underlying disease, such as:
- late congenital syphilis of thymus gland [Dubois disease] (A50.5)
Type 1 Excludes
- Echinococcus granulosus infection of thyroid gland (B67.3)
- meningococcal hemorrhagic adrenalitis (A39.1)
- syphilis of endocrine gland (A52.79)
- tuberculosis of adrenal gland, except calcification (A18.7)
- tuberculosis of endocrine gland NEC (A18.82)
- tuberculosis of thyroid gland (A18.81)
- Waterhouse-Friderichsen syndrome (A39.1)
Use Additional
- code, if applicable, to identify:
- sequelae of tuberculosis of other organs (B90.8)
ICD-10-CM Diagnosis Code M02
Postinfective and reactive arthropathies
Code First
- underlying disease, such as:
- congenital syphilis [Clutton's joints] (A50.5)
- enteritis due to Yersinia enterocolitica (A04.6)
- infective endocarditis (I33.0)
- viral hepatitis (B15-B19)
Type 1 Excludes
- Behçet's disease (M35.2)
- direct infections of joint in infectious and parasitic diseases classified elsewhere (M01.-)
- postmeningococcal arthritis (A39.84)
- mumps arthritis (B26.85)
- rubella arthritis (B06.82)
- syphilis arthritis (late) (A52.77)
- rheumatic fever (I00)
- tabetic arthropathy [Charcôt's] (A52.16)
ICD-10-CM Diagnosis Code I52
Other heart disorders in diseases classified elsewhere
Code First
- underlying disease, such as:
- congenital syphilis (A50.5)
- mucopolysaccharidosis (E76.3)
- schistosomiasis (B65.0-B65.9)
Type 1 Excludes
- heart disease (in):
- gonococcal infection (A54.83)
- meningococcal infection (A39.50)
- rheumatoid arthritis (M05.31)
- syphilis (A52.06)
Type 1 Excludes: K00.2
, K00.4
, Q67.4

ICD-10-CM Diagnosis Code K00.2
Abnormalities of size and form of teeth
Applicable To
- Concrescence of teeth
- Fusion of teeth
- Gemination of teeth
- Dens evaginatus
- Dens in dente
- Dens invaginatus
- Enamel pearls
- Macrodontia
- Microdontia
- Peg-shaped [conical] teeth
- Supernumerary roots
- Taurodontism
- Tuberculum paramolare
Type 1 Excludes
- abnormalities of teeth due to congenital syphilis (A50.5)
- tuberculum Carabelli, which is regarded as a normal variation and should not be coded
ICD-10-CM Diagnosis Code K00.4
Disturbances in tooth formation
Applicable To
- Aplasia and hypoplasia of cementum
- Dilaceration of tooth
- Enamel hypoplasia (neonatal) (postnatal) (prenatal)
- Regional odontodysplasia
- Turner's tooth
Type 1 Excludes
- Hutchinson's teeth and mulberry molars in congenital syphilis (A50.5)
Type 2 Excludes
- mottled teeth (K00.3)
ICD-10-CM Diagnosis Code Q67.4
Other congenital deformities of skull, face and jaw
Applicable To
- Congenital depressions in skull
- Congenital hemifacial atrophy or hypertrophy
- Deviation of nasal septum, congenital
- Squashed or bent nose, congenital
Type 1 Excludes
- dentofacial anomalies [including malocclusion] (M26.-)
- syphilitic saddle nose (A50.5)

ICD-10-CM Codes Adjacent To A50.5

A50.32 Late congenital syphilitic chorioretinitis

A50.39 Other late congenital syphilitic oculopathy

A50.4 Late congenital neurosyphilis [juvenile neurosyphilis]

A50.40 Late congenital neurosyphilis, unspecified

A50.41 Late congenital syphilitic meningitis

A50.42 Late congenital syphilitic encephalitis

A50.43 Late congenital syphilitic polyneuropathy

A50.44 Late congenital syphilitic optic nerve atrophy

A50.45 Juvenile general paresis

A50.49 Other late congenital neurosyphilis

A50.5 Other late congenital syphilis, symptomatic

A50.51 Clutton's joints

A50.52 Hutchinson's teeth

A50.53 Hutchinson's triad

A50.54 Late congenital cardiovascular syphilis

A50.55 Late congenital syphilitic arthropathy

A50.56 Late congenital syphilitic osteochondropathy

A50.57 Syphilitic saddle nose

A50.59 Other late congenital syphilis, symptomatic

A50.6 Late congenital syphilis, latent

A50.7 Late congenital syphilis, unspecified

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2018/2019 ICD-10-CM Diagnosis Code A50.5

Other late congenital syphilis, symptomatic

Certain infectious and parasitic diseases

Infections with a predominantly sexual mode of transmission

Glomerular disorders in diseases classified elsewhere

Respiratory disorders in diseases classified elsewhere

Disorders of esophagus in diseases classified elsewhere

Liver disorders in diseases classified elsewhere

Disorders of endocrine glands in diseases classified elsewhere

Postinfective and reactive arthropathies

Other heart disorders in diseases classified elsewhere

Abnormalities of size and form of teeth

Disturbances in tooth formation

Other congenital deformities of skull, face and jaw