2020 ICD-10-CM Diagnosis Code A81.1

Subacute sclerosing panencephalitis

    2016 2017 2018 2019 2020 Billable/Specific Code
  • A81.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM A81.1 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of A81.1 - other international versions of ICD-10 A81.1 may differ.
Applicable To
  • Dawson's inclusion body encephalitis
  • Van Bogaert's sclerosing leukoencephalopathy
The following code(s) above A81.1 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to A81.1:
  • A00-B99
    2020 ICD-10-CM Range A00-B99

    Certain infectious and parasitic diseases

    Includes
    • diseases generally recognized as communicable or transmissible
    Type 1 Excludes
    • certain localized infections - see body system-related chapters
    Type 2 Excludes
    • carrier or suspected carrier of infectious disease (Z22.-)
    • infectious and parasitic diseases complicating pregnancy, childbirth and the puerperium (O98.-)
    • infectious and parasitic diseases specific to the perinatal period (P35-P39)
    • influenza and other acute respiratory infections (J00-J22)
    Use Additional
    • code to identify resistance to antimicrobial drugs (Z16.-)
    Certain infectious and parasitic diseases
  • A80-A89
    2020 ICD-10-CM Range A80-A89

    Viral and prion infections of the central nervous system

    Type 1 Excludes
    • postpolio syndrome (G14)
    • sequelae of poliomyelitis (B91)
    • sequelae of viral encephalitis (B94.1)
    Viral and prion infections of the central nervous system
  • A81
    ICD-10-CM Diagnosis Code A81

    Atypical virus infections of central nervous system

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Includes
    • diseases of the central nervous system caused by prions
    Use Additional
    • code to identify:
    • dementia with behavioral disturbance (F02.81)
    • dementia without behavioral disturbance (F02.80)
    Atypical virus infections of central nervous system
Clinical Information
  • A rare, slowly progressive encephalitis caused by chronic infection with the measles virus. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive myoclonus; muscle spasticity; seizures; dementia; autonomic dysfunction; and ataxia. Death usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the sspe virus, which is a defective variant of measles virus. (from Adams et al., Principles of Neurology, 6th ed, pp767-8)
  • A rare, slowly progressive post-infectious neurological disorder affecting the central nervous system. It is characterized by seizures, ataxia, myoclonus, personality changes, spasticity, and coma. The symptoms appear several years following measles infection at an early age.
  • Rare chronic progressive encephalitis caused by the measles virus and occurring primarily in children and young adults; death usually occurs within three years; characterized by primary measles infection before the age of two years.
ICD-10-CM A81.1 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 056 Degenerative nervous system disorders with mcc
  • 057 Degenerative nervous system disorders without mcc
  • 791 Prematurity with major problems
  • 793 Full term neonate with major problems

Convert A81.1 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to A81.1:
  • Type 1 Excludes: B05
    ICD-10-CM Diagnosis Code B05

    Measles

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Includes
    • morbilli
    Type 1 Excludes
    • subacute sclerosing panencephalitis (A81.1)

Diagnosis Index entries containing back-references to A81.1:
  • Bodechtel-Guttman disease A81.1 (subacute sclerosing panencephalitis)
  • Dawson's A81.1 (inclusion body)
  • Disease, diseased - see also Syndrome
    • Bodechtel-Guttmann A81.1 (subacute sclerosing panencephalitis)
  • Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute) G04.90
    ICD-10-CM Diagnosis Code G04.90

    Encephalitis and encephalomyelitis, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Ventriculitis (cerebral) NOS
    • Dawson's A81.1 (inclusion body)
    • diffuse sclerosing A81.1
    • inclusion body A81.1
    • subacute sclerosing A81.1
    • van Bogaert's A81.1
  • Leukoencephalitis G04.81
    ICD-10-CM Diagnosis Code G04.81

    Other encephalitis and encephalomyelitis

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Noninfectious acute disseminated encephalomyelitis (noninfectious ADEM)
    • subacute sclerosing A81.1
    • van Bogaert's A81.1 (sclerosing)
  • Leukoencephalopathy G93.49
    - see also Encephalopathy
    ICD-10-CM Diagnosis Code G93.49

    Other encephalopathy

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Encephalopathy NEC
    • van Bogaert's A81.1 (sclerosing)
  • Panencephalitis, subacute, sclerosing A81.1
  • Van Bogaert's leukoencephalopathy A81.1 (sclerosing) (subacute)

ICD-10-CM Codes Adjacent To A81.1
A80.3 Acute paralytic poliomyelitis, other and unspecified
A80.30 Acute paralytic poliomyelitis, unspecified
A80.39 Other acute paralytic poliomyelitis
A80.4 Acute nonparalytic poliomyelitis
A80.9 Acute poliomyelitis, unspecified
A81 Atypical virus infections of central nervous system
A81.0 Creutzfeldt-Jakob disease
A81.00 …… unspecified
A81.01 Variant Creutzfeldt-Jakob disease
A81.09 Other Creutzfeldt-Jakob disease
A81.1 Subacute sclerosing panencephalitis
A81.2 Progressive multifocal leukoencephalopathy
A81.8 Other atypical virus infections of central nervous system
A81.81 Kuru
A81.82 Gerstmann-Sträussler-Scheinker syndrome
A81.83 Fatal familial insomnia
A81.89 Other atypical virus infections of central nervous system
A81.9 Atypical virus infection of central nervous system, unspecified
A82 Rabies
A82.0 Sylvatic rabies
A82.1 Urban rabies

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.