1. ICD-10-CM Codes
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2. A00-B99
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3. A80-A89
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4. A81-
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5. 2023 ICD-10-CM Diagnosis Code A81.1

2023 ICD-10-CM Diagnosis Code A81.1

Subacute sclerosing panencephalitis

2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

• A81.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
• The 2023 edition of ICD-10-CM A81.1 became effective on October 1, 2022.
• This is the American ICD-10-CM version of A81.1 - other international versions of ICD-10 A81.1 may differ.

• A rare, slowly progressive encephalitis caused by chronic infection with the measles virus. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive myoclonus; muscle spasticity; seizures; dementia; autonomic dysfunction; and ataxia. Death usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the sspe virus, which is a defective variant of measles virus. (from Adams et al., Principles of Neurology, 6th ed, pp767-8)
• A rare, slowly progressive post-infectious neurological disorder affecting the central nervous system. It is characterized by seizures, ataxia, myoclonus, personality changes, spasticity, and coma. The symptoms appear several years following measles infection at an early age.
• Rare chronic progressive encephalitis caused by the measles virus and occurring primarily in children and young adults; death usually occurs within three years; characterized by primary measles infection before the age of two years.

• 056 Degenerative nervous system disorders with mcc
• 057 Degenerative nervous system disorders without mcc
• 791 Prematurity with major problems
• 793 Full term neonate with major problems

Convert A81.1 to ICD-9-CM

• 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
• 2017 (effective 10/1/2016): No change
• 2018 (effective 10/1/2017): No change
• 2019 (effective 10/1/2018): No change
• 2020 (effective 10/1/2019): No change
• 2021 (effective 10/1/2020): No change
• 2022 (effective 10/1/2021): No change
• 2023 (effective 10/1/2022): No change

• Type 1 Excludes: B05
  ICD-10-CM Diagnosis Code B05

  Measles

  2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code

  Includes

  • morbilli

  Type 1 Excludes

  • subacute sclerosing panencephalitis (A81.1)

• Bodechtel-Guttman disease A81.1 (subacute sclerosing panencephalitis)
• Dawson's A81.1 (inclusion body)
• Disease, diseased - see also Syndrome
  • Bodechtel-Guttmann A81.1 (subacute sclerosing panencephalitis)
• Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute) G04.90
  ICD-10-CM Diagnosis Code G04.90

  Encephalitis and encephalomyelitis, unspecified

  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

  Applicable To

  • Ventriculitis (cerebral) NOS
  • Dawson's A81.1 (inclusion body)
  • diffuse sclerosing A81.1
  • inclusion body A81.1
  • subacute sclerosing A81.1
  • van Bogaert's A81.1
• Leukoencephalitis G04.81
  ICD-10-CM Diagnosis Code G04.81

  Other encephalitis and encephalomyelitis

  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

  Applicable To

  • Noninfectious acute disseminated encephalomyelitis (noninfectious ADEM)
  • subacute sclerosing A81.1
  • van Bogaert's A81.1 (sclerosing)
• Leukoencephalopathy G93.49
  - see also Encephalopathy
  ICD-10-CM Diagnosis Code G93.49

  Other encephalopathy

  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

  Applicable To

  • Encephalopathy NEC
  • van Bogaert's A81.1 (sclerosing)
• Panencephalitis, subacute, sclerosing A81.1
• Van Bogaert's leukoencephalopathy A81.1 (sclerosing) (subacute)

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.