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ICD-10-CM Codes
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A00-B99
Certain infectious and parasitic diseases
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A80-A89
Viral and prion infections of the central nervous system
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A81-
Atypical virus infections of central nervous system
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2020 ICD-10-CM Diagnosis Code A81.82
Gerstmann-Sträussler-Scheinker syndrome
2016 2017 2018 2019 2020 Billable/Specific Code
- A81.82 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
- Short description: Gerstmann-Straussler-Scheinker syndrome
- The 2020 edition of ICD-10-CM A81.82 became effective on October 1, 2019.
- This is the American ICD-10-CM version of A81.82 - other international versions of ICD-10 A81.82 may differ.
The following code(s) above
A81.82 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
- Applicable To annotations, or
- Code Also annotations, or
- Code First annotations, or
- Excludes1 annotations, or
- Excludes2 annotations, or
- Includes annotations, or
- Note annotations, or
- Use Additional annotations
that may be applicable to
A81.82:
- A00-B99
2020 ICD-10-CM Range A00-B99
Certain infectious and parasitic diseasesIncludes- diseases generally recognized as communicable or transmissible
Type 1 Excludes- certain localized infections - see body system-related chapters
Type 2 Excludes- carrier or suspected carrier of infectious disease (Z22.-)
- infectious and parasitic diseases complicating pregnancy, childbirth and the puerperium (O98.-)
- infectious and parasitic diseases specific to the perinatal period (P35-P39)
- influenza and other acute respiratory infections (J00-J22)
Use Additional- code to identify resistance to antimicrobial drugs (Z16.-)
- A80-A89
2020 ICD-10-CM Range A80-A89
Viral and prion infections of the central nervous systemType 1 Excludes- postpolio syndrome (G14)
- sequelae of poliomyelitis (B91)
- sequelae of viral encephalitis (B94.1)
- A81
ICD-10-CM Diagnosis Code A81
Atypical virus infections of central nervous system
2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
Includes- diseases of the central nervous system caused by prions
Use Additional- code to identify:
- dementia with behavioral disturbance (F02.81)
- dementia without behavioral disturbance (F02.80)
- Gerstmann-straussler-scheinker syndrome
Clinical Information
- A very rare and fatal disorder of spongiform encephalopathy usually caused by mutations of the prion protein (prnp) gene. It is characterized by the accumulation of amyloid in the brain. Signs and symptoms include lack of motor coordination, unsteady gait, and difficulty walking. As the disease progresses, patients develop speech difficulties and dementia.
- An autosomal dominant familial prion disease with a wide spectrum of clinical presentations including ataxia, spastic paraparesis, extrapyramidal signs, and dementia. Clinical onset is in the third to sixth decade of life and the mean duration of illness prior to death is five years. Several kindreds with variable clinical and pathologic features have been described. Pathologic features include cerebral prion protein amyloidosis, and spongiform or neurofibrillary degeneration. (from brain pathol 1998 jul;8(3):499-513; brain pathol 1995 jan;5(1):61-75)
ICD-10-CM A81.82 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
- 056 Degenerative nervous system disorders with mcc
- 057 Degenerative nervous system disorders without mcc
- 974 Hiv with major related condition with mcc
- 975 Hiv with major related condition with cc
- 976 Hiv with major related condition without cc/mcc
Convert A81.82 to ICD-9-CM
Code History
- 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
- 2017 (effective 10/1/2016): No change
- 2018 (effective 10/1/2017): No change
- 2019 (effective 10/1/2018): No change
- 2020 (effective 10/1/2019): No change
- Gerstmann-Sträussler-Scheinker syndrome A81.82 (GSS)
- Syndrome - see also Disease
- Gerstmann-Sträussler-Scheinker A81.82 (GSS)
ICD-10-CM Codes Adjacent To A81.82
A80.9 Acute poliomyelitis, unspecified
A81 Atypical virus infections of central nervous system
A81.0 Creutzfeldt-Jakob disease
A81.01 Variant Creutzfeldt-Jakob disease
A81.09 Other Creutzfeldt-Jakob disease
A81.1 Subacute sclerosing panencephalitis
A81.2 Progressive multifocal leukoencephalopathy
A81.8 Other atypical virus infections of central nervous system
A81.82
Gerstmann-Sträussler-Scheinker syndrome
A81.83 Fatal familial insomnia
A81.89 Other atypical virus infections of central nervous system
A81.9 Atypical virus infection of central nervous system, unspecified
A82.9 Rabies, unspecified
A83 Mosquito-borne viral encephalitis
A83.0 Japanese encephalitis
A83.1 Western equine encephalitis
Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.
