2020 ICD-10-CM Diagnosis Code A81.83

Fatal familial insomnia

    2016 2017 2018 2019 2020 Billable/Specific Code
  • A81.83 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM A81.83 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of A81.83 - other international versions of ICD-10 A81.83 may differ.
Applicable To
  • FFI
The following code(s) above A81.83 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to A81.83:
  • A00-B99
    2020 ICD-10-CM Range A00-B99

    Certain infectious and parasitic diseases

    Includes
    • diseases generally recognized as communicable or transmissible
    Type 1 Excludes
    • certain localized infections - see body system-related chapters
    Type 2 Excludes
    • carrier or suspected carrier of infectious disease (Z22.-)
    • infectious and parasitic diseases complicating pregnancy, childbirth and the puerperium (O98.-)
    • infectious and parasitic diseases specific to the perinatal period (P35-P39)
    • influenza and other acute respiratory infections (J00-J22)
    Use Additional
    • code to identify resistance to antimicrobial drugs (Z16.-)
    Certain infectious and parasitic diseases
  • A80-A89
    2020 ICD-10-CM Range A80-A89

    Viral and prion infections of the central nervous system

    Type 1 Excludes
    • postpolio syndrome (G14)
    • sequelae of poliomyelitis (B91)
    • sequelae of viral encephalitis (B94.1)
    Viral and prion infections of the central nervous system
  • A81
    ICD-10-CM Diagnosis Code A81

    Atypical virus infections of central nervous system

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Includes
    • diseases of the central nervous system caused by prions
    Use Additional
    • code to identify:
    • dementia with behavioral disturbance (F02.81)
    • dementia without behavioral disturbance (F02.80)
    Atypical virus infections of central nervous system
Clinical Information
  • A very rare autosomal dominant inherited sleep disorder caused by a mutation in the gene responsible for the prion protein. It affects individuals usually in their fourth decade. Its initial manifestation is difficulty in falling asleep. It is followed by complete inability to sleep. Patients develop deterioration of their mental and motor functions and die soon after the first symptoms appear, because of the total absence of sleep.
  • An autosomal dominant disorder characterized by degeneration of the thalamus and progressive insomnia. It is caused by a mutation in the prion protein (prions).
ICD-10-CM A81.83 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 056 Degenerative nervous system disorders with mcc
  • 057 Degenerative nervous system disorders without mcc
  • 974 Hiv with major related condition with mcc
  • 975 Hiv with major related condition with cc
  • 976 Hiv with major related condition without cc/mcc

Convert A81.83 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change

Diagnosis Index entries containing back-references to A81.83:
  • Insomnia (organic) G47.00
    ICD-10-CM Diagnosis Code G47.00

    Insomnia, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Insomnia NOS
    • fatal familial A81.83 (FFI)

ICD-10-CM Codes Adjacent To A81.83
A81 Atypical virus infections of central nervous system
A81.0 Creutzfeldt-Jakob disease
A81.00 …… unspecified
A81.01 Variant Creutzfeldt-Jakob disease
A81.09 Other Creutzfeldt-Jakob disease
A81.1 Subacute sclerosing panencephalitis
A81.2 Progressive multifocal leukoencephalopathy
A81.8 Other atypical virus infections of central nervous system
A81.81 Kuru
A81.82 Gerstmann-Sträussler-Scheinker syndrome
A81.83 Fatal familial insomnia
A81.89 Other atypical virus infections of central nervous system
A81.9 Atypical virus infection of central nervous system, unspecified
A82 Rabies
A82.0 Sylvatic rabies
A82.1 Urban rabies
A82.9 Rabies, unspecified
A83 Mosquito-borne viral encephalitis
A83.0 Japanese encephalitis
A83.1 Western equine encephalitis
A83.2 Eastern equine encephalitis

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.