2019 ICD-10-CM Diagnosis Code C86.6

Primary cutaneous CD30-positive T-cell proliferations

    2016 2017 2018 2019 Billable/Specific Code
  • C86.6 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2019 edition of ICD-10-CM C86.6 became effective on October 1, 2018.
  • This is the American ICD-10-CM version of C86.6 - other international versions of ICD-10 C86.6 may differ.
Applicable To
  • Lymphomatoid papulosis
  • Primary cutaneous anaplastic large cell lymphoma
  • Primary cutaneous CD30-positive large T-cell lymphoma
The following code(s) above C86.6 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to C86.6:
  • C00-D49
    2019 ICD-10-CM Range C00-D49

    Neoplasms

    Note
    • Functional activity
    • All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
    • Morphology [Histology]
    • Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
    • Primary malignant neoplasms overlapping site boundaries
    • A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
    • Malignant neoplasm of ectopic tissue
    • Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).
    Neoplasms
  • C81-C96
    2019 ICD-10-CM Range C81-C96

    Malignant neoplasms of lymphoid, hematopoietic and related tissue

    Type 2 Excludes
    • Kaposi's sarcoma of lymph nodes (C46.3)
    • secondary and unspecified neoplasm of lymph nodes (C77.-)
    • secondary neoplasm of bone marrow (C79.52)
    • secondary neoplasm of spleen (C78.89)
    Malignant neoplasms of lymphoid, hematopoietic and related tissue
  • C86
    ICD-10-CM Diagnosis Code C86

    Other specified types of T/NK-cell lymphoma

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • anaplastic large cell lymphoma, ALK negative (C84.7-)
    • anaplastic large cell lymphoma, ALK positive (C84.6-)
    • mature T/NK-cell lymphomas (C84.-)
    • other specified types of non-Hodgkin lymphoma (C85.8-)
    Other specified types of T/NK-cell lymphoma
Approximate Synonyms
  • Lymphoma, primary cutaneous, large t cell, cd30 po
  • Lymphomatoid papulosis
  • Primary cutaneous cd30+ large t-cell lymphoma
Clinical Information
  • A chronic, recurrent cutaneous disorder characterized by the presence of spontaneously regressing papules. The papules are composed of an atypical lymphocytic infiltrate that contains anaplastic cd30-positive t-cells, which are found in type a and diffuse large cell type (type c) lymphomatoid papulosis. In a small number of cases, of type b, the lymphocytic infiltrate is composed of small, cerebriform-like lymphocytes that are often negative for cd30. The majority of cases follow a benign clinical course, but some cases are clonal and may progress to lymphoma. Treatment options include low dose methotrexate and psoralen/uva (puva).
  • An anaplastic large cell lymphoma limited to the skin at the time of diagnosis. Most patients present with solitary or localized skin lesions, which may be tumors, nodules or papules. The t(2;5) translocation that is present in many cases of systemic anaplastic large cell lymphoma, is not found in this disease. (who, 2001)
  • Anaplastic lymphoma of the skin which develops as a primary neoplasm expressing the cd30 antigen. It is characterized by solitary nodules or ulcerated tumors.
  • Clinically benign, histologically malignant, recurrent cutaneous t-cell lymphoproliferative disorder characterized by an infiltration of large atypical cells surrounded by inflammatory cells. The atypical cells resemble reed-sternberg cells of hodgkin disease or the malignant cells of cutaneous t-cell lymphoma. In some cases, lymphomatoid papulosis progresses to lymphomatous conditions including mycosis fungoides; hodgkin disease; cutaneous t-cell lymphoma; or anaplastic large-cell lymphoma.
ICD-10-CM C86.6 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):
  • 820 Lymphoma and leukemia with major o.r. Procedure with mcc
  • 821 Lymphoma and leukemia with major o.r. Procedure with cc
  • 822 Lymphoma and leukemia with major o.r. Procedure without cc/mcc
  • 823 Lymphoma and non-acute leukemia with other procedure with mcc
  • 824 Lymphoma and non-acute leukemia with other procedure with cc
  • 825 Lymphoma and non-acute leukemia with other procedure without cc/mcc
  • 840 Lymphoma and non-acute leukemia with mcc
  • 841 Lymphoma and non-acute leukemia with cc
  • 842 Lymphoma and non-acute leukemia without cc/mcc
  • 974 Hiv with major related condition with mcc
  • 975 Hiv with major related condition with cc
  • 976 Hiv with major related condition without cc/mcc

Convert C86.6 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
Code annotations containing back-references to C86.6:
  • Type 1 Excludes: C84.7
    , C84.Z
    ICD-10-CM Diagnosis Code C84.7

    Anaplastic large cell lymphoma, ALK-negative

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • primary cutaneous CD30-positive T-cell proliferations (C86.6-)
    ICD-10-CM Diagnosis Code C84.Z

    Other mature T/NK-cell lymphomas

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Note
    • If T-cell lineage or involvement is mentioned in conjunction with a specific lymphoma, code to the more specific description.
    Type 1 Excludes
    • angioimmunoblastic T-cell lymphoma (C86.5)
    • blastic NK-cell lymphoma (C86.4)
    • enteropathy-type T-cell lymphoma (C86.2)
    • extranodal NK-cell lymphoma, nasal type (C86.0)
    • hepatosplenic T-cell lymphoma (C86.1)
    • primary cutaneous CD30-positive T-cell proliferations (C86.6)
    • subcutaneous panniculitis-like T-cell lymphoma (C86.3)
    • T-cell leukemia (C91.1-)

Diagnosis Index entries containing back-references to C86.6:
  • Lymphoma (of) (malignant) C85.90
    ICD-10-CM Diagnosis Code C85.90

    Non-Hodgkin lymphoma, unspecified, unspecified site

      2016 2017 2018 2019 Billable/Specific Code
  • Papulosis
    • lymphomatoid C86.6
  • Proliferation(s)
    • primary cutaneous CD30-positive large T-cell C86.6

ICD-10-CM Codes Adjacent To C86.6
C85.97 …… spleen
C85.98 …… lymph nodes of multiple sites
C85.99 …… extranodal and solid organ sites
C86 Other specified types of T/NK-cell lymphoma
C86.0 Extranodal NK/T-cell lymphoma, nasal type
C86.1 Hepatosplenic T-cell lymphoma
C86.2 Enteropathy-type (intestinal) T-cell lymphoma
C86.3 Subcutaneous panniculitis-like T-cell lymphoma
C86.4 Blastic NK-cell lymphoma
C86.5 Angioimmunoblastic T-cell lymphoma
C86.6 Primary cutaneous CD30-positive T-cell proliferations
C88 Malignant immunoproliferative diseases and certain other B-cell lymphomas
C88.0 Waldenström macroglobulinemia
C88.2 Heavy chain disease
C88.3 Immunoproliferative small intestinal disease
C88.4 Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]
C88.8 Other malignant immunoproliferative diseases
C88.9 Malignant immunoproliferative disease, unspecified
C90 Multiple myeloma and malignant plasma cell neoplasms
C90.0 Multiple myeloma
C90.00 …… not having achieved remission

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.