2021 ICD-10-CM Diagnosis Code D47.01

Cutaneous mastocytosis

    2018 - New Code 2019 2020 2021 Billable/Specific Code
  • D47.01 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2021 edition of ICD-10-CM D47.01 became effective on October 1, 2020.
  • This is the American ICD-10-CM version of D47.01 - other international versions of ICD-10 D47.01 may differ.
Applicable To
  • Diffuse cutaneous mastocytosis
  • Maculopapular cutaneous mastocytosis
  • Solitary mastocytoma
  • Telangiectasia macularis eruptiva perstans
  • Urticaria pigmentosa
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as D47.01. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • congenital (diffuse) (maculopapular) cutaneous mastocytosis (
    ICD-10-CM Diagnosis Code Q82.2

    Congenital cutaneous mastocytosis

      2016 2017 2018 - Revised Code 2019 2020 2021 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital diffuse cutaneous mastocytosis
    • Congenital maculopapular cutaneous mastocytosis
    • Congenital urticaria pigmentosa
    Type 1 Excludes
    • cutaneous mastocytosis NOS (D47.01)
    • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
    • malignant mastocytosis (C96.2-)
    • systemic mastocytosis (D47.02)
    • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
    Q82.2
    )
  • congenital urticaria pigmentosa (
    ICD-10-CM Diagnosis Code Q82.2

    Congenital cutaneous mastocytosis

      2016 2017 2018 - Revised Code 2019 2020 2021 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital diffuse cutaneous mastocytosis
    • Congenital maculopapular cutaneous mastocytosis
    • Congenital urticaria pigmentosa
    Type 1 Excludes
    • cutaneous mastocytosis NOS (D47.01)
    • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
    • malignant mastocytosis (C96.2-)
    • systemic mastocytosis (D47.02)
    • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
    Q82.2
    )
  • extracutaneous mastocytoma (
    ICD-10-CM Diagnosis Code D47.09

    Other mast cell neoplasms of uncertain behavior

      2018 - New Code 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Extracutaneous mastocytoma
    • Mast cell tumor NOS
    • Mastocytoma NOS
    • Mastocytosis NOS
    D47.09
    )
The following code(s) above D47.01 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to D47.01:
  • C00-D49
    2021 ICD-10-CM Range C00-D49

    Neoplasms

    Note
    • Functional activity
    • All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
    • Morphology [Histology]
    • Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
    • Primary malignant neoplasms overlapping site boundaries
    • A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
    • Malignant neoplasm of ectopic tissue
    • Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).
    Neoplasms
  • D37-D48
    2021 ICD-10-CM Range D37-D48

    Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes

    Note
    • Categories D37-D44, and D48 classify by site neoplasms of uncertain behavior, i.e., histologic confirmation whether the neoplasm is malignant or benign cannot be made.
    Type 1 Excludes
    • neoplasms of unspecified behavior (D49.-)
    Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes
  • D47.0
    ICD-10-CM Diagnosis Code D47.0

    Mast cell neoplasms of uncertain behavior

      2016 2017 2018 - Converted to Parent Code 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • congenital cutaneous mastocytosis (Q82.2)
    • histiocytic neoplasms of uncertain behavior (D47.Z9)
    • malignant mast cell neoplasm (C96.2-)
    Mast cell neoplasms of uncertain behavior
ICD-10-CM D47.01 is grouped within Diagnostic Related Group(s) (MS-DRG v38.0):
  • 820 Lymphoma and leukemia with major o.r. Procedures with mcc
  • 821 Lymphoma and leukemia with major o.r. Procedures with cc
  • 822 Lymphoma and leukemia with major o.r. Procedures without cc/mcc
  • 823 Lymphoma and non-acute leukemia with other procedures with mcc
  • 824 Lymphoma and non-acute leukemia with other procedures with cc
  • 825 Lymphoma and non-acute leukemia with other procedures without cc/mcc
  • 840 Lymphoma and non-acute leukemia with mcc
  • 841 Lymphoma and non-acute leukemia with cc
  • 842 Lymphoma and non-acute leukemia without cc/mcc

Convert D47.01 to ICD-9-CM

Code History
  • 2018 (effective 10/1/2017): New code
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
Code annotations containing back-references to D47.01:
  • Type 1 Excludes: D89.4
    , Q82.2
    , Q82.2
    , Q82.2
    , L50
    ICD-10-CM Diagnosis Code D89.4

    Mast cell activation syndrome and related disorders

      2017 - New Code 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • aggressive systemic mastocytosis (C96.21)
    • congenital cutaneous mastocytosis (Q82.2)
    • (non-congenital) cutaneous mastocytosis (D47.01)
    • (indolent) systemic mastocytosis (D47.02)
    • malignant mast cell neoplasm (C96.2-)
    • malignant mastocytoma (C96.29)
    • mast cell leukemia (C94.3-)
    • mast cell sarcoma (C96.22)
    • mastocytoma NOS (D47.09)
    • other mast cell neoplasms of uncertain behavior (D47.09)
    • systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (D47.02)
    ICD-10-CM Diagnosis Code Q82.2

    Congenital cutaneous mastocytosis

      2016 2017 2018 - Revised Code 2019 2020 2021 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital diffuse cutaneous mastocytosis
    • Congenital maculopapular cutaneous mastocytosis
    • Congenital urticaria pigmentosa
    Type 1 Excludes
    • cutaneous mastocytosis NOS (D47.01)
    • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
    • malignant mastocytosis (C96.2-)
    • systemic mastocytosis (D47.02)
    • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
    ICD-10-CM Diagnosis Code Q82.2

    Congenital cutaneous mastocytosis

      2016 2017 2018 - Revised Code 2019 2020 2021 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital diffuse cutaneous mastocytosis
    • Congenital maculopapular cutaneous mastocytosis
    • Congenital urticaria pigmentosa
    Type 1 Excludes
    • cutaneous mastocytosis NOS (D47.01)
    • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
    • malignant mastocytosis (C96.2-)
    • systemic mastocytosis (D47.02)
    • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
    ICD-10-CM Diagnosis Code Q82.2

    Congenital cutaneous mastocytosis

      2016 2017 2018 - Revised Code 2019 2020 2021 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital diffuse cutaneous mastocytosis
    • Congenital maculopapular cutaneous mastocytosis
    • Congenital urticaria pigmentosa
    Type 1 Excludes
    • cutaneous mastocytosis NOS (D47.01)
    • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
    • malignant mastocytosis (C96.2-)
    • systemic mastocytosis (D47.02)
    • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
    ICD-10-CM Diagnosis Code L50

    Urticaria

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • allergic contact dermatitis (L23.-)
    • angioneurotic edema (T78.3)
    • giant urticaria (T78.3)
    • hereditary angio-edema (D84.1)
    • Quincke's edema (T78.3)
    • serum urticaria (T80.6-)
    • solar urticaria (L56.3)
    • urticaria neonatorum (P83.8)
    • urticaria papulosa (L28.2)
    • urticaria pigmentosa (D47.01)

Diagnosis Index entries containing back-references to D47.01:
  • Mastocytoma (extracutaneous) D47.09
    ICD-10-CM Diagnosis Code D47.09

    Other mast cell neoplasms of uncertain behavior

      2018 - New Code 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Extracutaneous mastocytoma
    • Mast cell tumor NOS
    • Mastocytoma NOS
    • Mastocytosis NOS
    • solitary D47.01
  • Mastocytosis D47.09
    ICD-10-CM Diagnosis Code D47.09

    Other mast cell neoplasms of uncertain behavior

      2018 - New Code 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Extracutaneous mastocytoma
    • Mast cell tumor NOS
    • Mastocytoma NOS
    • Mastocytosis NOS
  • Telangiectasia, telangiectasis (verrucous) I78.1
    ICD-10-CM Diagnosis Code I78.1

    Nevus, non-neoplastic

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Araneus nevus
    • Senile nevus
    • Spider nevus
    • Stellar nevus
    Type 1 Excludes
    Type 2 Excludes
    • macularis eruptiva perstans D47.01
  • Urticaria L50.9
    ICD-10-CM Diagnosis Code L50.9

    Urticaria, unspecified

      2016 2017 2018 2019 2020 2021 Billable/Specific Code

ICD-10-CM Codes Adjacent To D47.01
D46.21 Refractory anemia with excess of blasts 1
D46.22 Refractory anemia with excess of blasts 2
D46.A Refractory cytopenia with multilineage dysplasia
D46.B Refractory cytopenia with multilineage dysplasia and ring sideroblasts
D46.C Myelodysplastic syndrome with isolated del(5q) chromosomal abnormality
D46.4 Refractory anemia, unspecified
D46.Z Other myelodysplastic syndromes
D46.9 Myelodysplastic syndrome, unspecified
D47 Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
D47.0 Mast cell neoplasms of uncertain behavior
D47.01 Cutaneous mastocytosis
D47.02 Systemic mastocytosis
D47.09 Other mast cell neoplasms of uncertain behavior
D47.1 Chronic myeloproliferative disease
D47.2 Monoclonal gammopathy
D47.3 Essential (hemorrhagic) thrombocythemia
D47.4 Osteomyelofibrosis
D47.Z Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
D47.Z1 Post-transplant lymphoproliferative disorder (PTLD)
D47.Z2 Castleman disease
D47.Z9 Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.