2020 ICD-10-CM Diagnosis Code D47.02

Systemic mastocytosis

    2018 - New Code 2019 2020 Billable/Specific Code
  • D47.02 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM D47.02 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of D47.02 - other international versions of ICD-10 D47.02 may differ.
Applicable To
  • Indolent systemic mastocytosis
  • Isolated bone marrow mastocytosis
  • Smoldering systemic mastocytosis
  • Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
Code Also Help
A code also note instructs that 2 codes may be required to fully describe a condition but the sequencing of the two codes is discretionary, depending on the severity of the conditions and the reason for the encounter.
  • , if applicable, any associated hematological non-mast cell lineage disease, such as:
  • acute myeloid leukemia (
    ICD-10-CM Diagnosis Code C92.6

    Acute myeloid leukemia with 11q23-abnormality

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Applicable To
    • Acute myeloid leukemia with variation of MLL-gene
    C92.6-
    ,
    ICD-10-CM Diagnosis Code C92.A

    Acute myeloid leukemia with multilineage dysplasia

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Applicable To
    • Acute myeloid leukemia with dysplasia of remaining hematopoesis and/or myelodysplastic disease in its history
    C92.A-
    )
  • chronic myelomonocytic leukemia (
    ICD-10-CM Diagnosis Code C93.1

    Chronic myelomonocytic leukemia

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Applicable To
    • Chronic monocytic leukemia
    • CMML-1
    • CMML-2
    • CMML with eosinophilia
    C93.1-
    )
  • essential thrombocytosis (
    ICD-10-CM Diagnosis Code D47.3

    Essential (hemorrhagic) thrombocythemia

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Essential thrombocytosis
    • Idiopathic hemorrhagic thrombocythemia
    D47.3
    )
  • hypereosinophilic syndrome (
    ICD-10-CM Diagnosis Code D72.1

    Eosinophilia

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Allergic eosinophilia
    • Hereditary eosinophilia
    Type 1 Excludes
    • Löffler's syndrome (J82)
    • pulmonary eosinophilia (J82)
    D72.1
    )
  • myelodysplastic syndrome (
    ICD-10-CM Diagnosis Code D46.9

    Myelodysplastic syndrome, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Myelodysplasia NOS
    D46.9
    )
  • myeloproliferative syndrome (
    ICD-10-CM Diagnosis Code D47.1

    Chronic myeloproliferative disease

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Chronic neutrophilic leukemia
    • Myeloproliferative disease, unspecified
    Type 1 Excludes
    • atypical chronic myeloid leukemia BCR/ABL-negative (C92.2-)
    • chronic myeloid leukemia BCR/ABL-positive (C92.1-)
    • myelofibrosis NOS (D75.81)
    • myelophthisic anemia (D61.82)
    • myelophthisis (D61.82)
    • secondary myelofibrosis NOS (D75.81)
    D47.1
    )
  • non-Hodgkin lymphoma (
    ICD-10-CM Diagnosis Code C82

    Follicular lymphoma

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Includes
    • follicular lymphoma with or without diffuse areas
    Type 1 Excludes
    • mature T/NK-cell lymphomas (C84.-)
    • personal history of non-Hodgkin lymphoma (Z85.72)
    C82
    -
    ICD-10-CM Diagnosis Code C85

    Other specified and unspecified types of non-Hodgkin lymphoma

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • other specified types of T/NK-cell lymphoma (C86.-)
    • personal history of non-Hodgkin lymphoma (Z85.72)
    C85
    )
  • plasma cell myeloma (
    ICD-10-CM Diagnosis Code C90.0

    Multiple myeloma

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Applicable To
    • Kahler's disease
    • Medullary plasmacytoma
    • Myelomatosis
    • Plasma cell myeloma
    Type 1 Excludes
    C90.0-
    )
  • polycythemia vera (
    ICD-10-CM Diagnosis Code D45

    Polycythemia vera

      2016 2017 2018 2019 2020 Billable/Specific Code
    Type 1 Excludes
    • familial polycythemia (D75.0)
    • secondary polycythemia (D75.1)
    D45
    )
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as D47.02. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • aggressive systemic mastocytosis (
    ICD-10-CM Diagnosis Code C96.21

    Aggressive systemic mastocytosis

      2018 - New Code 2019 2020 Billable/Specific Code
    C96.21
    )
  • mast cell leukemia (
    ICD-10-CM Diagnosis Code C94.3

    Mast cell leukemia

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    C94.3-
    )
The following code(s) above D47.02 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to D47.02:
  • C00-D49
    2020 ICD-10-CM Range C00-D49

    Neoplasms

    Note
    • Functional activity
    • All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
    • Morphology [Histology]
    • Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
    • Primary malignant neoplasms overlapping site boundaries
    • A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
    • Malignant neoplasm of ectopic tissue
    • Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).
    Neoplasms
  • D37-D48
    2020 ICD-10-CM Range D37-D48

    Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes

    Note
    • Categories D37-D44, and D48 classify by site neoplasms of uncertain behavior, i.e., histologic confirmation whether the neoplasm is malignant or benign cannot be made.
    Type 1 Excludes
    • neoplasms of unspecified behavior (D49.-)
    Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes
  • D47.0
    ICD-10-CM Diagnosis Code D47.0

    Mast cell neoplasms of uncertain behavior

      2016 2017 2018 - Converted to Parent Code 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • congenital cutaneous mastocytosis (Q82.2)
    • histiocytic neoplasms of uncertain behavior (D47.Z9)
    • malignant mast cell neoplasm (C96.2-)
    Mast cell neoplasms of uncertain behavior
ICD-10-CM D47.02 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 820 Lymphoma and leukemia with major o.r. Procedure with mcc
  • 821 Lymphoma and leukemia with major o.r. Procedure with cc
  • 822 Lymphoma and leukemia with major o.r. Procedure without cc/mcc
  • 823 Lymphoma and non-acute leukemia with other procedure with mcc
  • 824 Lymphoma and non-acute leukemia with other procedure with cc
  • 825 Lymphoma and non-acute leukemia with other procedure without cc/mcc
  • 840 Lymphoma and non-acute leukemia with mcc
  • 841 Lymphoma and non-acute leukemia with cc
  • 842 Lymphoma and non-acute leukemia without cc/mcc

Convert D47.02 to ICD-9-CM

Code History
  • 2018 (effective 10/1/2017): New code
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to D47.02:
  • Type 1 Excludes: C96.2
    , D89.4
    , D89.4
    , Q82.2
    ICD-10-CM Diagnosis Code C96.2

    Malignant mast cell neoplasm

      2016 2017 2018 - Converted to Parent Code 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • indolent mastocytosis (D47.02)
    • mast cell leukemia (C94.30)
    • mastocytosis (congenital) (cutaneous) (Q82.2)
    ICD-10-CM Diagnosis Code D89.4

    Mast cell activation syndrome and related disorders

      2017 - New Code 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • aggressive systemic mastocytosis (C96.21)
    • congenital cutaneous mastocytosis (Q82.2)
    • (non-congenital) cutaneous mastocytosis (D47.01)
    • (indolent) systemic mastocytosis (D47.02)
    • malignant mast cell neoplasm (C96.2-)
    • malignant mastocytoma (C96.29)
    • mast cell leukemia (C94.3-)
    • mast cell sarcoma (C96.22)
    • mastocytoma NOS (D47.09)
    • other mast cell neoplasms of uncertain behavior (D47.09)
    • systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (D47.02)
    ICD-10-CM Diagnosis Code D89.4

    Mast cell activation syndrome and related disorders

      2017 - New Code 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • aggressive systemic mastocytosis (C96.21)
    • congenital cutaneous mastocytosis (Q82.2)
    • (non-congenital) cutaneous mastocytosis (D47.01)
    • (indolent) systemic mastocytosis (D47.02)
    • malignant mast cell neoplasm (C96.2-)
    • malignant mastocytoma (C96.29)
    • mast cell leukemia (C94.3-)
    • mast cell sarcoma (C96.22)
    • mastocytoma NOS (D47.09)
    • other mast cell neoplasms of uncertain behavior (D47.09)
    • systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (D47.02)
    ICD-10-CM Diagnosis Code Q82.2

    Congenital cutaneous mastocytosis

      2016 2017 2018 - Revised Code 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital diffuse cutaneous mastocytosis
    • Congenital maculopapular cutaneous mastocytosis
    • Congenital urticaria pigmentosa
    Type 1 Excludes
    • cutaneous mastocytosis NOS (D47.01)
    • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
    • malignant mastocytosis (C96.2-)
    • systemic mastocytosis (D47.02)
    • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)

Diagnosis Index entries containing back-references to D47.02:
  • Disease, diseased - see also Syndrome
    • systemic tissue mast cell D47.02
  • Mast cell
    • disease, systemic tissue D47.02
  • Mastocytosis D47.09
    ICD-10-CM Diagnosis Code D47.09

    Other mast cell neoplasms of uncertain behavior

      2018 - New Code 2019 2020 Billable/Specific Code
    Applicable To
    • Extracutaneous mastocytoma
    • Mast cell tumor NOS
    • Mastocytoma NOS
    • Mastocytosis NOS
    • systemic (indolent) (smoldering)
      • with an associated hematological non-mast cell lineage disease D47.02 (SM-AHNMD)
    • indolent systemic D47.02
    • isolated bone marrow D47.02

ICD-10-CM Codes Adjacent To D47.02
D46.22 Refractory anemia with excess of blasts 2
D46.A Refractory cytopenia with multilineage dysplasia
D46.B Refractory cytopenia with multilineage dysplasia and ring sideroblasts
D46.C Myelodysplastic syndrome with isolated del(5q) chromosomal abnormality
D46.4 Refractory anemia, unspecified
D46.Z Other myelodysplastic syndromes
D46.9 Myelodysplastic syndrome, unspecified
D47 Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
D47.0 Mast cell neoplasms of uncertain behavior
D47.01 Cutaneous mastocytosis
D47.02 Systemic mastocytosis
D47.09 Other mast cell neoplasms of uncertain behavior
D47.1 Chronic myeloproliferative disease
D47.2 Monoclonal gammopathy
D47.3 Essential (hemorrhagic) thrombocythemia
D47.4 Osteomyelofibrosis
D47.Z Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
D47.Z1 Post-transplant lymphoproliferative disorder (PTLD)
D47.Z2 Castleman disease
D47.Z9 Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
D47.9 Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.