ICD-10-CM Codes
C00-D49
D37-D48
D47-
2023 ICD-10-CM Diagnosis Code D47.3

2023 ICD-10-CM Diagnosis Code D47.3

Essential (hemorrhagic) thrombocythemia

2016

2017

2018

2019

2020

2021

2022

2023

Billable/Specific Code

D47.3 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2023 edition of ICD-10-CM D47.3 became effective on October 1, 2022.
This is the American ICD-10-CM version of D47.3 - other international versions of ICD-10 D47.3 may differ.

Applicable To

Essential thrombocytosis
Idiopathic hemorrhagic thrombocythemia
Primary thrombocytosis

Type 2 Excludes

Type 2 Excludes Help

A type 2 excludes note represents "not included here". A type 2 excludes note indicates that the condition excluded is not part of the condition it is excluded from but a patient may have both conditions at the same time. When a type 2 excludes note appears under a code it is acceptable to use both the code (D47.3) and the excluded code together.

reactive thrombocytosis (
ICD-10-CM Diagnosis Code D75.838
Other thrombocytosis
Applicable To
- Reactive thrombocytosis
- Secondary thrombocytosis
Code Also
- underlying condition, if known and applicable
D75.838
)
secondary thrombocytosis (
ICD-10-CM Diagnosis Code D75.838
Other thrombocytosis
Applicable To
- Reactive thrombocytosis
- Secondary thrombocytosis
Code Also
- underlying condition, if known and applicable
D75.838
)
thrombocythemia NOS (
ICD-10-CM Diagnosis Code D75.839
Thrombocytosis, unspecified
Applicable To
- Thrombocythemia NOS
- Thrombocytosis NOS
D75.839
)
thrombocytosis NOS (
ICD-10-CM Diagnosis Code D75.839
Thrombocytosis, unspecified
Applicable To
- Thrombocythemia NOS
- Thrombocytosis NOS
D75.839
)

The following code(s) above D47.3 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to D47.3:

C00-D49
2023 ICD-10-CM Range C00-D49
Neoplasms
Note
- Functional activity
- All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
- Morphology [Histology]
- Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
- Primary malignant neoplasms overlapping site boundaries
- A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
- Malignant neoplasm of ectopic tissue
- Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).
Neoplasms
D37-D48
2023 ICD-10-CM Range D37-D48
Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes
Note
- Categories D37-D44, and D48 classify by site neoplasms of uncertain behavior, i.e., histologic confirmation whether the neoplasm is malignant or benign cannot be made.
Type 1 Excludes
- neoplasms of unspecified behavior (D49.-)
Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes

Approximate Synonyms

Essential thrombocythemia
Thrombocytosis
Thrombocytosis (high blood platelets)

Clinical Information

A chronic myeloproliferative neoplasm that involves primarily the megakaryocytic lineage. It is characterized by sustained thrombocytosis in the blood, increased numbers of large, mature megakaryocytes in the bone marrow, and episodes of thrombosis and/or hemorrhage. The cause is unknown. Median survival times of 10-15 years are commonly reported. (who, 2008)
A clinical syndrome characterized by repeated spontaneous hemorrhages and a remarkable increase in the number of circulating platelets.
An increased number of thrombocytes (platelets) in the blood, without a known cause.
Clinical syndrome characterized by repeated spontaneous hemorrhages and a remarkable increase in the number of circulating platelets.

ICD-10-CM D47.3 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):

814 Reticuloendothelial and immunity disorders with mcc
815 Reticuloendothelial and immunity disorders with cc
816 Reticuloendothelial and immunity disorders without cc/mcc

Convert D47.3 to ICD-9-CM

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change
2021 (effective 10/1/2020): No change
2022 (effective 10/1/2021): No change
2023 (effective 10/1/2022): No change

Code annotations containing back-references to D47.3:

Code Also: D47.02
, I27.29

ICD-10-CM Diagnosis Code D47.02
Systemic mastocytosis
Applicable To
- Indolent systemic mastocytosis
- Isolated bone marrow mastocytosis
- Smoldering systemic mastocytosis
- Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
- , if applicable, any associated hematological non-mast cell lineage disease, such as:
- acute myeloid leukemia (C92.6-, C92.A-)
- chronic myelomonocytic leukemia (C93.1-)
- essential thrombocytosis (D47.3)
- hypereosinophilic syndrome (D72.1)
- myelodysplastic syndrome (D46.9)
- myeloproliferative syndrome (D47.1)
- non-Hodgkin lymphoma (C82-C85)
- plasma cell myeloma (C90.0-)
- polycythemia vera (D45)
Type 1 Excludes
- aggressive systemic mastocytosis (C96.21)
- mast cell leukemia (C94.3-)
ICD-10-CM Diagnosis Code I27.29
Other secondary pulmonary hypertension
Applicable To
- Group 5 pulmonary hypertension
- Pulmonary hypertension with unclear multifactorial mechanisms
- Pulmonary hypertension due to hematologic disorders
- Pulmonary hypertension due to metabolic disorders
- Pulmonary hypertension due to other systemic disorders
Code Also
- other associated disorders, if known, such as:
- chronic myeloid leukemia (C92.10-C92.22)
- essential thrombocythemia (D47.3)
- Gaucher disease (E75.22)
- hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
- hyperthyroidism (E05.-)
- hypothyroidism (E00-E03)
- polycythemia vera (D45)
- sarcoidosis (D86.-)
Type 1 Excludes: D69
, D69

ICD-10-CM Diagnosis Code D69
Purpura and other hemorrhagic conditions
Type 1 Excludes
- benign hypergammaglobulinemic purpura (D89.0)
- cryoglobulinemic purpura (D89.1)
- essential (hemorrhagic) thrombocythemia (D47.3)
- hemorrhagic thrombocythemia (D47.3)
- purpura fulminans (D65)
- thrombotic thrombocytopenic purpura (M31.19)
- Waldenström hypergammaglobulinemic purpura (D89.0)
ICD-10-CM Diagnosis Code D69
Purpura and other hemorrhagic conditions
Type 1 Excludes
- benign hypergammaglobulinemic purpura (D89.0)
- cryoglobulinemic purpura (D89.1)
- essential (hemorrhagic) thrombocythemia (D47.3)
- hemorrhagic thrombocythemia (D47.3)
- purpura fulminans (D65)
- thrombotic thrombocytopenic purpura (M31.19)
- Waldenström hypergammaglobulinemic purpura (D89.0)
Type 2 Excludes: D75.83

ICD-10-CM Diagnosis Code D75.83
Thrombocytosis
Type 2 Excludes
- essential thrombocythemia (D47.3)

Diagnosis Index entries containing back-references to D47.3:

Thrombocythemia (hemorrhagic) D75.839
- see also Thrombocytosis
ICD-10-CM Diagnosis Code D75.839
Thrombocytosis, unspecified
Applicable To
Thrombocythemia NOS
Thrombocytosis NOS
- essential D47.3
- idiopathic D47.3
- primary D47.3
Thrombocytosis D75.839
ICD-10-CM Diagnosis Code D75.839
Thrombocytosis, unspecified
Applicable To
Thrombocythemia NOS
Thrombocytosis NOS
- essential D47.3
- idiopathic D47.3
- primary D47.3

ICD-10-CM Codes Adjacent To D47.3

D46.4 Refractory anemia, unspecified

D46.Z Other myelodysplastic syndromes

D46.9 Myelodysplastic syndrome, unspecified

D47 Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue

D47.0 Mast cell neoplasms of uncertain behavior

D47.01 Cutaneous mastocytosis

D47.02 Systemic mastocytosis

D47.09 Other mast cell neoplasms of uncertain behavior

D47.1 Chronic myeloproliferative disease

D47.2 Monoclonal gammopathy

D47.3 Essential (hemorrhagic) thrombocythemia

D47.4 Osteomyelofibrosis

D47.Z Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue

D47.Z1 Post-transplant lymphoproliferative disorder (PTLD)

D47.Z2 Castleman disease

D47.Z9 Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue

D47.9 Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified

D48 Neoplasm of uncertain behavior of other and unspecified sites

D48.0 Neoplasm of uncertain behavior of bone and articular cartilage

D48.1 Neoplasm of uncertain behavior of connective and other soft tissue

D48.2 Neoplasm of uncertain behavior of peripheral nerves and autonomic nervous system

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2023 ICD-10-CM Diagnosis Code D47.3

Essential (hemorrhagic) thrombocythemia

Other thrombocytosis

Other thrombocytosis

Thrombocytosis, unspecified

Thrombocytosis, unspecified

Neoplasms

Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes

Systemic mastocytosis

Other secondary pulmonary hypertension

Purpura and other hemorrhagic conditions

Purpura and other hemorrhagic conditions

Thrombocytosis

Thrombocytosis, unspecified

Thrombocytosis, unspecified