Sickle-cell disorders D57- >

Use Additional
Use Additional Help
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
  • code for any associated fever (
    ICD-10-CM Diagnosis Code R50.81

    Fever presenting with conditions classified elsewhere

      2016 2017 2018 2019 Billable/Specific Code Manifestation Code
    Code First
    • underlying condition when associated fever is present, such as with:
    • leukemia (C91-C95)
    • neutropenia (D70.-)
    • sickle-cell disease (D57.-)
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as D57. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • other hemoglobinopathies (
    ICD-10-CM Diagnosis Code D58
    • D58 Other hereditary hemolytic anemias
      • D58.0 Hereditary spherocytosis
      • D58.1 Hereditary elliptocytosis
      • D58.2 Other hemoglobinopathies
      • D58.8 Other specified hereditary hemolytic anemias
      • D58.9 Hereditary hemolytic anemia, unspecified
Clinical Information