2020 ICD-10-CM Diagnosis Code D58.0

Hereditary spherocytosis

    2016 2017 2018 2019 2020 Billable/Specific Code
  • D58.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM D58.0 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of D58.0 - other international versions of ICD-10 D58.0 may differ.
Applicable To
  • Acholuric (familial) jaundice
  • Congenital (spherocytic) hemolytic icterus
  • Minkowski-Chauffard syndrome
The following code(s) above D58.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to D58.0:
  • D50-D89
    2020 ICD-10-CM Range D50-D89

    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

    Type 2 Excludes
    • autoimmune disease (systemic) NOS (M35.9)
    • certain conditions originating in the perinatal period (P00-P96)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • human immunodeficiency virus [HIV] disease (B20)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
  • D58
    ICD-10-CM Diagnosis Code D58

    Other hereditary hemolytic anemias

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • hemolytic anemia of the newborn (P55.-)
    Other hereditary hemolytic anemias
Approximate Synonyms
  • Spherocytosis, hereditary
Clinical Information
  • A familial congenital hemolytic anemia characterized by numerous abnormally shaped erythrocytes which are generally spheroidal. The erythrocytes have increased osmotic fragility and are abnormally permeable to sodium ions.
  • An autosomal dominant inherited disorder characterized by the presence of smaller than normal, sphere-shaped erythrocytes. It results in hemolytic anemia and splenomegaly.
  • Autosomal dominant trait marked by splenomegaly, jaundice, and fragile, spheroid erythrocytes which are prematurely cleared by the spleen; anemia is usually mild; treatment is splenectomy.
ICD-10-CM D58.0 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 811 Red blood cell disorders with mcc
  • 812 Red blood cell disorders without mcc

Convert D58.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change

Diagnosis Index entries containing back-references to D58.0:
  • Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) D64.9
    ICD-10-CM Diagnosis Code D64.9

    Anemia, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    • congenital P61.4
      ICD-10-CM Diagnosis Code P61.4

      Other congenital anemias, not elsewhere classified

        2016 2017 2018 2019 2020 Billable/Specific Code Code on Newborn Record
      Applicable To
      • Congenital anemia NOS
      • spherocytic D58.0
  • Disease, diseased - see also Syndrome
  • Jaundice (yellow) R17
    ICD-10-CM Diagnosis Code R17

    Unspecified jaundice

      2016 2017 2018 2019 2020 Billable/Specific Code
    Type 1 Excludes
    • newborn P59.9
      ICD-10-CM Diagnosis Code P59.9

      Neonatal jaundice, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code Code on Newborn Record
      Applicable To
      • Neonatal physiological jaundice (intense)(prolonged) NOS
      • spherocytosis D58.0 (congenital)
  • Spherocytosis (congenital) (familial) (hereditary) D58.0
    • hemoglobin disease D58.0
  • Syndrome - see also Disease
    • Minkowski-Chauffard D58.0

ICD-10-CM Codes Adjacent To D58.0
D57.411 Sickle-cell thalassemia with acute chest syndrome
D57.412 Sickle-cell thalassemia with splenic sequestration
D57.419 …… unspecified
D57.8 Other sickle-cell disorders
D57.80 …… without crisis
D57.81 Other sickle-cell disorders with crisis
D57.811 Other sickle-cell disorders with acute chest syndrome
D57.812 Other sickle-cell disorders with splenic sequestration
D57.819 …… unspecified
D58 Other hereditary hemolytic anemias
D58.0 Hereditary spherocytosis
D58.1 Hereditary elliptocytosis
D58.2 Other hemoglobinopathies
D58.8 Other specified hereditary hemolytic anemias
D58.9 Hereditary hemolytic anemia, unspecified
D59 Acquired hemolytic anemia
D59.0 Drug-induced autoimmune hemolytic anemia
D59.1 Other autoimmune hemolytic anemias
D59.2 Drug-induced nonautoimmune hemolytic anemia
D59.3 Hemolytic-uremic syndrome
D59.4 Other nonautoimmune hemolytic anemias

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.