2019 ICD-10-CM Diagnosis Code D67

Hereditary factor IX deficiency

    2016 2017 2018 2019 Billable/Specific Code
  • D67 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2019 edition of ICD-10-CM D67 became effective on October 1, 2018.
  • This is the American ICD-10-CM version of D67 - other international versions of ICD-10 D67 may differ.
Applicable To
  • Christmas disease
  • Factor IX deficiency (with functional defect)
  • Hemophilia B
  • Plasma thromboplastin component [PTC] deficiency
The following code(s) above D67 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to D67:
  • D50-D89
    2019 ICD-10-CM Range D50-D89

    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

    Type 2 Excludes
    • autoimmune disease (systemic) NOS (M35.9)
    • certain conditions originating in the perinatal period (P00-P96)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • human immunodeficiency virus [HIV] disease (B20)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Approximate Synonyms
  • Acquired factor ix deficiency disease
  • Hemophilia b, acquired
  • Hereditary factor ix deficiency disease
Clinical Information
  • A deficiency of blood coagulation factor ix inherited as an x-linked disorder. (also known as christmas disease, after the first patient studied in detail, not the holy day.) historical and clinical features resemble those in classic hemophilia (hemophilia a), but patients present with fewer symptoms. Severity of bleeding is usually similar in members of a single family. Many patients are asymptomatic until the hemostatic system is stressed by surgery or trauma. Treatment is similar to that for hemophilia a. (from cecil textbook of medicine, 19th ed, p1008)
  • An x-linked inherited bleeding disorder caused by deficiency of the coagulation factor ix.
  • Deficiency of blood coagulation factor ix inherited as an x-linked disorder; clinical features resemble those in hemophilia a, but patients present with fewer symptoms.
ICD-10-CM D67 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):
  • 813 Coagulation disorders

Convert D67 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
Code annotations containing back-references to D67:
  • Code First: M36.2
    , M36.2
    ICD-10-CM Diagnosis Code M36.2

    Hemophilic arthropathy

      2016 2017 2018 2019 Billable/Specific Code Manifestation Code
    Applicable To
    • Hemarthrosis in hemophilic arthropathy
    Code First
    • underlying disease, such as:
    • factor VIII deficiency (D66)
    • with vascular defect (D68.0)
    • factor IX deficiency (D67)
    • hemophilia (classical) (D66)
    • hemophilia B (D67)
    • hemophilia C (D68.1)
    ICD-10-CM Diagnosis Code M36.2

    Hemophilic arthropathy

      2016 2017 2018 2019 Billable/Specific Code Manifestation Code
    Applicable To
    • Hemarthrosis in hemophilic arthropathy
    Code First
    • underlying disease, such as:
    • factor VIII deficiency (D66)
    • with vascular defect (D68.0)
    • factor IX deficiency (D67)
    • hemophilia (classical) (D66)
    • hemophilia B (D67)
    • hemophilia C (D68.1)

Diagnosis Index entries containing back-references to D67:
  • Christmas disease D67
  • Deficiency, deficient
    • anti-hemophilic
      • factor (A) D66
        ICD-10-CM Diagnosis Code D66

        Hereditary factor VIII deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Classical hemophilia
        • Deficiency factor VIII (with functional defect)
        • Hemophilia NOS
        • Hemophilia A
        Type 1 Excludes
        • factor VIII deficiency with vascular defect (D68.0)
        • B D67
    • autoprothrombin
      • II D67
    • factor - see also Deficiency, coagulation
      • IX D67 (congenital) (functional) (hereditary) (with functional defect)
    • plasma thromboplastin
      • component D67 (PTC)
    • Christmas factor D67
    • PTC D67 (plasma thromboplastin component)
  • Disease, diseased - see also Syndrome
    • Christmas D67
  • Hemophilia (classical) (familial) (hereditary) D66
    ICD-10-CM Diagnosis Code D66

    Hereditary factor VIII deficiency

      2016 2017 2018 2019 Billable/Specific Code
    Applicable To
    • Classical hemophilia
    • Deficiency factor VIII (with functional defect)
    • Hemophilia NOS
    • Hemophilia A
    Type 1 Excludes
    • factor VIII deficiency with vascular defect (D68.0)
    • B D67

ICD-10-CM Codes Adjacent To D67
D64.1 Secondary sideroblastic anemia due to disease
D64.2 Secondary sideroblastic anemia due to drugs and toxins
D64.3 Other sideroblastic anemias
D64.4 Congenital dyserythropoietic anemia
D64.8 Other specified anemias
D64.81 Anemia due to antineoplastic chemotherapy
D64.89 Other specified anemias
D64.9 Anemia, unspecified
D65 Disseminated intravascular coagulation [defibrination syndrome]
D66 Hereditary factor VIII deficiency
D67 Hereditary factor IX deficiency
D68 Other coagulation defects
D68.0 Von Willebrand's disease
D68.1 Hereditary factor XI deficiency
D68.2 Hereditary deficiency of other clotting factors
D68.3 Hemorrhagic disorder due to circulating anticoagulants
D68.31 Hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
D68.311 Acquired hemophilia
D68.312 Antiphospholipid antibody with hemorrhagic disorder
D68.318 Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
D68.32 Hemorrhagic disorder due to extrinsic circulating anticoagulants

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.