2020 ICD-10-CM Diagnosis Code D68.0

Von Willebrand's disease

    2016 2017 2018 2019 2020 Billable/Specific Code
  • D68.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM D68.0 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of D68.0 - other international versions of ICD-10 D68.0 may differ.
Applicable To
  • Angiohemophilia
  • Factor VIII deficiency with vascular defect
  • Vascular hemophilia
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as D68.0. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • capillary fragility (hereditary) (
    ICD-10-CM Diagnosis Code D69.8

    Other specified hemorrhagic conditions

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Capillary fragility (hereditary)
    • Vascular pseudohemophilia
    D69.8
    )
  • factor VIII deficiency NOS (
    ICD-10-CM Diagnosis Code D66

    Hereditary factor VIII deficiency

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Classical hemophilia
    • Deficiency factor VIII (with functional defect)
    • Hemophilia NOS
    • Hemophilia A
    Type 1 Excludes
    • factor VIII deficiency with vascular defect (D68.0)
    D66
    )
  • factor VIII deficiency with functional defect (
    ICD-10-CM Diagnosis Code D66

    Hereditary factor VIII deficiency

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Classical hemophilia
    • Deficiency factor VIII (with functional defect)
    • Hemophilia NOS
    • Hemophilia A
    Type 1 Excludes
    • factor VIII deficiency with vascular defect (D68.0)
    D66
    )
The following code(s) above D68.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to D68.0:
  • D50-D89
    2020 ICD-10-CM Range D50-D89

    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

    Type 2 Excludes
    • autoimmune disease (systemic) NOS (M35.9)
    • certain conditions originating in the perinatal period (P00-P96)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • human immunodeficiency virus [HIV] disease (B20)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
  • D68
    ICD-10-CM Diagnosis Code D68

    Other coagulation defects

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • abnormal coagulation profile (R79.1)
    • coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
    • coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
    Other coagulation defects
Approximate Synonyms
  • Von willebrand disease
  • Von willebrand disorder
Clinical Information
  • Group of hemorrhagic disorders in which the von willebrand factor is either quantitatively or qualitatively abnormal. They are usually inherited as an autosomal dominant trait though rare kindreds are autosomal recessive. Symptoms vary depending on severity and disease type but may include prolonged bleeding time, deficiency of factor viii, and impaired platelet adhesion.
  • Hemophilioid disorder due to deficiency of von willebrand factor and thus of factor viii complex.
  • Hereditary or acquired coagulation disorder characterized by a qualitative or quantitative deficiency of the von willebrand factor. The latter plays an important role in platelet adhesion. Signs and symptoms include bruises, nose bleeding, gum bleeding following a dental procedure, heavy menstrual bleeding, and gastrointestinal bleeding.
  • Includes true von willebrand disease with mutation at the vwf locus, as well as mimicking disorders with other mutations (pseudo vwd) and acquired von willebrand syndrome
ICD-10-CM D68.0 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 813 Coagulation disorders

Convert D68.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to D68.0:
  • Code First: M36.2
    ICD-10-CM Diagnosis Code M36.2

    Hemophilic arthropathy

      2016 2017 2018 2019 2020 Billable/Specific Code Manifestation Code
    Applicable To
    • Hemarthrosis in hemophilic arthropathy
    Code First
    • underlying disease, such as:
    • factor VIII deficiency (D66)
    • with vascular defect (D68.0)
    • factor IX deficiency (D67)
    • hemophilia (classical) (D66)
    • hemophilia B (D67)
    • hemophilia C (D68.1)
  • Type 1 Excludes: D66
    , D69.1
    , R04.81
    ICD-10-CM Diagnosis Code D66

    Hereditary factor VIII deficiency

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Classical hemophilia
    • Deficiency factor VIII (with functional defect)
    • Hemophilia NOS
    • Hemophilia A
    Type 1 Excludes
    • factor VIII deficiency with vascular defect (D68.0)
    ICD-10-CM Diagnosis Code D69.1

    Qualitative platelet defects

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Bernard-Soulier [giant platelet] syndrome
    • Glanzmann's disease
    • Grey platelet syndrome
    • Thromboasthenia (hemorrhagic) (hereditary)
    • Thrombocytopathy
    Type 1 Excludes
    • von Willebrand's disease (D68.0)
    ICD-10-CM Diagnosis Code R04.81

    Acute idiopathic pulmonary hemorrhage in infants

      2016 2017 2018 2019 2020 Billable/Specific Code Pediatric Dx (0-17 years)
    Applicable To
    • AIPHI
    • Acute idiopathic hemorrhage in infants over 28 days old
    Type 1 Excludes
    • perinatal pulmonary hemorrhage (P26.-)
    • von Willebrand's disease (D68.0)

Diagnosis Index entries containing back-references to D68.0:
  • Angiohemophilia D68.0 (A) (B)
  • Defect, defective Q89.9
    ICD-10-CM Diagnosis Code Q89.9

    Congenital malformation, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital anomaly NOS
    • Congenital deformity NOS
    • platelets, qualitative D69.1
      ICD-10-CM Diagnosis Code D69.1

      Qualitative platelet defects

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Bernard-Soulier [giant platelet] syndrome
      • Glanzmann's disease
      • Grey platelet syndrome
      • Thromboasthenia (hemorrhagic) (hereditary)
      • Thrombocytopathy
      Type 1 Excludes
      • von Willebrand's disease (D68.0)
      • constitutional D68.0
  • Deficiency, deficient
    • factor - see also Deficiency, coagulation
      • VIII (congenital) (functional) (hereditary) (with functional defect) D66
        ICD-10-CM Diagnosis Code D66

        Hereditary factor VIII deficiency

          2016 2017 2018 2019 2020 Billable/Specific Code
        Applicable To
        • Classical hemophilia
        • Deficiency factor VIII (with functional defect)
        • Hemophilia NOS
        • Hemophilia A
        Type 1 Excludes
        • factor VIII deficiency with vascular defect (D68.0)
        • with vascular defect D68.0
    • platelet NEC D69.1
      ICD-10-CM Diagnosis Code D69.1

      Qualitative platelet defects

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Bernard-Soulier [giant platelet] syndrome
      • Glanzmann's disease
      • Grey platelet syndrome
      • Thromboasthenia (hemorrhagic) (hereditary)
      • Thrombocytopathy
      Type 1 Excludes
      • von Willebrand's disease (D68.0)
      • constitutional D68.0
  • Disease, diseased - see also Syndrome
    • Minot-von Willebrand-Jürgens D68.0 (angiohemophilia)
    • von Willebrand D68.0 (-Jürgens) (angiohemophilia)
  • Hemophilia (classical) (familial) (hereditary) D66
    ICD-10-CM Diagnosis Code D66

    Hereditary factor VIII deficiency

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Classical hemophilia
    • Deficiency factor VIII (with functional defect)
    • Hemophilia NOS
    • Hemophilia A
    Type 1 Excludes
    • factor VIII deficiency with vascular defect (D68.0)
    • vascular D68.0
  • Minot-von Willebrand-Jurgens disease or syndrome D68.0 (angiohemophilia)
  • Pseudohemophilia (Bernuth's) (hereditary) (type B) D68.0
  • Syndrome - see also Disease
    • von Willebrand D68.0 (-Jürgen)
    • Willebrand D68.0 (-Jürgens)
  • Thrombopathy (Bernard-Soulier) D69.1
    ICD-10-CM Diagnosis Code D69.1

    Qualitative platelet defects

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Bernard-Soulier [giant platelet] syndrome
    • Glanzmann's disease
    • Grey platelet syndrome
    • Thromboasthenia (hemorrhagic) (hereditary)
    • Thrombocytopathy
    Type 1 Excludes
    • von Willebrand's disease (D68.0)
    • constitutional D68.0
    • Willebrand-Jurgens D68.0
  • Von Willebrand D68.0 (-Jurgens)(-Minot)
  • Willebrand D68.0 (-Jürgens)

ICD-10-CM Codes Adjacent To D68.0
D64.3 Other sideroblastic anemias
D64.4 Congenital dyserythropoietic anemia
D64.8 Other specified anemias
D64.81 Anemia due to antineoplastic chemotherapy
D64.89 Other specified anemias
D64.9 Anemia, unspecified
D65 Disseminated intravascular coagulation [defibrination syndrome]
D66 Hereditary factor VIII deficiency
D67 Hereditary factor IX deficiency
D68 Other coagulation defects
D68.0 Von Willebrand's disease
D68.1 Hereditary factor XI deficiency
D68.2 Hereditary deficiency of other clotting factors
D68.3 Hemorrhagic disorder due to circulating anticoagulants
D68.31 Hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
D68.311 Acquired hemophilia
D68.312 Antiphospholipid antibody with hemorrhagic disorder
D68.318 Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
D68.32 Hemorrhagic disorder due to extrinsic circulating anticoagulants
D68.4 Acquired coagulation factor deficiency
D68.5 Primary thrombophilia

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.