1. ICD-10-CM Codes
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2. D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
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3. D65-D69 Coagulation defects, purpura and other hemorrhagic conditions
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4. D68- Other coagulation defects
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5. 2022 ICD-10-CM Diagnosis Code D68.1

2022 ICD-10-CM Diagnosis Code D68.1

Hereditary factor XI deficiency

2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code

• D68.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
• The 2022 edition of ICD-10-CM D68.1 became effective on October 1, 2021.
• This is the American ICD-10-CM version of D68.1 - other international versions of ICD-10 D68.1 may differ.

• Factor xi deficiency, type i
• Hemophilia c
• Hemophilia c, type 1
• Hereditary factor xi deficiency disease

• A hereditary deficiency of blood coagulation factor xi (also known as plasma thromboplastin antecedent or pta or antihemophilic factor c) resulting in a systemic blood-clotting defect called hemophilia c or rosenthal's syndrome, that may resemble classical hemophilia.
• A rare inherited bleeding disorder caused by deficiency of coagulation factor xi. It may be asymptomatic or manifest with bleeding.

• 813 Coagulation disorders

Convert D68.1 to ICD-9-CM

• 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
• 2017 (effective 10/1/2016): No change
• 2018 (effective 10/1/2017): No change
• 2019 (effective 10/1/2018): No change
• 2020 (effective 10/1/2019): No change
• 2021 (effective 10/1/2020): No change
• 2022 (effective 10/1/2021): No change

• Code First: M36.2
  ICD-10-CM Diagnosis Code M36.2

  Hemophilic arthropathy

  2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code Manifestation Code

  Applicable To

  • Hemarthrosis in hemophilic arthropathy

  Code First

  • underlying disease, such as:
  • factor VIII deficiency (D66)
  • with vascular defect (D68.0)
  • factor IX deficiency (D67)
  • hemophilia (classical) (D66)
  • hemophilia B (D67)
  • hemophilia C (D68.1)

• Deficiency, deficient
  • anti-hemophilic
    • factor (A) D66
      ICD-10-CM Diagnosis Code D66

      Hereditary factor VIII deficiency

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code

      Applicable To

      • Classical hemophilia
      • Deficiency factor VIII (with functional defect)
      • Hemophilia NOS
      • Hemophilia A

      Type 1 Excludes

      • factor VIII deficiency with vascular defect (D68.0)
      • C D68.1
  • factor - see also Deficiency, coagulation
    • XI D68.1 (congenital) (hereditary)
  • plasma thromboplastin
    • antecedent D68.1 (PTA)
  • PTA D68.1 (plasma thromboplastin antecedent)
• Disease, diseased - see also Syndrome
  • Rosenthal's D68.1 (factor XI deficiency)
• Hemophilia (classical) (familial) (hereditary) D66
  ICD-10-CM Diagnosis Code D66

  Hereditary factor VIII deficiency

  2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code

  Applicable To

  • Classical hemophilia
  • Deficiency factor VIII (with functional defect)
  • Hemophilia NOS
  • Hemophilia A

  Type 1 Excludes

  • factor VIII deficiency with vascular defect (D68.0)
  • C D68.1
• Rosenthal's disease or syndrome D68.1

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.