2019 ICD-10-CM Diagnosis Code D68.2

Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 Billable/Specific Code
  • D68.2 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2019 edition of ICD-10-CM D68.2 became effective on October 1, 2018.
  • This is the American ICD-10-CM version of D68.2 - other international versions of ICD-10 D68.2 may differ.
Applicable To
  • AC globulin deficiency
  • Congenital afibrinogenemia
  • Deficiency of factor I [fibrinogen]
  • Deficiency of factor II [prothrombin]
  • Deficiency of factor V [labile]
  • Deficiency of factor VII [stable]
  • Deficiency of factor X [Stuart-Prower]
  • Deficiency of factor XII [Hageman]
  • Deficiency of factor XIII [fibrin stabilizing]
  • Dysfibrinogenemia (congenital)
  • Hypoproconvertinemia
  • Owren's disease
  • Proaccelerin deficiency
The following code(s) above D68.2 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to D68.2:
  • D50-D89
    2019 ICD-10-CM Range D50-D89

    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

    Type 2 Excludes
    • autoimmune disease (systemic) NOS (M35.9)
    • certain conditions originating in the perinatal period (P00-P96)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • human immunodeficiency virus [HIV] disease (B20)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
  • D68
    ICD-10-CM Diagnosis Code D68

    Other coagulation defects

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • abnormal coagulation profile (R79.1)
    • coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
    • coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
    Other coagulation defects
Approximate Synonyms
  • Clotting factor deficiency, congenital
  • Congenital coagulation factor deficiency
  • Dysfibrinogenemia
  • Dysfibrinogenemia, congenital
  • Factor 10 deficiency
  • Factor 12 deficiency
  • Factor 2 mutation
  • Factor 5 deficiency
  • Factor 7 deficiency
  • Factor ii deficiency
  • Factor v deficiency
  • Factor v quebec
  • Factor vii deficiency
  • Factor x deficiency
  • Factor xii deficiency disease
  • Hereditary dysfibrinogenemia
  • Platelet factor v deficiency (factor v quebec)
Clinical Information
  • A blood coagulation disorder characterized by the complete absence of fibrinogen in the blood, resulting in bleeding.
  • A deficiency of blood coagulation factor v (known as proaccelerin or accelerator globulin or labile factor) leading to a rare hemorrhagic tendency known as owren's disease or parahemophilia. It varies greatly in severity. Factor v deficiency is an autosomal recessive trait. (Dorland, 27th ed)
  • A deficiency or absence of fibrinogen in the blood.
  • A usually inherited blood coagulation disorder characterized by the partial or complete absence of fibrinogen in the blood, resulting in bleeding.
  • A very rare autosomal recessive inherited blood coagulation disorder characterized by deficiency of factor v, resulting in bleeding.
  • An autosomal recessive characteristic or a coagulation disorder acquired in association with vitamin k deficiency. Factor vii is a vitamin k dependent glycoprotein essential to the extrinsic pathway of coagulation.
  • Deficiency or absence of fibrinogen (coagulation factor i) in the blood.
ICD-10-CM D68.2 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):
  • 813 Coagulation disorders

Convert D68.2 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change

Diagnosis Index entries containing back-references to D68.2:
  • Absence (of) (organ or part) (complete or partial)
  • Afibrinogenemia D68.8
    - see also Defect, coagulation
    ICD-10-CM Diagnosis Code D68.8

    Other specified coagulation defects

      2016 2017 2018 2019 Billable/Specific Code
    Type 1 Excludes
    • hemorrhagic disease of newborn (P53)
    • congenital D68.2
  • Defect, defective Q89.9
    ICD-10-CM Diagnosis Code Q89.9

    Congenital malformation, unspecified

      2016 2017 2018 2019 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital anomaly NOS
    • Congenital deformity NOS
    • coagulation (factor) D68.9
      - see also Deficiency, factor
      ICD-10-CM Diagnosis Code D68.9

      Coagulation defect, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      • hereditary NEC D68.2
    • fibrin polymerization D68.2
    • Hageman D68.2 (factor)
  • Deficiency, deficient
    • AC globulin (congenital) (hereditary) D68.2
    • autoprothrombin
      • I D68.2
      • C D68.2
    • coagulation NOS D68.9
      ICD-10-CM Diagnosis Code D68.9

      Coagulation defect, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      • clotting factor NEC D68.2 - see also Deficiency, factor
    • factor - see also Deficiency, coagulation
      • Hageman D68.2
      • I D68.2 (congenital) (hereditary)
      • II D68.2 (congenital) (hereditary)
      • V D68.2 (congenital) (hereditary)
      • VII D68.2 (congenital) (hereditary)
      • X D68.2 (congenital) (hereditary)
      • XII D68.2 (congenital) (hereditary)
      • XIII D68.2 (congenital) (hereditary)
    • fibrin-stabilizing factor (congenital) (hereditary) D68.2
    • fibrinogen (congenital) (hereditary) D68.2
    • labile factor (congenital) (hereditary) D68.2
    • proaccelerin (congenital) (hereditary) D68.2
    • proconvertin factor (congenital) (hereditary) D68.2
    • prothrombin (congenital) (heredItary) D68.2
    • stable factor (congenital) (hereditary) D68.2
    • thrombokinase D68.2
    • accelerator globulin D68.2 (Ac G) (blood)
    • activating factor D68.2 (blood)
    • clotting factor NEC D68.2 (hereditary) - see also Deficiency, factor
    • contact factor D68.2
    • fibrinase D68.2
    • glass factor D68.2
    • Hageman factor D68.2
    • Laki-Lorand factor D68.2
    • Prower factor D68.2
    • SPCA D68.2 (factor VII)
    • Stuart-Prower D68.2 (factor X)
  • Disease, diseased - see also Syndrome
    • Hageman D68.2 (congenital factor XII deficiency)
    • Stuart-Prower D68.2 (congenital factor X deficiency)
    • Stuart's D68.2 (congenital factor X deficiency)
  • Dysfibrinogenemia D68.2 (congenital)
  • Fibrinogenopenia D68.8
    ICD-10-CM Diagnosis Code D68.8

    Other specified coagulation defects

      2016 2017 2018 2019 Billable/Specific Code
    Type 1 Excludes
    • hemorrhagic disease of newborn (P53)
    • congenital D68.2
  • Fibrinopenia (hereditary) D68.2
  • Hageman's factor defect, deficiency or disease D68.2
  • Hypofibrinogenemia D68.8
    ICD-10-CM Diagnosis Code D68.8

    Other specified coagulation defects

      2016 2017 2018 2019 Billable/Specific Code
    Type 1 Excludes
    • hemorrhagic disease of newborn (P53)
    • congenital D68.2 (hereditary)
  • Hypoproconvertinemia, congenital D68.2 (hereditary)
  • Hypoprothrombinemia (congenital) (hereditary) (idiopathic) D68.2
  • Owren's disease or syndrome D68.2 (parahemophilia)
  • Parahemophilia D68.2 - see also Defect, coagulation
  • Stuart deficiency disease D68.2 (factor X)
  • Stuart-Prower factor deficiency D68.2 (factor X)
  • Syndrome - see also Disease
    • Owren's D68.2

ICD-10-CM Codes Adjacent To D68.2
D64.8 Other specified anemias
D64.81 Anemia due to antineoplastic chemotherapy
D64.89 Other specified anemias
D64.9 Anemia, unspecified
D65 Disseminated intravascular coagulation [defibrination syndrome]
D66 Hereditary factor VIII deficiency
D67 Hereditary factor IX deficiency
D68 Other coagulation defects
D68.0 Von Willebrand's disease
D68.1 Hereditary factor XI deficiency
D68.2 Hereditary deficiency of other clotting factors
D68.3 Hemorrhagic disorder due to circulating anticoagulants
D68.31 Hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
D68.311 Acquired hemophilia
D68.312 Antiphospholipid antibody with hemorrhagic disorder
D68.318 Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
D68.32 Hemorrhagic disorder due to extrinsic circulating anticoagulants
D68.4 Acquired coagulation factor deficiency
D68.5 Primary thrombophilia
D68.51 Activated protein C resistance
D68.52 Prothrombin gene mutation

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.