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ICD-10-CM Codes
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D50-D89
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
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D65-D69
Coagulation defects, purpura and other hemorrhagic conditions
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D68-
Other coagulation defects
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2022 ICD-10-CM Diagnosis Code D68.4
2022 ICD-10-CM Diagnosis Code D68.4
Acquired coagulation factor deficiency
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
- D68.4 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
- The 2022 edition of ICD-10-CM D68.4 became effective on October 1, 2021.
- This is the American ICD-10-CM version of D68.4 - other international versions of ICD-10 D68.4 may differ.
Applicable To- Deficiency of coagulation factor due to liver disease
- Deficiency of coagulation factor due to vitamin K deficiency
Type 1 ExcludesType 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as D68.4. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
The following code(s) above
D68.4 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
- Applicable To annotations, or
- Code Also annotations, or
- Code First annotations, or
- Excludes1 annotations, or
- Excludes2 annotations, or
- Includes annotations, or
- Note annotations, or
- Use Additional annotations
that may be applicable to
D68.4:
Approximate Synonyms
- Acquired factor viii deficiency disease
- Acquired factor x deficiency disease
- Acquired factor xii deficiency disease
- Clotting factor deficiency due to liver disease
- Clotting factor deficiency from vitamin k deficien
- Clotting factor deficiency, acquired
- Deficiency of coagulation factor due to liver disease
- Deficiency of coagulation factor due to vitamin k deficiency
- Factor 10 deficiency, acquired
- Factor 12 deficiency, acquired
- Factor 8 deficiency, acquired
Clinical Information
- Deficiency of a coagulation factor that is not caused by genetic alterations. Causes include vitamin k deficiency, amyloidosis, and severe liver disease.
ICD-10-CM D68.4 is grouped within Diagnostic Related Group(s) (MS-DRG v39.0):
- 813 Coagulation disorders
Convert D68.4 to ICD-9-CM
Code History
- 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
- 2017 (effective 10/1/2016): No change
- 2018 (effective 10/1/2017): No change
- 2019 (effective 10/1/2018): No change
- 2020 (effective 10/1/2019): No change
- 2021 (effective 10/1/2020): No change
- 2022 (effective 10/1/2021): No change
Code annotations containing back-references to D68.4:
- Defect, defective Q89.9
ICD-10-CM Diagnosis Code Q89.9
Congenital malformation, unspecified
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code POA Exempt
Applicable To- Congenital anomaly NOS
- Congenital deformity NOS
- coagulation (factor) D68.9 - see also Deficiency, factor
ICD-10-CM Diagnosis Code D68.9
Coagulation defect, unspecified
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
- due to
- liver disease D68.4
- vitamin K deficiency D68.4
- acquired D68.4
- Deficiency, deficient
- AC globulin (congenital) (hereditary) D68.2
ICD-10-CM Diagnosis Code D68.2
Hereditary deficiency of other clotting factors
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
Applicable To- AC globulin deficiency
- Congenital afibrinogenemia
- Deficiency of factor I [fibrinogen]
- Deficiency of factor II [prothrombin]
- Deficiency of factor V [labile]
- Deficiency of factor VII [stable]
- Deficiency of factor X [Stuart-Prower]
- Deficiency of factor XII [Hageman]
- Deficiency of factor XIII [fibrin stabilizing]
- Dysfibrinogenemia (congenital)
- Hypoproconvertinemia
- Owren's disease
- Proaccelerin deficiency
- coagulation NOS D68.9
ICD-10-CM Diagnosis Code D68.9
Coagulation defect, unspecified
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
- due to
- hyperprothrombinemia D68.4
- liver disease D68.4
- vitamin K deficiency D68.4
- acquired D68.4 (any)
- factor - see also Deficiency, coagulation
- multiple (congenital) D68.8
ICD-10-CM Diagnosis Code D68.8
Other specified coagulation defects
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
Type 1 Excludes- hemorrhagic disease of newborn (P53)
- fibrin-stabilizing factor (congenital) (hereditary) D68.2
ICD-10-CM Diagnosis Code D68.2
Hereditary deficiency of other clotting factors
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
Applicable To- AC globulin deficiency
- Congenital afibrinogenemia
- Deficiency of factor I [fibrinogen]
- Deficiency of factor II [prothrombin]
- Deficiency of factor V [labile]
- Deficiency of factor VII [stable]
- Deficiency of factor X [Stuart-Prower]
- Deficiency of factor XII [Hageman]
- Deficiency of factor XIII [fibrin stabilizing]
- Dysfibrinogenemia (congenital)
- Hypoproconvertinemia
- Owren's disease
- Proaccelerin deficiency
- labile factor (congenital) (hereditary) D68.2
ICD-10-CM Diagnosis Code D68.2
Hereditary deficiency of other clotting factors
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
Applicable To- AC globulin deficiency
- Congenital afibrinogenemia
- Deficiency of factor I [fibrinogen]
- Deficiency of factor II [prothrombin]
- Deficiency of factor V [labile]
- Deficiency of factor VII [stable]
- Deficiency of factor X [Stuart-Prower]
- Deficiency of factor XII [Hageman]
- Deficiency of factor XIII [fibrin stabilizing]
- Dysfibrinogenemia (congenital)
- Hypoproconvertinemia
- Owren's disease
- Proaccelerin deficiency
- proaccelerin (congenital) (hereditary) D68.2
ICD-10-CM Diagnosis Code D68.2
Hereditary deficiency of other clotting factors
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
Applicable To- AC globulin deficiency
- Congenital afibrinogenemia
- Deficiency of factor I [fibrinogen]
- Deficiency of factor II [prothrombin]
- Deficiency of factor V [labile]
- Deficiency of factor VII [stable]
- Deficiency of factor X [Stuart-Prower]
- Deficiency of factor XII [Hageman]
- Deficiency of factor XIII [fibrin stabilizing]
- Dysfibrinogenemia (congenital)
- Hypoproconvertinemia
- Owren's disease
- Proaccelerin deficiency
- proconvertin factor (congenital) (hereditary) D68.2
ICD-10-CM Diagnosis Code D68.2
Hereditary deficiency of other clotting factors
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
Applicable To- AC globulin deficiency
- Congenital afibrinogenemia
- Deficiency of factor I [fibrinogen]
- Deficiency of factor II [prothrombin]
- Deficiency of factor V [labile]
- Deficiency of factor VII [stable]
- Deficiency of factor X [Stuart-Prower]
- Deficiency of factor XII [Hageman]
- Deficiency of factor XIII [fibrin stabilizing]
- Dysfibrinogenemia (congenital)
- Hypoproconvertinemia
- Owren's disease
- Proaccelerin deficiency
- prothrombin (congenital) (heredItary) D68.2
ICD-10-CM Diagnosis Code D68.2
Hereditary deficiency of other clotting factors
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
Applicable To- AC globulin deficiency
- Congenital afibrinogenemia
- Deficiency of factor I [fibrinogen]
- Deficiency of factor II [prothrombin]
- Deficiency of factor V [labile]
- Deficiency of factor VII [stable]
- Deficiency of factor X [Stuart-Prower]
- Deficiency of factor XII [Hageman]
- Deficiency of factor XIII [fibrin stabilizing]
- Dysfibrinogenemia (congenital)
- Hypoproconvertinemia
- Owren's disease
- Proaccelerin deficiency
- stable factor (congenital) (hereditary) D68.2
ICD-10-CM Diagnosis Code D68.2
Hereditary deficiency of other clotting factors
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
Applicable To- AC globulin deficiency
- Congenital afibrinogenemia
- Deficiency of factor I [fibrinogen]
- Deficiency of factor II [prothrombin]
- Deficiency of factor V [labile]
- Deficiency of factor VII [stable]
- Deficiency of factor X [Stuart-Prower]
- Deficiency of factor XII [Hageman]
- Deficiency of factor XIII [fibrin stabilizing]
- Dysfibrinogenemia (congenital)
- Hypoproconvertinemia
- Owren's disease
- Proaccelerin deficiency
- Fibrinopenia (hereditary) D68.2
ICD-10-CM Diagnosis Code D68.2
Hereditary deficiency of other clotting factors
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
Applicable To- AC globulin deficiency
- Congenital afibrinogenemia
- Deficiency of factor I [fibrinogen]
- Deficiency of factor II [prothrombin]
- Deficiency of factor V [labile]
- Deficiency of factor VII [stable]
- Deficiency of factor X [Stuart-Prower]
- Deficiency of factor XII [Hageman]
- Deficiency of factor XIII [fibrin stabilizing]
- Dysfibrinogenemia (congenital)
- Hypoproconvertinemia
- Owren's disease
- Proaccelerin deficiency
- Hemophilia (classical) (familial) (hereditary) D66
ICD-10-CM Diagnosis Code D66
Hereditary factor VIII deficiency
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
Applicable To- Classical hemophilia
- Deficiency factor VIII (with functional defect)
- Hemophilia NOS
- Hemophilia A
Type 1 Excludes- factor VIII deficiency with vascular defect (D68.0)
- Hyperprothrombinemia, causing coagulation factor deficiency D68.4
- Hypoprothrombinemia (congenital) (hereditary) (idiopathic) D68.2
ICD-10-CM Diagnosis Code D68.2
Hereditary deficiency of other clotting factors
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
Applicable To- AC globulin deficiency
- Congenital afibrinogenemia
- Deficiency of factor I [fibrinogen]
- Deficiency of factor II [prothrombin]
- Deficiency of factor V [labile]
- Deficiency of factor VII [stable]
- Deficiency of factor X [Stuart-Prower]
- Deficiency of factor XII [Hageman]
- Deficiency of factor XIII [fibrin stabilizing]
- Dysfibrinogenemia (congenital)
- Hypoproconvertinemia
- Owren's disease
- Proaccelerin deficiency
ICD-10-CM Codes Adjacent To D68.4
D68 Other coagulation defects
D68.0 Von Willebrand's disease
D68.1 Hereditary factor XI deficiency
D68.2 Hereditary deficiency of other clotting factors
D68.3 Hemorrhagic disorder due to circulating anticoagulants
D68.31 Hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
D68.312 Antiphospholipid antibody with hemorrhagic disorder
D68.318 Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
D68.32 Hemorrhagic disorder due to extrinsic circulating anticoagulants
D68.4
Acquired coagulation factor deficiency
D68.5 Primary thrombophilia
D68.51 Activated protein C resistance
D68.52 Prothrombin gene mutation
D68.59 Other primary thrombophilia
D68.6 Other thrombophilia
D68.61 Antiphospholipid syndrome
D68.62 Lupus anticoagulant syndrome
D68.8 Other specified coagulation defects
D68.9 Coagulation defect, unspecified
Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.