ICD-10-CM Codes
D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
D65-D69 Coagulation defects, purpura and other hemorrhagic conditions
D69- Purpura and other hemorrhagic conditions
2022 ICD-10-CM Diagnosis Code D69.42

2022 ICD-10-CM Diagnosis Code D69.42

Congenital and hereditary thrombocytopenia purpura

2016

2017

2018

2019

2020

2021

2022

Billable/Specific Code

D69.42 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2022 edition of ICD-10-CM D69.42 became effective on October 1, 2021.
This is the American ICD-10-CM version of D69.42 - other international versions of ICD-10 D69.42 may differ.

Applicable To

Congenital thrombocytopenia
Hereditary thrombocytopenia

Code First

Code First Help

Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.

congential or hereditary disorder, such as:
thrombocytopenia with absent radius (TAR syndrome) (
ICD-10-CM Diagnosis Code Q87.2
Congenital malformation syndromes predominantly involving limbs
Applicable To
- Holt-Oram syndrome
- Klippel-Trenaunay-Weber syndrome
- Nail patella syndrome
- Rubinstein-Taybi syndrome
- Sirenomelia syndrome
- Thrombocytopenia with absent radius [TAR] syndrome
- VATER syndrome
Q87.2
)

The following code(s) above D69.42 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to D69.42:

D50-D89
2022 ICD-10-CM Range D50-D89
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Type 2 Excludes
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
D69
ICD-10-CM Diagnosis Code D69
Purpura and other hemorrhagic conditions
Type 1 Excludes
- benign hypergammaglobulinemic purpura (D89.0)
- cryoglobulinemic purpura (D89.1)
- essential (hemorrhagic) thrombocythemia (D47.3)
- hemorrhagic thrombocythemia (D47.3)
- purpura fulminans (D65)
- thrombotic thrombocytopenic purpura (M31.19)
- Waldenström hypergammaglobulinemic purpura (D89.0)
Purpura and other hemorrhagic conditions
D69.4
ICD-10-CM Diagnosis Code D69.4
Other primary thrombocytopenia
Type 1 Excludes
- transient neonatal thrombocytopenia (P61.0)
- Wiskott-Aldrich syndrome (D82.0)
Other primary thrombocytopenia

Approximate Synonyms

Congenital and hereditary thrombocytopenic purpura

ICD-10-CM D69.42 is grouped within Diagnostic Related Group(s) (MS-DRG v39.0):

813 Coagulation disorders

Convert D69.42 to ICD-9-CM

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change
2021 (effective 10/1/2020): No change
2022 (effective 10/1/2021): No change

Diagnosis Index entries containing back-references to D69.42:

Purpura D69.2
ICD-10-CM Diagnosis Code D69.2
Other nonthrombocytopenic purpura
Applicable To
Purpura NOS
Purpura simplex
Senile purpura
- thrombocytopenic D69.49
  ICD-10-CM Diagnosis Code D69.49
  Other primary thrombocytopenia
  2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
  Applicable To
  Megakaryocytic hypoplasia
  Primary thrombocytopenia NOS
  - congenital D69.42
  - hereditary D69.42
Thrombocytopenia, thrombocytopenic D69.6
ICD-10-CM Diagnosis Code D69.6
Thrombocytopenia, unspecified
- congenital D69.42
- hereditary D69.42

ICD-10-CM Codes Adjacent To D69.42

D68.69 Other thrombophilia

D68.8 Other specified coagulation defects

D68.9 Coagulation defect, unspecified

D69 Purpura and other hemorrhagic conditions

D69.0 Allergic purpura

D69.1 Qualitative platelet defects

D69.2 Other nonthrombocytopenic purpura

D69.3 Immune thrombocytopenic purpura

D69.4 Other primary thrombocytopenia

D69.41 Evans syndrome

D69.42 Congenital and hereditary thrombocytopenia purpura

D69.49 Other primary thrombocytopenia

D69.5 Secondary thrombocytopenia

D69.51 Posttransfusion purpura

D69.59 Other secondary thrombocytopenia

D69.6 Thrombocytopenia, unspecified

D69.8 Other specified hemorrhagic conditions

D69.9 Hemorrhagic condition, unspecified

D70 Neutropenia

D70.0 Congenital agranulocytosis

D70.1 Agranulocytosis secondary to cancer chemotherapy

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2022 ICD-10-CM Diagnosis Code D69.42

Congenital and hereditary thrombocytopenia purpura

Congenital malformation syndromes predominantly involving limbs

Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

Purpura and other hemorrhagic conditions

Other primary thrombocytopenia

Other nonthrombocytopenic purpura

Other primary thrombocytopenia

Thrombocytopenia, unspecified