2023 ICD-10-CM Diagnosis Code D70.0

Congenital agranulocytosis

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • D70.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2023 edition of ICD-10-CM D70.0 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of D70.0 - other international versions of ICD-10 D70.0 may differ.
Applicable To
  • Congenital neutropenia
  • Infantile genetic agranulocytosis
  • Kostmann's disease
The following code(s) above D70.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to D70.0:
  • D50-D89
    2023 ICD-10-CM Range D50-D89

    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

    Type 2 Excludes
    • autoimmune disease (systemic) NOS (M35.9)
    • certain conditions originating in the perinatal period (P00-P96)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • human immunodeficiency virus [HIV] disease (B20)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
  • D70
    ICD-10-CM Diagnosis Code D70

    Neutropenia

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Includes
    • agranulocytosis
    • decreased absolute neurophile count (ANC)
    Type 1 Excludes
    • neutropenic splenomegaly (D73.81)
    • transient neonatal neutropenia (P61.5)
    Use Additional
    Neutropenia
Approximate Synonyms
  • Congenital neutropenia
  • Neutropenia, congenital
Clinical Information
  • A rare disorder characterized by recurrent infantile infections and absence of neutrophils in the peripheral blood.
  • An inherited disorder in which there is a lower-than-normal number of neutrophils (a type of white blood cell that is important in fighting infections). Infants with the disorder get infections caused by bacteria, and are at an increased risk of acute myelogenous leukemia (aml) or myelodysplasia (a bone marrow disorder).
ICD-10-CM D70.0 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):
  • 808 Major hematological and immunological diagnoses except sickle cell crisis and coagulation disorders with mcc
  • 809 Major hematological and immunological diagnoses except sickle cell crisis and coagulation disorders with cc
  • 810 Major hematological and immunological diagnoses except sickle cell crisis and coagulation disorders without cc/mcc

Convert D70.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change
Code annotations containing back-references to D70.0:
  • Type 1 Excludes: P61.5
    ICD-10-CM Diagnosis Code P61.5

    Transient neonatal neutropenia

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Code on Newborn Record
    Type 1 Excludes
    • congenital neutropenia (nontransient) (D70.0)

Diagnosis Index entries containing back-references to D70.0:
  • Agranulocytosis (chronic) (cyclical) (genetic) (infantile) (periodic) (pernicious) D70.9
    - see also Neutropenia
    ICD-10-CM Diagnosis Code D70.9

    Neutropenia, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • congenital D70.0
  • Aleukia
    • congenital D70.0
  • Disease, diseased - see also Syndrome
    • Kostmann's D70.0 (infantile genetic agranulocytosis)
  • Leukopenia D72.819
    ICD-10-CM Diagnosis Code D72.819

    Decreased white blood cell count, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    • Decreased leukocytes, unspecified
    • Leukocytopenia, unspecified
    • Leukopenia
    Type 1 Excludes
    • malignant leukopenia (D70.9)
    • congenital D70.0
    • cyclic D70.0
    • familial D70.0
    • infantile genetic D70.0
    • periodic D70.0
  • Neutropenia, neutropenic (chronic) (genetic) (idiopathic) (immune) (infantile) (malignant) (pernicious) (splenic) D70.9
    ICD-10-CM Diagnosis Code D70.9

    Neutropenia, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • congenital D70.0 (primary)
  • Syndrome - see also Disease
    • Kostmann's D70.0

ICD-10-CM Codes Adjacent To D70.0
D69.41 Evans syndrome
D69.42 Congenital and hereditary thrombocytopenia purpura
D69.49 Other primary thrombocytopenia
D69.5 Secondary thrombocytopenia
D69.51 Posttransfusion purpura
D69.59 Other secondary thrombocytopenia
D69.6 Thrombocytopenia, unspecified
D69.8 Other specified hemorrhagic conditions
D69.9 Hemorrhagic condition, unspecified
D70 Neutropenia
D70.0 Congenital agranulocytosis
D70.1 Agranulocytosis secondary to cancer chemotherapy
D70.2 Other drug-induced agranulocytosis
D70.3 Neutropenia due to infection
D70.4 Cyclic neutropenia
D70.8 Other neutropenia
D70.9 Neutropenia, unspecified
D71 Functional disorders of polymorphonuclear neutrophils
D72 Other disorders of white blood cells
D72.0 Genetic anomalies of leukocytes
D72.1 Eosinophilia

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.