2023 ICD-10-CM Diagnosis Code D74.0

Congenital methemoglobinemia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • D74.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2023 edition of ICD-10-CM D74.0 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of D74.0 - other international versions of ICD-10 D74.0 may differ.
Applicable To
  • Congenital NADH-methemoglobin reductase deficiency
  • Hemoglobin-M [Hb-M] disease
  • Methemoglobinemia, hereditary
The following code(s) above D74.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to D74.0:
  • D50-D89
    2023 ICD-10-CM Range D50-D89

    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

    Type 2 Excludes
    • autoimmune disease (systemic) NOS (M35.9)
    • certain conditions originating in the perinatal period (P00-P96)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • human immunodeficiency virus [HIV] disease (B20)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Clinical Information
  • Methemoglobinemia inherited in an autosomal recessive pattern. It is caused by deficiency of the enzyme nadh methemoglobin reductase or the presence of abnormal hemoglobin m. It presents with cyanosis early in life. There is no evidence of cardiopulmonary disease present.
ICD-10-CM D74.0 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):
  • 811 Red blood cell disorders with mcc
  • 812 Red blood cell disorders without mcc

Convert D74.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change
Code annotations containing back-references to D74.0:
  • Type 1 Excludes: D58.2
    ICD-10-CM Diagnosis Code D58.2

    Other hemoglobinopathies

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    • Abnormal hemoglobin NOS
    • Congenital Heinz body anemia
    • Hb-C disease
    • Hb-D disease
    • Hb-E disease
    • Hemoglobinopathy NOS
    • Unstable hemoglobin hemolytic disease
    Type 1 Excludes
    • familial polycythemia (D75.0)
    • Hb-M disease (D74.0)
    • hemoglobin E-beta thalassemia (D56.5)
    • hereditary persistence of fetal hemoglobin [HPFH] (D56.4)
    • high-altitude polycythemia (D75.1)
    • methemoglobinemia (D74.-)
    • other hemoglobinopathies with thalassemia (D56.8)

Diagnosis Index entries containing back-references to D74.0:
  • Deficiency, deficient
    • NADH diaphorase or reductase D74.0 (congenital)
    • NADH-methemoglobin reductase D74.0 (congenital)
  • Disease, diseased - see also Syndrome
  • Methemoglobinemia D74.9
    ICD-10-CM Diagnosis Code D74.9

    Methemoglobinemia, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • congenital D74.0
    • enzymatic D74.0 (congenital)
    • Hb M disease D74.0
    • hereditary D74.0

ICD-10-CM Codes Adjacent To D74.0
D73.1 Hypersplenism
D73.2 Chronic congestive splenomegaly
D73.3 Abscess of spleen
D73.4 Cyst of spleen
D73.5 Infarction of spleen
D73.8 Other diseases of spleen
D73.81 Neutropenic splenomegaly
D73.89 Other diseases of spleen
D73.9 Disease of spleen, unspecified
D74 Methemoglobinemia
D74.0 Congenital methemoglobinemia
D74.8 Other methemoglobinemias
D74.9 Methemoglobinemia, unspecified
D75 Other and unspecified diseases of blood and blood-forming organs
D75.0 Familial erythrocytosis
D75.1 Secondary polycythemia
D75.8 Other specified diseases of blood and blood-forming organs
D75.81 Myelofibrosis
D75.82 Heparin induced thrombocytopenia (HIT)
D75.821 Non-immune heparin-induced thrombocytopenia
D75.822 Immune-mediated heparin-induced thrombocytopenia

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.