2020 ICD-10-CM Diagnosis Code D75.0

Familial erythrocytosis

    2016 2017 2018 2019 2020 Billable/Specific Code
  • D75.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM D75.0 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of D75.0 - other international versions of ICD-10 D75.0 may differ.
Applicable To
  • Benign polycythemia
  • Familial polycythemia
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as D75.0. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • hereditary ovalocytosis (
    ICD-10-CM Diagnosis Code D58.1

    Hereditary elliptocytosis

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Elliptocytosis (congenital)
    • Ovalocytosis (congenital) (hereditary)
    D58.1
    )
The following code(s) above D75.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to D75.0:
  • D50-D89
    2020 ICD-10-CM Range D50-D89

    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

    Type 2 Excludes
    • autoimmune disease (systemic) NOS (M35.9)
    • certain conditions originating in the perinatal period (P00-P96)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • human immunodeficiency virus [HIV] disease (B20)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
  • D75
    ICD-10-CM Diagnosis Code D75

    Other and unspecified diseases of blood and blood-forming organs

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • acute lymphadenitis (L04.-)
    • chronic lymphadenitis (I88.1)
    • enlarged lymph nodes (R59.-)
    • hypergammaglobulinemia NOS (D89.2)
    • lymphadenitis NOS (I88.9)
    • mesenteric lymphadenitis (acute) (chronic) (I88.0)
    Other and unspecified diseases of blood and blood-forming organs
Approximate Synonyms
  • Familial polycythemia vera
  • Polycythemia vera, familial
ICD-10-CM D75.0 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 814 Reticuloendothelial and immunity disorders with mcc
  • 815 Reticuloendothelial and immunity disorders with cc
  • 816 Reticuloendothelial and immunity disorders without cc/mcc

Convert D75.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to D75.0:
  • Type 1 Excludes: D45
    , D58.2
    , R71
    ICD-10-CM Diagnosis Code D45

    Polycythemia vera

      2016 2017 2018 2019 2020 Billable/Specific Code
    Type 1 Excludes
    • familial polycythemia (D75.0)
    • secondary polycythemia (D75.1)
    ICD-10-CM Diagnosis Code D58.2

    Other hemoglobinopathies

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Abnormal hemoglobin NOS
    • Congenital Heinz body anemia
    • Hb-C disease
    • Hb-D disease
    • Hb-E disease
    • Hemoglobinopathy NOS
    • Unstable hemoglobin hemolytic disease
    Type 1 Excludes
    • familial polycythemia (D75.0)
    • Hb-M disease (D74.0)
    • hemoglobin E-beta thalassemia (D56.5)
    • hereditary persistence of fetal hemoglobin [HPFH] (D56.4)
    • high-altitude polycythemia (D75.1)
    • methemoglobinemia (D74.-)
    • other hemoglobinopathies with thalassemia (D56.8)
    ICD-10-CM Diagnosis Code R71

    Abnormality of red blood cells

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • anemias (D50-D64)
    • anemia of premature infant (P61.2)
    • benign (familial) polycythemia (D75.0)
    • congenital anemias (P61.2-P61.4)
    • newborn anemia due to isoimmunization (P55.-)
    • polycythemia neonatorum (P61.1)
    • polycythemia NOS (D75.1)
    • polycythemia vera (D45)
    • secondary polycythemia (D75.1)

Diagnosis Index entries containing back-references to D75.0:
  • Erythrocytosis (megalosplenic) (secondary) D75.1
    ICD-10-CM Diagnosis Code D75.1

    Secondary polycythemia

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Acquired polycythemia
    • Emotional polycythemia
    • Erythrocytosis NOS
    • Hypoxemic polycythemia
    • Nephrogenous polycythemia
    • Polycythemia due to erythropoietin
    • Polycythemia due to fall in plasma volume
    • Polycythemia due to high altitude
    • Polycythemia due to stress
    • Polycythemia NOS
    • Relative polycythemia
    Type 1 Excludes
    • polycythemia neonatorum (P61.1)
    • polycythemia vera (D45)
    • familial D75.0
  • Polycythemia (secondary) D75.1
    ICD-10-CM Diagnosis Code D75.1

    Secondary polycythemia

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Acquired polycythemia
    • Emotional polycythemia
    • Erythrocytosis NOS
    • Hypoxemic polycythemia
    • Nephrogenous polycythemia
    • Polycythemia due to erythropoietin
    • Polycythemia due to fall in plasma volume
    • Polycythemia due to high altitude
    • Polycythemia due to stress
    • Polycythemia NOS
    • Relative polycythemia
    Type 1 Excludes
    • polycythemia neonatorum (P61.1)
    • polycythemia vera (D45)
    • benign D75.0 (familial)
    • familial D75.0 (benign)

ICD-10-CM Codes Adjacent To D75.0
D73.5 Infarction of spleen
D73.8 Other diseases of spleen
D73.81 Neutropenic splenomegaly
D73.89 Other diseases of spleen
D73.9 Disease of spleen, unspecified
D74 Methemoglobinemia
D74.0 Congenital methemoglobinemia
D74.8 Other methemoglobinemias
D74.9 Methemoglobinemia, unspecified
D75 Other and unspecified diseases of blood and blood-forming organs
D75.0 Familial erythrocytosis
D75.1 Secondary polycythemia
D75.8 Other specified diseases of blood and blood-forming organs
D75.81 Myelofibrosis
D75.82 Heparin induced thrombocytopenia (HIT)
D75.89 Other specified diseases of blood and blood-forming organs
D75.9 Disease of blood and blood-forming organs, unspecified
D75.A Glucose-6-phosphate dehydrogenase (G6PD) deficiency without anemia
D76 Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue
D76.1 Hemophagocytic lymphohistiocytosis
D76.2 Hemophagocytic syndrome, infection-associated

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.