2018

  1. ICD-10-CM Codes
    2. ›
  2. D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
    3. ›
  3. D70-D77 Other disorders of blood and blood-forming organs
    4. ›

Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue D76- >

Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as D76. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • (Abt-) Letterer-Siwe disease (
    ICD-10-CM Diagnosis Code C96.0

    Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Histiocytosis X, multisystemic
    • Letterer-Siwe disease
    Type 1 Excludes
    • adult pulmonary Langerhans cell histiocytosis (J84.82)
    • multifocal and unisystemic Langerhans-cell histiocytosis (C96.5)
    • unifocal Langerhans-cell histiocytosis (C96.6)
    C96.0
    )
  • eosinophilic granuloma (
    ICD-10-CM Diagnosis Code C96.6

    Unifocal Langerhans-cell histiocytosis

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Eosinophilic granuloma
    • Histiocytosis X, unifocal
    • Histiocytosis X NOS
    • Langerhans-cell histiocytosis NOS
    Type 1 Excludes
    • multifocal and multisysemic (disseminated) Langerhans-cell histiocytosis (C96.0)
    • multifocal and unisystemic Langerhans-cell histiocytosis (C96.5)
    C96.6
    )
  • Hand-Schüller-Christian disease (
    ICD-10-CM Diagnosis Code C96.5

    Multifocal and unisystemic Langerhans-cell histiocytosis

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Hand-Schüller-Christian disease
    • Histiocytosis X, multifocal
    Type 1 Excludes
    • multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis (C96.0)
    • unifocal Langerhans-cell histiocytosis (C96.6)
    C96.5
    )
  • histiocytic medullary reticulosis (
    ICD-10-CM Diagnosis Code C96.9

    Malignant neoplasm of lymphoid, hematopoietic and related tissue, unspecified

      2016 2017 2018 Billable/Specific Code
    C96.9
    )
  • histiocytic sarcoma (
    ICD-10-CM Diagnosis Code C96.A

    Histiocytic sarcoma

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Malignant histiocytosis
    C96.A
    )
  • histiocytosis X, multifocal (
    ICD-10-CM Diagnosis Code C96.5

    Multifocal and unisystemic Langerhans-cell histiocytosis

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Hand-Schüller-Christian disease
    • Histiocytosis X, multifocal
    Type 1 Excludes
    • multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis (C96.0)
    • unifocal Langerhans-cell histiocytosis (C96.6)
    C96.5
    )
  • histiocytosis X, unifocal (
    ICD-10-CM Diagnosis Code C96.6

    Unifocal Langerhans-cell histiocytosis

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Eosinophilic granuloma
    • Histiocytosis X, unifocal
    • Histiocytosis X NOS
    • Langerhans-cell histiocytosis NOS
    Type 1 Excludes
    • multifocal and multisysemic (disseminated) Langerhans-cell histiocytosis (C96.0)
    • multifocal and unisystemic Langerhans-cell histiocytosis (C96.5)
    C96.6
    )
  • Langerhans-cell histiocytosis, multifocal (
    ICD-10-CM Diagnosis Code C96.5

    Multifocal and unisystemic Langerhans-cell histiocytosis

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Hand-Schüller-Christian disease
    • Histiocytosis X, multifocal
    Type 1 Excludes
    • multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis (C96.0)
    • unifocal Langerhans-cell histiocytosis (C96.6)
    C96.5
    )
  • Langerhans-cell histiocytosis NOS (
    ICD-10-CM Diagnosis Code C96.6

    Unifocal Langerhans-cell histiocytosis

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Eosinophilic granuloma
    • Histiocytosis X, unifocal
    • Histiocytosis X NOS
    • Langerhans-cell histiocytosis NOS
    Type 1 Excludes
    • multifocal and multisysemic (disseminated) Langerhans-cell histiocytosis (C96.0)
    • multifocal and unisystemic Langerhans-cell histiocytosis (C96.5)
    C96.6
    )
  • Langerhans-cell histiocytosis, unifocal (
    ICD-10-CM Diagnosis Code C96.6

    Unifocal Langerhans-cell histiocytosis

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Eosinophilic granuloma
    • Histiocytosis X, unifocal
    • Histiocytosis X NOS
    • Langerhans-cell histiocytosis NOS
    Type 1 Excludes
    • multifocal and multisysemic (disseminated) Langerhans-cell histiocytosis (C96.0)
    • multifocal and unisystemic Langerhans-cell histiocytosis (C96.5)
    C96.6
    )
  • leukemic reticuloendotheliosis (
    ICD-10-CM Diagnosis Code C91.4

    Hairy cell leukemia

      2016 2017 2018 Non-Billable/Non-Specific Code
    Applicable To
    • Leukemic reticuloendotheliosis
    C91.4-
    )
  • lipomelanotic reticulosis (
    ICD-10-CM Diagnosis Code I89.8

    Other specified noninfective disorders of lymphatic vessels and lymph nodes

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Chylocele (nonfilarial)
    • Chylous ascites
    • Chylous cyst
    • Lipomelanotic reticulosis
    • Lymph node or vessel fistula
    • Lymph node or vessel infarction
    • Lymph node or vessel rupture
    I89.8
    )
  • malignant histiocytosis (
    ICD-10-CM Diagnosis Code C96.A

    Histiocytic sarcoma

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Malignant histiocytosis
    C96.A
    )
  • malignant reticulosis (
    ICD-10-CM Diagnosis Code C86.0

    Extranodal NK/T-cell lymphoma, nasal type

      2016 2017 2018 Billable/Specific Code
    C86.0
    )
  • nonlipid reticuloendotheliosis (
    ICD-10-CM Diagnosis Code C96.0

    Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis

      2016 2017 2018 Billable/Specific Code
    Applicable To
    • Histiocytosis X, multisystemic
    • Letterer-Siwe disease
    Type 1 Excludes
    • adult pulmonary Langerhans cell histiocytosis (J84.82)
    • multifocal and unisystemic Langerhans-cell histiocytosis (C96.5)
    • unifocal Langerhans-cell histiocytosis (C96.6)
    C96.0
    )

Codes