ICD-10-CM Codes
D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
D70-D77 Other disorders of blood and blood-forming organs
D76- Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue

2019 ICD-10-CM Diagnosis Code D76

Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue

2016

2017

2018

2019

Non-Billable/Non-Specific Code

D76 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
Short description: Oth dis with lymphoreticular and reticulohistiocytic tissue
The 2019 edition of ICD-10-CM D76 became effective on October 1, 2018.
This is the American ICD-10-CM version of D76 - other international versions of ICD-10 D76 may differ.

Type 1 Excludes

Type 1 Excludes Help

A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as D76. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

(Abt-) Letterer-Siwe disease (
ICD-10-CM Diagnosis Code C96.0
Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis
Applicable To
- Histiocytosis X, multisystemic
- Letterer-Siwe disease
Type 1 Excludes
- adult pulmonary Langerhans cell histiocytosis (J84.82)
- multifocal and unisystemic Langerhans-cell histiocytosis (C96.5)
- unifocal Langerhans-cell histiocytosis (C96.6)
C96.0
)
eosinophilic granuloma (
ICD-10-CM Diagnosis Code C96.6
Unifocal Langerhans-cell histiocytosis
Applicable To
- Eosinophilic granuloma
- Histiocytosis X, unifocal
- Histiocytosis X NOS
- Langerhans-cell histiocytosis NOS
Type 1 Excludes
- multifocal and multisysemic (disseminated) Langerhans-cell histiocytosis (C96.0)
- multifocal and unisystemic Langerhans-cell histiocytosis (C96.5)
C96.6
)
Hand-Schüller-Christian disease (
ICD-10-CM Diagnosis Code C96.5
Multifocal and unisystemic Langerhans-cell histiocytosis
Applicable To
- Hand-Schüller-Christian disease
- Histiocytosis X, multifocal
Type 1 Excludes
- multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis (C96.0)
- unifocal Langerhans-cell histiocytosis (C96.6)
C96.5
)
histiocytic medullary reticulosis (
ICD-10-CM Diagnosis Code C96.9
Malignant neoplasm of lymphoid, hematopoietic and related tissue, unspecified
C96.9
)
histiocytic sarcoma (
ICD-10-CM Diagnosis Code C96.A
Histiocytic sarcoma
Applicable To
- Malignant histiocytosis
C96.A
)
histiocytosis X, multifocal (
ICD-10-CM Diagnosis Code C96.5
Multifocal and unisystemic Langerhans-cell histiocytosis
Applicable To
- Hand-Schüller-Christian disease
- Histiocytosis X, multifocal
Type 1 Excludes
- multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis (C96.0)
- unifocal Langerhans-cell histiocytosis (C96.6)
C96.5
)
histiocytosis X, unifocal (
ICD-10-CM Diagnosis Code C96.6
Unifocal Langerhans-cell histiocytosis
Applicable To
- Eosinophilic granuloma
- Histiocytosis X, unifocal
- Histiocytosis X NOS
- Langerhans-cell histiocytosis NOS
Type 1 Excludes
- multifocal and multisysemic (disseminated) Langerhans-cell histiocytosis (C96.0)
- multifocal and unisystemic Langerhans-cell histiocytosis (C96.5)
C96.6
)
Langerhans-cell histiocytosis, multifocal (
ICD-10-CM Diagnosis Code C96.5
Multifocal and unisystemic Langerhans-cell histiocytosis
Applicable To
- Hand-Schüller-Christian disease
- Histiocytosis X, multifocal
Type 1 Excludes
- multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis (C96.0)
- unifocal Langerhans-cell histiocytosis (C96.6)
C96.5
)
Langerhans-cell histiocytosis NOS (
ICD-10-CM Diagnosis Code C96.6
Unifocal Langerhans-cell histiocytosis
Applicable To
- Eosinophilic granuloma
- Histiocytosis X, unifocal
- Histiocytosis X NOS
- Langerhans-cell histiocytosis NOS
Type 1 Excludes
- multifocal and multisysemic (disseminated) Langerhans-cell histiocytosis (C96.0)
- multifocal and unisystemic Langerhans-cell histiocytosis (C96.5)
C96.6
)
Langerhans-cell histiocytosis, unifocal (
ICD-10-CM Diagnosis Code C96.6
Unifocal Langerhans-cell histiocytosis
Applicable To
- Eosinophilic granuloma
- Histiocytosis X, unifocal
- Histiocytosis X NOS
- Langerhans-cell histiocytosis NOS
Type 1 Excludes
- multifocal and multisysemic (disseminated) Langerhans-cell histiocytosis (C96.0)
- multifocal and unisystemic Langerhans-cell histiocytosis (C96.5)
C96.6
)
leukemic reticuloendotheliosis (
ICD-10-CM Diagnosis Code C91.4
Hairy cell leukemia
Applicable To
- Leukemic reticuloendotheliosis
C91.4-
)
lipomelanotic reticulosis (
ICD-10-CM Diagnosis Code I89.8
Other specified noninfective disorders of lymphatic vessels and lymph nodes
Applicable To
- Chylocele (nonfilarial)
- Chylous ascites
- Chylous cyst
- Lipomelanotic reticulosis
- Lymph node or vessel fistula
- Lymph node or vessel infarction
- Lymph node or vessel rupture
I89.8
)
malignant histiocytosis (
ICD-10-CM Diagnosis Code C96.A
Histiocytic sarcoma
Applicable To
- Malignant histiocytosis
C96.A
)
malignant reticulosis (
ICD-10-CM Diagnosis Code C86.0
Extranodal NK/T-cell lymphoma, nasal type
C86.0
)
nonlipid reticuloendotheliosis (
ICD-10-CM Diagnosis Code C96.0
Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis
Applicable To
- Histiocytosis X, multisystemic
- Letterer-Siwe disease
Type 1 Excludes
- adult pulmonary Langerhans cell histiocytosis (J84.82)
- multifocal and unisystemic Langerhans-cell histiocytosis (C96.5)
- unifocal Langerhans-cell histiocytosis (C96.6)
C96.0
)

The following code(s) above D76 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to D76:

D50-D89
2019 ICD-10-CM Range D50-D89
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Type 2 Excludes
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change

ICD-10-CM Codes Adjacent To D76

D74.8 Other methemoglobinemias

D74.9 Methemoglobinemia, unspecified

D75 Other and unspecified diseases of blood and blood-forming organs

D75.0 Familial erythrocytosis

D75.1 Secondary polycythemia

D75.8 Other specified diseases of blood and blood-forming organs

D75.81 Myelofibrosis

D75.82 Heparin induced thrombocytopenia (HIT)

D75.89 Other specified diseases of blood and blood-forming organs

D75.9 Disease of blood and blood-forming organs, unspecified

D76 Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue

D76.1 Hemophagocytic lymphohistiocytosis

D76.2 Hemophagocytic syndrome, infection-associated

D76.3 Other histiocytosis syndromes

D77 Other disorders of blood and blood-forming organs in diseases classified elsewhere

D78 Intraoperative and postprocedural complications of the spleen

D78.0 Intraoperative hemorrhage and hematoma of the spleen complicating a procedure

D78.01 …… on the spleen

D78.02 Intraoperative hemorrhage and hematoma of the spleen complicating other procedure

D78.1 Accidental puncture and laceration of the spleen during a procedure

D78.11 …… on the spleen

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2019 ICD-10-CM Diagnosis Code D76

Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue

Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis

Unifocal Langerhans-cell histiocytosis

Multifocal and unisystemic Langerhans-cell histiocytosis

Malignant neoplasm of lymphoid, hematopoietic and related tissue, unspecified

Histiocytic sarcoma

Multifocal and unisystemic Langerhans-cell histiocytosis

Unifocal Langerhans-cell histiocytosis

Multifocal and unisystemic Langerhans-cell histiocytosis

Unifocal Langerhans-cell histiocytosis

Unifocal Langerhans-cell histiocytosis

Hairy cell leukemia

Other specified noninfective disorders of lymphatic vessels and lymph nodes

Histiocytic sarcoma

Extranodal NK/T-cell lymphoma, nasal type

Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis

Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism