ICD-10-CM Codes
D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
D80-D89 Certain disorders involving the immune mechanism

Combined immunodeficiencies D81- >

Type 1 Excludes

Type 1 Excludes Help

A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as D81. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

autosomal recessive agammaglobulinemia (Swiss type) (
ICD-10-CM Diagnosis Code D80.0
Hereditary hypogammaglobulinemia
Applicable To
- Autosomal recessive agammaglobulinemia (Swiss type)
- X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency)
D80.0
)

Codes

D81 Combined immunodeficiencies
- D81.0 Severe combined immunodeficiency [SCID] with reticular dysgenesis
- D81.1 Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
- D81.2 Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
- D81.3 Adenosine deaminase [ADA] deficiency
  - D81.30 Adenosine deaminase deficiency, unspecified
  - D81.31 Severe combined immunodeficiency due to adenosine deaminase deficiency
  - D81.32 Adenosine deaminase 2 deficiency
  - D81.39 Other adenosine deaminase deficiency
- D81.4 Nezelof's syndrome
- D81.5 Purine nucleoside phosphorylase [PNP] deficiency
- D81.6 Major histocompatibility complex class I deficiency
- D81.7 Major histocompatibility complex class II deficiency
- D81.8 Other combined immunodeficiencies
  - D81.81 Biotin-dependent carboxylase deficiency
    - D81.810 Biotinidase deficiency
    - D81.818 Other biotin-dependent carboxylase deficiency
    - D81.819 …… unspecified
  - D81.89 Other combined immunodeficiencies
- D81.9 Combined immunodeficiency, unspecified

Combined immunodeficiencies D81- >

Hereditary hypogammaglobulinemia