Combined immunodeficiencies D81-

Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as D81. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • autosomal recessive agammaglobulinemia (Swiss type) (
    ICD-10-CM Diagnosis Code D80.0

    Hereditary hypogammaglobulinemia

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
    Applicable To
    • Autosomal recessive agammaglobulinemia (Swiss type)
    • X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency)
  • D81 Combined immunodeficiencies
    • D81.0 Severe combined immunodeficiency [SCID] with reticular dysgenesis
    • D81.1 Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
    • D81.2 Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
    • D81.3 Adenosine deaminase [ADA] deficiency
      • D81.30 Adenosine deaminase deficiency, unspecified
      • D81.31 Severe combined immunodeficiency due to adenosine deaminase deficiency
      • D81.32 Adenosine deaminase 2 deficiency
      • D81.39 Other adenosine deaminase deficiency
    • D81.4 Nezelof's syndrome
    • D81.5 Purine nucleoside phosphorylase [PNP] deficiency
    • D81.6 Major histocompatibility complex class I deficiency
    • D81.7 Major histocompatibility complex class II deficiency
    • D81.8 Other combined immunodeficiencies
      • D81.81 Biotin-dependent carboxylase deficiency
        • D81.810 Biotinidase deficiency
        • D81.818 Other biotin-dependent carboxylase deficiency
        • D81.819 …… unspecified
      • D81.89 Other combined immunodeficiencies
    • D81.9 Combined immunodeficiency, unspecified