2019 ICD-10-CM Diagnosis Code D82.0

Wiskott-Aldrich syndrome

    2016 2017 2018 2019 Billable/Specific Code
  • D82.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2019 edition of ICD-10-CM D82.0 became effective on October 1, 2018.
  • This is the American ICD-10-CM version of D82.0 - other international versions of ICD-10 D82.0 may differ.
Applicable To
  • Immunodeficiency with thrombocytopenia and eczema
The following code(s) above D82.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to D82.0:
  • D50-D89
    2019 ICD-10-CM Range D50-D89

    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

    Type 2 Excludes
    • autoimmune disease (systemic) NOS (M35.9)
    • certain conditions originating in the perinatal period (P00-P96)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • human immunodeficiency virus [HIV] disease (B20)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
  • D80-D89
    2019 ICD-10-CM Range D80-D89

    Certain disorders involving the immune mechanism

    Includes
    • defects in the complement system
    • immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
    • sarcoidosis
    Type 1 Excludes
    • autoimmune disease (systemic) NOS (M35.9)
    • functional disorders of polymorphonuclear neutrophils (D71)
    • human immunodeficiency virus [HIV] disease (B20)
    Certain disorders involving the immune mechanism
  • D82
    ICD-10-CM Diagnosis Code D82

    Immunodeficiency associated with other major defects

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • ataxia telangiectasia [Louis-Bar] (G11.3)
    Immunodeficiency associated with other major defects
Approximate Synonyms
  • Wiskott aldrich syndrome
Clinical Information
  • A rare, x-linked immunodeficiency syndrome characterized by eczema, thrombocytopenia, and recurrent pyogenic infection. It is seen exclusively in young boys. Typically, igm levels are low and iga and ige levels are elevated. Lymphoreticular malignancies are common.
  • A rare, x-linked immunodeficiency syndrome characterized by eczema; lymphopenia; and, recurrent pyogenic infection. It is seen exclusively in young boys. Typically, immunoglobulin m levels are low and immunoglobulin a and immunoglobulin e levels are elevated. Lymphoreticular malignancies are common.
  • An inherited immune disorder that occurs in young boys. It causes eczema (a type of skin inflammation), a decrease in the number of platelets (blood cells that help prevent bleeding), and frequent bacterial infections. People with wiskott-aldrich syndrome are at increased risk of developing leukemia and lymphoma.
  • Rare x-linked immunodeficiency syndrome of young boys characterized by eczema, thrombocytopenic purpura and recurrent pyogenic infection; igm levels are low and iga and ige levels are elevated; lymphoreticular malignancies are common.
ICD-10-CM D82.0 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):
  • 808 Major hematological and immunological diagnoses except sickle cell crisis and coagulation disorders with mcc
  • 809 Major hematological and immunological diagnoses except sickle cell crisis and coagulation disorders with cc
  • 810 Major hematological and immunological diagnoses except sickle cell crisis and coagulation disorders without cc/mcc

Convert D82.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
Code annotations containing back-references to D82.0:
  • Type 1 Excludes: D69.4
    ICD-10-CM Diagnosis Code D69.4

    Other primary thrombocytopenia

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • transient neonatal thrombocytopenia (P61.0)
    • Wiskott-Aldrich syndrome (D82.0)

Diagnosis Index entries containing back-references to D82.0:
  • Aldrich D82.0 (-Wiskott) syndrome (eczema-thrombocytopenia)
  • Deficiency, deficient
    • immunity D84.9
      ICD-10-CM Diagnosis Code D84.9

      Immunodeficiency, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      • cell-mediated D84.8
        ICD-10-CM Diagnosis Code D84.8

        Other specified immunodeficiencies

          2016 2017 2018 2019 Billable/Specific Code
        • with thrombocytopenia and eczema D82.0
  • Immunodeficiency D84.9
    ICD-10-CM Diagnosis Code D84.9

    Immunodeficiency, unspecified

      2016 2017 2018 2019 Billable/Specific Code
    • with
      • thrombocytopenia and eczema D82.0
  • Syndrome - see also Disease
    • Aldrich D82.0 (-Wiskott)
    • eczema-thrombocytopenia D82.0
    • familial eczema-thrombocytopenia D82.0 (Wiskott-Aldrich)
    • Wiskott-Aldrich D82.0
  • Wiskott-Aldrich syndrome D82.0

ICD-10-CM Codes Adjacent To D82.0
D81.6 Major histocompatibility complex class I deficiency
D81.7 Major histocompatibility complex class II deficiency
D81.8 Other combined immunodeficiencies
D81.81 Biotin-dependent carboxylase deficiency
D81.810 Biotinidase deficiency
D81.818 Other biotin-dependent carboxylase deficiency
D81.819 …… unspecified
D81.89 Other combined immunodeficiencies
D81.9 Combined immunodeficiency, unspecified
D82 Immunodeficiency associated with other major defects
D82.0 Wiskott-Aldrich syndrome
D82.1 Di George's syndrome
D82.2 Immunodeficiency with short-limbed stature
D82.3 Immunodeficiency following hereditary defective response to Epstein-Barr virus
D82.4 Hyperimmunoglobulin E [IgE] syndrome
D82.8 Immunodeficiency associated with other specified major defects
D82.9 Immunodeficiency associated with major defect, unspecified
D83 Common variable immunodeficiency
D83.0 Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function
D83.1 Common variable immunodeficiency with predominant immunoregulatory T-cell disorders
D83.2 Common variable immunodeficiency with autoantibodies to B- or T-cells

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.