ICD-10-CM Codes
E00-E89 Endocrine, nutritional and metabolic diseases
E00-E07 Disorders of thyroid gland
E00- Congenital iodine-deficiency syndrome

2018 ICD-10-CM Diagnosis Code E00

Congenital iodine-deficiency syndrome

2016

2017

2018

Non-Billable/Non-Specific Code

E00 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
The 2018 edition of ICD-10-CM E00 became effective on October 1, 2017.
This is the American ICD-10-CM version of E00 - other international versions of ICD-10 E00 may differ.

Use Additional

Use Additional Help

Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.

code (F70-F79
ICD-10-CM Range F70-F79
Intellectual disabilities
Code First
- any associated physical or developmental disorders
Type 1 Excludes
- borderline intellectual functioning, IQ above 70 to 84 (R41.83)
- F70 Mild intellectual disabilities
- F71 Moderate intellectual disabilities
- F72 Severe intellectual disabilities
- F73 Profound intellectual disabilities
- F78 Other intellectual disabilities
- F79 Unspecified intellectual disabilities
) to identify associated intellectual disabilities.

Type 1 Excludes

Type 1 Excludes Help

A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as E00. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

subclinical iodine-deficiency hypothyroidism (
ICD-10-CM Diagnosis Code E02
Subclinical iodine-deficiency hypothyroidism
E02
)

The following code(s) above E00 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to E00:

E00-E89
2018 ICD-10-CM Range E00-E89
Endocrine, nutritional and metabolic diseases
Note
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Type 1 Excludes
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Endocrine, nutritional and metabolic diseases

Clinical Information

Severely reduced physical and mental growth associated with pyramidal and extrapyramidal signs and symptoms, due to dietary iodine deficiency.

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change

Code annotations containing back-references to E00:

Type 1 Excludes: E01

ICD-10-CM Diagnosis Code E01
Iodine-deficiency related thyroid disorders and allied conditions
Type 1 Excludes
- congenital iodine-deficiency syndrome (E00.-)
- subclinical iodine-deficiency hypothyroidism (E02)

ICD-10-CM Codes Adjacent To E00

D89.49 Other mast cell activation disorder

D89.8 Other specified disorders involving the immune mechanism, not elsewhere classified

D89.81 Graft-versus-host disease

D89.810 Acute graft-versus-host disease

D89.811 Chronic graft-versus-host disease

D89.812 Acute on chronic graft-versus-host disease

D89.813 …… unspecified

D89.82 Autoimmune lymphoproliferative syndrome [ALPS]

D89.89 Other specified disorders involving the immune mechanism, not elsewhere classified

D89.9 Disorder involving the immune mechanism, unspecified

E00 Congenital iodine-deficiency syndrome

E00.0 Congenital iodine-deficiency syndrome, neurological type

E00.1 Congenital iodine-deficiency syndrome, myxedematous type

E00.2 Congenital iodine-deficiency syndrome, mixed type

E00.9 Congenital iodine-deficiency syndrome, unspecified

E01 Iodine-deficiency related thyroid disorders and allied conditions

E01.0 Iodine-deficiency related diffuse (endemic) goiter

E01.1 Iodine-deficiency related multinodular (endemic) goiter

E01.2 Iodine-deficiency related (endemic) goiter, unspecified

E01.8 Other iodine-deficiency related thyroid disorders and allied conditions

E02 Subclinical iodine-deficiency hypothyroidism

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2018 ICD-10-CM Diagnosis Code E00

Congenital iodine-deficiency syndrome

Intellectual disabilities

Subclinical iodine-deficiency hypothyroidism

Endocrine, nutritional and metabolic diseases

Iodine-deficiency related thyroid disorders and allied conditions