1. ICD-10-CM Codes
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2. E00-E89
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3. E00-E07
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4. E03-
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5. 2023 ICD-10-CM Diagnosis Code E03.1

2023 ICD-10-CM Diagnosis Code E03.1

Congenital hypothyroidism without goiter

2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

• E03.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
• The 2023 edition of ICD-10-CM E03.1 became effective on October 1, 2022.
• This is the American ICD-10-CM version of E03.1 - other international versions of ICD-10 E03.1 may differ.

• Congenital hypothyroidism
• Hypothyroidism, congenital

• A condition in infancy or early childhood due to an in-utero deficiency of thyroid hormones that can be caused by genetic or environmental factors, such as thyroid dysgenesis or hypothyroidism in infants of mothers treated with thiouracil during pregnancy. Endemic cretinism is the result of iodine deficiency. Clinical symptoms include severe mental retardation, impaired skeletal development, short stature, and myxedema.
• A deficiency of thyroid hormone present at birth. The etiology can be genetic or environmental, or a combination of both; treatment is based on severity and causality.
• Condition due to congenital lack of thyroid hormone, marked by arrested physical and mental development, dystrophy of the bones and soft parts, and lowered basal metabolism; it is the congenital form of thyroid deficiency, while myxedema is the acquired form.

• 643 Endocrine disorders with mcc
• 644 Endocrine disorders with cc
• 645 Endocrine disorders without cc/mcc

Convert E03.1 to ICD-9-CM

• 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
• 2017 (effective 10/1/2016): No change
• 2018 (effective 10/1/2017): No change
• 2019 (effective 10/1/2018): No change
• 2020 (effective 10/1/2019): No change
• 2021 (effective 10/1/2020): No change
• 2022 (effective 10/1/2021): No change
• 2023 (effective 10/1/2022): No change

• Type 1 Excludes: P72
  , E03.4
  , Q89.2
  ICD-10-CM Diagnosis Code P72

  Other transitory neonatal endocrine disorders

  2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code

  Type 1 Excludes

  • congenital hypothyroidism with or without goiter (E03.0-E03.1)
  • dyshormogenetic goiter (E07.1)
  • Pendred's syndrome (E07.1)
  ICD-10-CM Diagnosis Code E03.4

  Atrophy of thyroid (acquired)

  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

  Type 1 Excludes

  • congenital atrophy of thyroid (E03.1)
  ICD-10-CM Diagnosis Code Q89.2

  Congenital malformations of other endocrine glands

  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

  Applicable To

  • Congenital malformation of parathyroid or thyroid gland
  • Persistent thyroglossal duct
  • Thyroglossal cyst

  Type 1 Excludes

  • congenital goiter (E03.0)
  • congenital hypothyroidism (E03.1)

• Absence (of) (organ or part) (complete or partial)
  • thyroid (gland) (acquired) E89.0
    ICD-10-CM Diagnosis Code E89.0

    Postprocedural hypothyroidism

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Postirradiation hypothyroidism
    • Postsurgical hypothyroidism
    • congenital E03.1
• Agenesis
  • thyroid (gland) E03.1
• Aplasia - see also Agenesis
  • thyroid E03.1 (congenital) (with myxedema)
• Athyrea (acquired) - see also Hypothyroidism
  • congenital E03.1
• Atrophy, atrophic (of)
  • thyroid (gland) (acquired) E03.4
    ICD-10-CM Diagnosis Code E03.4

    Atrophy of thyroid (acquired)

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Type 1 Excludes

    • congenital atrophy of thyroid (E03.1)
    • with cretinism E03.1
    • congenital E03.1 (with myxedema)
• Hypoplasia, hypoplastic
  • thyroid (gland) E03.1
• Hypothyroidism (acquired) E03.9
  ICD-10-CM Diagnosis Code E03.9

  Hypothyroidism, unspecified

  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

  Applicable To

  • Myxedema NOS
  • congenital (without goiter) E03.1
• Insufficiency, insufficient
  • thyroid (gland) (acquired) E03.9
    ICD-10-CM Diagnosis Code E03.9

    Hypothyroidism, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Myxedema NOS
    • congenital E03.1
• Jaundice (yellow) R17
  ICD-10-CM Diagnosis Code R17

  Unspecified jaundice

  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

  Type 1 Excludes

  • neonatal jaundice (P55, P57-P59)
  • newborn P59.9
    ICD-10-CM Diagnosis Code P59.9

    Neonatal jaundice, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Code on Newborn Record

    Applicable To

    • Neonatal physiological jaundice (intense)(prolonged) NOS
    • due to or associated with
      • hypothyroidism, congenital E03.1
• Subthyroidism (acquired) - see also Hypothyroidism
  • congenital E03.1

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.