2021 ICD-10-CM Diagnosis Code E20.1

Pseudohypoparathyroidism

    2016 2017 2018 2019 2020 2021 Billable/Specific Code
  • E20.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2021 edition of ICD-10-CM E20.1 became effective on October 1, 2020.
  • This is the American ICD-10-CM version of E20.1 - other international versions of ICD-10 E20.1 may differ.
The following code(s) above E20.1 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to E20.1:
  • E00-E89
    2021 ICD-10-CM Range E00-E89

    Endocrine, nutritional and metabolic diseases

    Note
    • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
    Type 1 Excludes
    • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
    Endocrine, nutritional and metabolic diseases
  • E20-E35
    2021 ICD-10-CM Range E20-E35

    Disorders of other endocrine glands

    Type 1 Excludes
    Disorders of other endocrine glands
  • E20
    ICD-10-CM Diagnosis Code E20

    Hypoparathyroidism

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • Di George's syndrome (D82.1)
    • postprocedural hypoparathyroidism (E89.2)
    • tetany NOS (R29.0)
    • transitory neonatal hypoparathyroidism (P71.4)
    Hypoparathyroidism
Approximate Synonyms
  • Pseudopseudohypoparathyroidism
Clinical Information
  • A condition characterized by the insensitivity of the tissues to respond to the activity of the parathyroid hormone. It results in increased levels of parathyroid hormone in the serum, hypocalcemia, and hyperphosphatemia.
  • A hereditary syndrome clinically similar to hypoparathyroidism. It is characterized by hypocalcemia; hyperphosphatemia; and associated skeletal development impairment and caused by failure of response to parathyroid hormone rather than deficiencies. A severe form with resistance to multiple hormones is referred to as type 1a and is associated with maternal mutant allele of the alpha chain of stimulatory g protein.
  • Hereditary condition clinically resembling hypoparathyroidism, but caused by failure of response to rather than deficiency of parathyroid hormones; characterized by hypocalcemia and hyperphosphatemia, and commonly associated with short stature, obesity, short metacarpals, and ectopic calcification.
  • Originally reported as a hypocalcemic syndrome similar to hypoparathyroidism, but with renal and skeletal resistance to parathyroid hormone (pth) and designated as "pseudohypoparathyroidism." albright later defined a normocalcemic variant which he termed "pseudopseudohypoparathyroidism." two separate forms of pseudohypoparathyroidism are recognized. Type i in which there is no increase in the urinary excretion of cyclic adenosine monophosphate (camp) and phosphate in response to parathyroid hormone (pth). Type ii in which there is a response to pth, but without phosphate diuresis. The erythrocytes of some patients with type i contain a defective receptor-cyclase coupling protein (stimulatory guanine nucleoside-binding protein, or gs) which is responsible for coupling the cellular receptor that binds parathyroid hormone (pth) and is involved with the formation and release of cyclic adenosine monophosphate (camp). This variant has been designated as "pseudohypoparathyroidism type ia." the syndrome is associated with mental deficiency, dystrophic bone lesions, short stature, and other defects.
ICD-10-CM E20.1 is grouped within Diagnostic Related Group(s) (MS-DRG v38.0):
  • 640 Miscellaneous disorders of nutrition, metabolism, fluids and electrolytes with mcc
  • 641 Miscellaneous disorders of nutrition, metabolism, fluids and electrolytes without mcc

Convert E20.1 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
Code annotations containing back-references to E20.1:
  • Type 1 Excludes: E31
    , E34
    ICD-10-CM Diagnosis Code E31

    Polyglandular dysfunction

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • ataxia telangiectasia [Louis-Bar] (G11.3)
    • dystrophia myotonica [Steinert] (G71.11)
    • pseudohypoparathyroidism (E20.1)
    ICD-10-CM Diagnosis Code E34

    Other endocrine disorders

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • pseudohypoparathyroidism (E20.1)
  • Type 2 Excludes: E34.8
    ICD-10-CM Diagnosis Code E34.8

    Other specified endocrine disorders

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Pineal gland dysfunction
    • Progeria
    Type 2 Excludes
    • pseudohypoparathyroidism (E20.1)

Diagnosis Index entries containing back-references to E20.1:
  • Pseudohypoparathyroidism E20.1
  • Pseudopseudohypoparathyroidism E20.1

ICD-10-CM Codes Adjacent To E20.1
E16 Other disorders of pancreatic internal secretion
E16.0 Drug-induced hypoglycemia without coma
E16.1 Other hypoglycemia
E16.2 Hypoglycemia, unspecified
E16.3 Increased secretion of glucagon
E16.4 Increased secretion of gastrin
E16.8 Other specified disorders of pancreatic internal secretion
E16.9 Disorder of pancreatic internal secretion, unspecified
E20 Hypoparathyroidism
E20.0 Idiopathic hypoparathyroidism
E20.1 Pseudohypoparathyroidism
E20.8 Other hypoparathyroidism
E20.9 Hypoparathyroidism, unspecified
E21 Hyperparathyroidism and other disorders of parathyroid gland
E21.0 Primary hyperparathyroidism
E21.1 Secondary hyperparathyroidism, not elsewhere classified
E21.2 Other hyperparathyroidism
E21.3 Hyperparathyroidism, unspecified
E21.4 Other specified disorders of parathyroid gland
E21.5 Disorder of parathyroid gland, unspecified
E22 Hyperfunction of pituitary gland

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.