2022 ICD-10-CM Diagnosis Code E34.0

Carcinoid syndrome

    2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
  • E34.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2022 edition of ICD-10-CM E34.0 became effective on October 1, 2021.
  • This is the American ICD-10-CM version of E34.0 - other international versions of ICD-10 E34.0 may differ.
  • May be used as an additional code to identify functional activity associated with a carcinoid tumor.
The following code(s) above E34.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to E34.0:
  • E00-E89
    2022 ICD-10-CM Range E00-E89

    Endocrine, nutritional and metabolic diseases

    • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
    Type 1 Excludes
    • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
    Endocrine, nutritional and metabolic diseases
  • E20-E35
    2022 ICD-10-CM Range E20-E35

    Disorders of other endocrine glands

    Type 1 Excludes
    Disorders of other endocrine glands
  • E34
    ICD-10-CM Diagnosis Code E34

    Other endocrine disorders

      2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • pseudohypoparathyroidism (E20.1)
    Other endocrine disorders
Clinical Information
  • A combination of symptoms caused by the release of serotonin and other substances from carcinoid tumors of the gastrointestinal tract. Symptoms may include flushing of the face, flat angiomas (small collections of dilated blood vessels) of the skin, diarrhea, bronchial spasms, rapid pulse, and sudden drops in blood pressure.
  • A symptom complex associated with carcinoid tumor and characterized by attacks of severe flushing of the skin, diarrheal watery stools, bronchoconstriction, sudden drops in blood pressure, edema, and ascites. The carcinoid tumors are usually located in the gastrointestinal tract and metastasize to the liver. Symptoms are caused by tumor secretion of serotonin, prostaglandins, and other biologically active substances. Cardiac manifestations constitute carcinoid heart disease. (Dorland, 27th ed; stedman, 25th ed)
ICD-10-CM E34.0 is grouped within Diagnostic Related Group(s) (MS-DRG v39.0):
  • 643 Endocrine disorders with mcc
  • 644 Endocrine disorders with cc
  • 645 Endocrine disorders without cc/mcc

Convert E34.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
Code annotations containing back-references to E34.0:
  • Use Additional: D3A
    , C7A
    ICD-10-CM Diagnosis Code D3A

    Benign neuroendocrine tumors

      2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
    Code Also
    • any associated multiple endocrine neoplasia [MEN] syndromes (E31.2-)
    Type 2 Excludes
    • benign pancreatic islet cell tumors (D13.7)
    Use Additional
    • code to identify any associated endocrine syndrome, such as:
    • carcinoid syndrome (E34.0)
    ICD-10-CM Diagnosis Code C7A

    Malignant neuroendocrine tumors

      2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
    Code Also
    • any associated multiple endocrine neoplasia [MEN] syndromes (E31.2-)
    Type 2 Excludes
    • malignant pancreatic islet cell tumors (C25.4)
    • Merkel cell carcinoma (C4A.-)
    Use Additional
    • code to identify any associated endocrine syndrome, such as:
    • carcinoid syndrome (E34.0)

Diagnosis Index entries containing back-references to E34.0:
  • Argentaffinoma - see also Neoplasm, uncertain behavior, by site
    • syndrome E34.0
  • Björck E34.0 (-Thorson) syndrome (malignant carcinoid)
  • Carcinoidosis E34.0
  • Cassidy E34.0 (-Scholte) syndrome (malignant carcinoid)
  • Flush syndrome E34.0
  • Scholte's syndrome E34.0 (malignant carcinoid)
  • Secretion
  • Syndrome - see also Disease
    • intestinal
      • carcinoid E34.0
    • malignant
      • carcinoid E34.0
    • argentaffin, argintaffinoma E34.0
    • Björck E34.0 (-Thorsen)
    • carcinoid E34.0
    • Cassidy E34.0 (-Scholte)
    • flush E34.0
    • Hedinger's E34.0
    • metastatic carcinoid E34.0
    • Scholte's E34.0
    • Thorson-Björck E34.0
  • Thorson-Björck syndrome E34.0

ICD-10-CM Codes Adjacent To E34.0
E31.22 Multiple endocrine neoplasia [MEN] type IIA
E31.23 Multiple endocrine neoplasia [MEN] type IIB
E31.8 Other polyglandular dysfunction
E31.9 Polyglandular dysfunction, unspecified
E32 Diseases of thymus
E32.0 Persistent hyperplasia of thymus
E32.1 Abscess of thymus
E32.8 Other diseases of thymus
E32.9 Disease of thymus, unspecified
E34 Other endocrine disorders
E34.0 Carcinoid syndrome
E34.1 Other hypersecretion of intestinal hormones
E34.2 Ectopic hormone secretion, not elsewhere classified
E34.3 Short stature due to endocrine disorder
E34.4 Constitutional tall stature
E34.5 Androgen insensitivity syndrome
E34.50 …… unspecified
E34.51 Complete androgen insensitivity syndrome
E34.52 Partial androgen insensitivity syndrome
E34.8 Other specified endocrine disorders
E34.9 Endocrine disorder, unspecified

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.