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ICD-10-CM Codes
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E00-E89
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Metabolic disorders E70-E88
Metabolic disorders E70-E88
Type 1 ExcludesType 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as E70-E88. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- androgen insensitivity syndrome (
ICD-10-CM Diagnosis Code E34.5
Androgen insensitivity syndrome
2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
E34.5-) - congenital adrenal hyperplasia (
ICD-10-CM Diagnosis Code E25.0
Congenital adrenogenital disorders associated with enzyme deficiency
2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
Applicable To- Congenital adrenal hyperplasia
- 21-Hydroxylase deficiency
- Salt-losing congenital adrenal hyperplasia
E25.0) - hemolytic anemias attributable to enzyme disorders (
ICD-10-CM Diagnosis Code D55
- D55 Anemia due to enzyme disorders
- D55.0 Anemia due to glucose-6-phosphate dehydrogena...
- D55.1 Anemia due to other disorders of glutathione ...
- D55.2 Anemia due to disorders of glycolytic enzymes...
- D55.21 Anemia due to pyruvate kinase deficiency
- D55.29 Anemia due to other disorders of glycolytic e...
- D55.3 Anemia due to disorders of nucleotide metabol...
- D55.8 Other anemias due to enzyme disorders
- D55.9 Anemia due to enzyme disorder, unspecified
D55.-) - Marfan's syndrome (
ICD-10-CM Diagnosis Code Q87.4
Marfan's syndrome
2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
Q87.4) - 5-alpha-reductase deficiency (
ICD-10-CM Diagnosis Code E29.1
Testicular hypofunction
2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx
Applicable To- Defective biosynthesis of testicular androgen NOS
- 5-delta-Reductase deficiency (with male pseudohermaphroditism)
- Testicular hypogonadism NOS
Type 1 Excludes- postprocedural testicular hypofunction (E89.5)
Use Additional- code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
E29.1)
Type 2 ExcludesType 2 Excludes Help
A type 2 excludes note represents "not included here". A type 2 excludes note indicates that the condition excluded is not part of the condition it is excluded from but a patient may have both conditions at the same time. When a type 2 excludes note appears under a code it is acceptable to use both the code (E70-E88) and the excluded code together.
Codes
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E70 Disorders of aromatic amino-acid metabolism
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E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
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E72 Other disorders of amino-acid metabolism
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E73 Lactose intolerance
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E74 Other disorders of carbohydrate metabolism
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E75 Disorders of sphingolipid metabolism and other lipid storage disorders
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E76 Disorders of glycosaminoglycan metabolism
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E77 Disorders of glycoprotein metabolism
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E78 Disorders of lipoprotein metabolism and other lipidemias
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E79 Disorders of purine and pyrimidine metabolism
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E80 Disorders of porphyrin and bilirubin metabolism
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E83 Disorders of mineral metabolism
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E84 Cystic fibrosis
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E85 Amyloidosis
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E86 Volume depletion
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E87 Other disorders of fluid, electrolyte and acid-base balance
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E88 Other and unspecified metabolic disorders
ICD-10-CM Diagnosis Codes E70-*
- E70 Disorders of aromatic amino-acid metabolism
- E70.0 Classical phenylketonuria
- E70.1 Other hyperphenylalaninemias
- E70.2 Disorders of tyrosine metabolism
- E70.20 Disorder of tyrosine metabolism, unspecified
- E70.21 Tyrosinemia
- E70.29 Other disorders of tyrosine metabolism
- E70.3 Albinism
- E70.30 …… unspecified
- E70.31 Ocular albinism
- E70.32 Oculocutaneous albinism
- E70.320 Tyrosinase negative oculocutaneous albinism
- E70.321 Tyrosinase positive oculocutaneous albinism
- E70.328 Other oculocutaneous albinism
- E70.329 …… unspecified
- E70.33 Albinism with hematologic abnormality
- E70.330 Chediak-Higashi syndrome
- E70.331 Hermansky-Pudlak syndrome
- E70.338 Other albinism with hematologic abnormality
- E70.339 Albinism with hematologic abnormality, unspec...
- E70.39 Other specified albinism
- E70.4 Disorders of histidine metabolism
- E70.40 Disorders of histidine metabolism, unspecifie...
- E70.41 Histidinemia
- E70.49 Other disorders of histidine metabolism
- E70.5 Disorders of tryptophan metabolism
- E70.8 Other disorders of aromatic amino-acid metabo...
- E70.81 Aromatic L-amino acid decarboxylase deficienc...
- E70.89 Other disorders of aromatic amino-acid metabo...
- E70.9 Disorder of aromatic amino-acid metabolism, u...
ICD-10-CM Diagnosis Codes E71-*
- E71 Disorders of branched-chain amino-acid metabo...
- E71.0 Maple-syrup-urine disease
- E71.1 Other disorders of branched-chain amino-acid ...
- E71.11 Branched-chain organic acidurias
- E71.110 Isovaleric acidemia
- E71.111 3-methylglutaconic aciduria
- E71.118 Other branched-chain organic acidurias
- E71.12 Disorders of propionate metabolism
- E71.120 Methylmalonic acidemia
- E71.121 Propionic acidemia
- E71.128 Other disorders of propionate metabolism
- E71.19 Other disorders of branched-chain amino-acid ...
- E71.2 Disorder of branched-chain amino-acid metabol...
- E71.3 Disorders of fatty-acid metabolism
- E71.30 Disorder of fatty-acid metabolism, unspecifie...
- E71.31 Disorders of fatty-acid oxidation
- E71.310 Long chain/very long chain acyl CoA dehydroge...
- E71.311 Medium chain acyl CoA dehydrogenase deficienc...
- E71.312 Short chain acyl CoA dehydrogenase deficiency...
- E71.313 Glutaric aciduria type II
- E71.314 Muscle carnitine palmitoyltransferase deficie...
- E71.318 Other disorders of fatty-acid oxidation
- E71.32 Disorders of ketone metabolism
- E71.39 Other disorders of fatty-acid metabolism
- E71.4 Disorders of carnitine metabolism
- E71.40 Disorder of carnitine metabolism, unspecified...
- E71.41 Primary carnitine deficiency
- E71.42 Carnitine deficiency due to inborn errors of ...
- E71.43 Iatrogenic carnitine deficiency
- E71.44 Other secondary carnitine deficiency
- E71.440 Ruvalcaba-Myhre-Smith syndrome
- E71.448 Other secondary carnitine deficiency
- E71.5 Peroxisomal disorders
- E71.50 Peroxisomal disorder, unspecified
- E71.51 Disorders of peroxisome biogenesis
- E71.510 Zellweger syndrome
- E71.511 Neonatal adrenoleukodystrophy
- E71.518 Other disorders of peroxisome biogenesis
- E71.52 X-linked adrenoleukodystrophy
- E71.520 Childhood cerebral X-linked adrenoleukodystro...
- E71.521 Adolescent X-linked adrenoleukodystrophy
- E71.522 Adrenomyeloneuropathy
- E71.528 Other X-linked adrenoleukodystrophy
- E71.529 X-linked adrenoleukodystrophy, unspecified ty...
- E71.53 Other group 2 peroxisomal disorders
- E71.54 Other peroxisomal disorders
- E71.540 Rhizomelic chondrodysplasia punctata
- E71.541 Zellweger-like syndrome
- E71.542 Other group 3 peroxisomal disorders
- E71.548 Other peroxisomal disorders
ICD-10-CM Diagnosis Codes E72-*
- E72 Other disorders of amino-acid metabolism
- E72.0 Disorders of amino-acid transport
- E72.00 Disorders of amino-acid transport, unspecifie...
- E72.01 Cystinuria
- E72.02 Hartnup's disease
- E72.03 Lowe's syndrome
- E72.04 Cystinosis
- E72.09 Other disorders of amino-acid transport
- E72.1 Disorders of sulfur-bearing amino-acid metabo...
- E72.10 Disorders of sulfur-bearing amino-acid metabo...
- E72.11 Homocystinuria
- E72.12 Methylenetetrahydrofolate reductase deficienc...
- E72.19 Other disorders of sulfur-bearing amino-acid ...
- E72.2 Disorders of urea cycle metabolism
- E72.20 Disorder of urea cycle metabolism, unspecifie...
- E72.21 Argininemia
- E72.22 Arginosuccinic aciduria
- E72.23 Citrullinemia
- E72.29 Other disorders of urea cycle metabolism
- E72.3 Disorders of lysine and hydroxylysine metabol...
- E72.4 Disorders of ornithine metabolism
- E72.5 Disorders of glycine metabolism
- E72.50 Disorder of glycine metabolism, unspecified
- E72.51 Non-ketotic hyperglycinemia
- E72.52 Trimethylaminuria
- E72.53 Primary hyperoxaluria
- E72.59 Other disorders of glycine metabolism
- E72.8 Other specified disorders of amino-acid metab...
- E72.81 Disorders of gamma aminobutyric acid metaboli...
- E72.89 Other specified disorders of amino-acid metab...
- E72.9 Disorder of amino-acid metabolism, unspecifie...
ICD-10-CM Diagnosis Codes E73-*
- E73 Lactose intolerance
- E73.0 Congenital lactase deficiency
- E73.1 Secondary lactase deficiency
- E73.8 Other lactose intolerance
- E73.9 Lactose intolerance, unspecified
ICD-10-CM Diagnosis Codes E74-*
- E74 Other disorders of carbohydrate metabolism
- E74.0 Glycogen storage disease
- E74.1 Disorders of fructose metabolism
- E74.10 Disorder of fructose metabolism, unspecified
- E74.11 Essential fructosuria
- E74.12 Hereditary fructose intolerance
- E74.19 Other disorders of fructose metabolism
- E74.2 Disorders of galactose metabolism
- E74.20 Disorders of galactose metabolism, unspecifie...
- E74.21 Galactosemia
- E74.29 Other disorders of galactose metabolism
- E74.3 Other disorders of intestinal carbohydrate ab...
- E74.31 Sucrase-isomaltase deficiency
- E74.39 Other disorders of intestinal carbohydrate ab...
- E74.4 Disorders of pyruvate metabolism and gluconeo...
- E74.8 Other specified disorders of carbohydrate met...
- E74.81 Disorders of glucose transport, not elsewhere...
- E74.810 Glucose transporter protein type 1 deficiency...
- E74.818 Other disorders of glucose transport
- E74.819 Disorders of glucose transport, unspecified
- E74.89 Other specified disorders of carbohydrate met...
- E74.9 Disorder of carbohydrate metabolism, unspecif...
ICD-10-CM Diagnosis Codes E75-*
- E75 Disorders of sphingolipid metabolism and othe...
- E75.0 GM2 gangliosidosis
- E75.1 Other and unspecified gangliosidosis
- E75.2 Other sphingolipidosis
- E75.3 Sphingolipidosis, unspecified
- E75.4 Neuronal ceroid lipofuscinosis
- E75.5 Other lipid storage disorders
- E75.6 Lipid storage disorder, unspecified
ICD-10-CM Diagnosis Codes E76-*
- E76 Disorders of glycosaminoglycan metabolism
- E76.0 Mucopolysaccharidosis, type I
- E76.1 Mucopolysaccharidosis, type II
- E76.2 Other mucopolysaccharidoses
- E76.21 Morquio mucopolysaccharidoses
- E76.22 Sanfilippo mucopolysaccharidoses
- E76.29 Other mucopolysaccharidoses
- E76.3 Mucopolysaccharidosis, unspecified
- E76.8 Other disorders of glucosaminoglycan metaboli...
- E76.9 Glucosaminoglycan metabolism disorder, unspec...
ICD-10-CM Diagnosis Codes E77-*
- E77 Disorders of glycoprotein metabolism
- E77.0 Defects in post-translational modification of...
- E77.1 Defects in glycoprotein degradation
- E77.8 Other disorders of glycoprotein metabolism
- E77.9 Disorder of glycoprotein metabolism, unspecif...
ICD-10-CM Diagnosis Codes E78-*
- E78 Disorders of lipoprotein metabolism and other...
- E78.0 Pure hypercholesterolemia
- E78.1 Pure hyperglyceridemia
- E78.2 Mixed hyperlipidemia
- E78.3 Hyperchylomicronemia
- E78.4 Other hyperlipidemia
- E78.5 Hyperlipidemia, unspecified
- E78.6 Lipoprotein deficiency
- E78.7 Disorders of bile acid and cholesterol metabo...
- E78.70 Disorder of bile acid and cholesterol metabol...
- E78.71 Barth syndrome
- E78.72 Smith-Lemli-Opitz syndrome
- E78.79 Other disorders of bile acid and cholesterol ...
- E78.8 Other disorders of lipoprotein metabolism
- E78.81 Lipoid dermatoarthritis
- E78.89 Other lipoprotein metabolism disorders
- E78.9 Disorder of lipoprotein metabolism, unspecifi...
ICD-10-CM Diagnosis Codes E79-*
- E79 Disorders of purine and pyrimidine metabolism...
- E79.0 Hyperuricemia without signs of inflammatory a...
- E79.1 Lesch-Nyhan syndrome
- E79.2 Myoadenylate deaminase deficiency
- E79.8 Other disorders of purine and pyrimidine meta...
- E79.9 Disorder of purine and pyrimidine metabolism,...
ICD-10-CM Diagnosis Codes E80-*
- E80 Disorders of porphyrin and bilirubin metaboli...
- E80.0 Hereditary erythropoietic porphyria
- E80.1 Porphyria cutanea tarda
- E80.2 Other and unspecified porphyria
- E80.20 Unspecified porphyria
- E80.21 Acute intermittent (hepatic) porphyria
- E80.29 Other porphyria
- E80.3 Defects of catalase and peroxidase
- E80.4 Gilbert syndrome
- E80.5 Crigler-Najjar syndrome
- E80.6 Other disorders of bilirubin metabolism
- E80.7 Disorder of bilirubin metabolism, unspecified...
ICD-10-CM Diagnosis Codes E83-*
- E83 Disorders of mineral metabolism
- E83.0 Disorders of copper metabolism
- E83.00 Disorder of copper metabolism, unspecified
- E83.01 Wilson's disease
- E83.09 Other disorders of copper metabolism
- E83.1 Disorders of iron metabolism
- E83.10 Disorder of iron metabolism, unspecified
- E83.11 Hemochromatosis
- E83.110 Hereditary hemochromatosis
- E83.111 Hemochromatosis due to repeated red blood cel...
- E83.118 Other hemochromatosis
- E83.119 …… unspecified
- E83.19 Other disorders of iron metabolism
- E83.2 Disorders of zinc metabolism
- E83.3 Disorders of phosphorus metabolism and phosph...
- E83.30 Disorder of phosphorus metabolism, unspecifie...
- E83.31 Familial hypophosphatemia
- E83.32 Hereditary vitamin D-dependent rickets (type ...
- E83.39 Other disorders of phosphorus metabolism
- E83.4 Disorders of magnesium metabolism
- E83.40 Disorders of magnesium metabolism, unspecifie...
- E83.41 Hypermagnesemia
- E83.42 Hypomagnesemia
- E83.49 Other disorders of magnesium metabolism
- E83.5 Disorders of calcium metabolism
- E83.50 Unspecified disorder of calcium metabolism
- E83.51 Hypocalcemia
- E83.52 Hypercalcemia
- E83.59 Other disorders of calcium metabolism
- E83.8 Other disorders of mineral metabolism
- E83.81 Hungry bone syndrome
- E83.89 Other disorders of mineral metabolism
- E83.9 Disorder of mineral metabolism, unspecified
ICD-10-CM Diagnosis Codes E84-*
- E84 Cystic fibrosis
- E84.0 Cystic fibrosis with pulmonary manifestations...
- E84.1 Cystic fibrosis with intestinal manifestation...
- E84.11 Meconium ileus in cystic fibrosis
- E84.19 Cystic fibrosis with other intestinal manifes...
- E84.8 Cystic fibrosis with other manifestations
- E84.9 Cystic fibrosis, unspecified
ICD-10-CM Diagnosis Codes E85-*
- E85 Amyloidosis
- E85.0 Non-neuropathic heredofamilial amyloidosis
- E85.1 Neuropathic heredofamilial amyloidosis
- E85.2 Heredofamilial amyloidosis, unspecified
- E85.3 Secondary systemic amyloidosis
- E85.4 Organ-limited amyloidosis
- E85.8 Other amyloidosis
- E85.81 Light chain (AL) amyloidosis
- E85.82 Wild-type transthyretin-related (ATTR) amyloi...
- E85.89 Other amyloidosis
- E85.9 Amyloidosis, unspecified
ICD-10-CM Diagnosis Codes E86-*
ICD-10-CM Diagnosis Codes E87-*
- E87 Other disorders of fluid, electrolyte and aci...
- E87.0 Hyperosmolality and hypernatremia
- E87.1 Hypo-osmolality and hyponatremia
- E87.2 Acidosis
- E87.3 Alkalosis
- E87.4 Mixed disorder of acid-base balance
- E87.5 Hyperkalemia
- E87.6 Hypokalemia
- E87.7 Fluid overload
- E87.70 …… unspecified
- E87.71 Transfusion associated circulatory overload
- E87.79 Other fluid overload
- E87.8 Other disorders of electrolyte and fluid bala...
ICD-10-CM Diagnosis Codes E88-*
- E88 Other and unspecified metabolic disorders
- E88.0 Disorders of plasma-protein metabolism, not e...
- E88.01 Alpha-1-antitrypsin deficiency
- E88.02 Plasminogen deficiency
- E88.09 Other disorders of plasma-protein metabolism,...
- E88.1 Lipodystrophy, not elsewhere classified
- E88.2 Lipomatosis, not elsewhere classified
- E88.3 Tumor lysis syndrome
- E88.4 Mitochondrial metabolism disorders
- E88.40 Mitochondrial metabolism disorder, unspecifie...
- E88.41 MELAS syndrome
- E88.42 MERRF syndrome
- E88.49 Other mitochondrial metabolism disorders
- E88.8 Other specified metabolic disorders
- E88.81 Metabolic syndrome
- E88.89 Other specified metabolic disorders
- E88.9 Metabolic disorder, unspecified
| E00-E89
ICD-10-CM Range E00-E89 Endocrine, nutritional and metabolic diseases- E00-E07 Disorders of thyroid gland
- E08-E13 Diabetes mellitus
- E15-E16 Other disorders of glucose regulation an...
- E20-E35 Disorders of other endocrine glands
- E36-E36 Intraoperative complications of endocrin...
- E40-E46 Malnutrition
- E50-E64 Other nutritional deficiencies
- E65-E68 Overweight, obesity and other hyperalime...
- E70-E88 Metabolic disorders
- E89-E89 Postprocedural endocrine and metabolic c...
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E65-E68 ICD-10-CM Range E65-E68 Overweight, obesity and other hyperalimentation- E65 Localized adiposity
- E66 Overweight and obesity
- E67 Other hyperalimentation
- E68 Sequelae of hyperalimentation
| ICD10Data.com | E89-E89 ICD-10-CM Range E89-E89 Postprocedural endocrine and metabolic complications and disorders, not elsewhere classified- E89 Postprocedural endocrine and metabolic c...
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| F01-F99
ICD-10-CM Range F01-F99 Mental, Behavioral and Neurodevelopmental disorders- F01-F09 Mental disorders due to known physiologi...
- F10-F19 Mental and behavioral disorders due to p...
- F20-F29 Schizophrenia, schizotypal, delusional, ...
- F30-F39 Mood [affective] disorders
- F40-F48 Anxiety, dissociative, stress-related, s...
- F50-F59 Behavioral syndromes associated with phy...
- F60-F69 Disorders of adult personality and behav...
- F70-F79 Intellectual disabilities
- F80-F89 Pervasive and specific developmental dis...
- F90-F98 Behavioral and emotional disorders with ...
- F99-F99 Unspecified mental disorder
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