ICD-10-CM Codes
E00-E89 Endocrine, nutritional and metabolic diseases
E70-E88 Metabolic disorders
E70- Disorders of aromatic amino-acid metabolism
2021 ICD-10-CM Diagnosis Code E70.1

2021 ICD-10-CM Diagnosis Code E70.1

Other hyperphenylalaninemias

2016

2017

2018

2019

2020

2021

Billable/Specific Code

E70.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2021 edition of ICD-10-CM E70.1 became effective on October 1, 2020.
This is the American ICD-10-CM version of E70.1 - other international versions of ICD-10 E70.1 may differ.

The following code(s) above E70.1 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to E70.1:

E00-E89
2021 ICD-10-CM Range E00-E89
Endocrine, nutritional and metabolic diseases
Note
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Type 1 Excludes
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Endocrine, nutritional and metabolic diseases
E70-E88
2021 ICD-10-CM Range E70-E88
Metabolic disorders
Type 1 Excludes
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- Ehlers-Danlos syndromes (Q79.6-)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan's syndrome (Q87.4)
- 5-alpha-reductase deficiency (E29.1)
Metabolic disorders

Approximate Synonyms

Classical phenylketonuria
Hyperphenylalaninemia
Maternal phenylketonuria
Phenylketonuria
Phenylketonuria, maternal

ICD-10-CM E70.1 is grouped within Diagnostic Related Group(s) (MS-DRG v38.0):

642 Inborn and other disorders of metabolism

Convert E70.1 to ICD-9-CM

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change
2021 (effective 10/1/2020): No change

Diagnosis Index entries containing back-references to E70.1:

Deficiency, deficient
- phenylalanine hydroxylase E70.1
Disorder (of) - see also Disease
- metabolism NOS E88.9
  ICD-10-CM Diagnosis Code E88.9
  Metabolic disorder, unspecified
  2016 2017 2018 2019 2020 2021 Billable/Specific Code
  - amino-acid E72.9
    ICD-10-CM Diagnosis Code E72.9
    Disorder of amino-acid metabolism, unspecified
    2016 2017 2018 2019 2020 2021 Billable/Specific Code
    - aromatic E70.9
      ICD-10-CM Diagnosis Code E70.9
      Disorder of aromatic amino-acid metabolism, unspecified
      2016 2017 2018 2019 2020 2021 Billable/Specific Code
      - hyperphenylalaninemia E70.1
Hyperphenylalaninemia NEC E70.1
Phenylketonuria E70.1
- maternal E70.1

ICD-10-CM Codes Adjacent To E70.1

E66.9 Obesity, unspecified

E67 Other hyperalimentation

E67.0 Hypervitaminosis A

E67.1 Hypercarotenemia

E67.2 Megavitamin-B6 syndrome

E67.3 Hypervitaminosis D

E67.8 Other specified hyperalimentation

E68 Sequelae of hyperalimentation

E70 Disorders of aromatic amino-acid metabolism

E70.0 Classical phenylketonuria

E70.1 Other hyperphenylalaninemias

E70.2 Disorders of tyrosine metabolism

E70.20 Disorder of tyrosine metabolism, unspecified

E70.21 Tyrosinemia

E70.29 Other disorders of tyrosine metabolism

E70.3 Albinism

E70.30 …… unspecified

E70.31 Ocular albinism

E70.310 X-linked ocular albinism

E70.311 Autosomal recessive ocular albinism

E70.318 Other ocular albinism

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2021 ICD-10-CM Diagnosis Code E70.1

Other hyperphenylalaninemias

Endocrine, nutritional and metabolic diseases

Metabolic disorders

Metabolic disorder, unspecified

Disorder of amino-acid metabolism, unspecified

Disorder of aromatic amino-acid metabolism, unspecified